Recurrent lower respiratory tract infections in a 14-year-old boy with tracheobronchomegaly (Mounier-Kuhn syndrome).

Abstract:

:Tracheobronchomegaly (Mounier-Kuhn syndrome) is characterized by dilatation of the central airways, tracheobronchial outpouchings, and chronic tracheobronchitis. Most cases are diagnosed in adulthood. We report the clinical, radiographic, and bronchoscopic findings in a 14-year-old boy with tracheobronchomegaly, ptosis of the right eyelid, and redundant skin and mucosa of the upper lip, who presented with a 2-year history of recurrent lower respiratory tract infections. Pediatricians should be aware of the possibility that tracheobronchomegaly may cause clinical symptoms in childhood and adolescence. Pediatr Pulmonol. 2000; 29: 476-479.

journal_name

Pediatr Pulmonol

journal_title

Pediatric pulmonology

authors

Benesch M,Eber E,Pfleger A,Zach MS

doi

10.1002/(sici)1099-0496(200006)29:6<476::aid-ppul1

subject

Has Abstract

pub_date

2000-06-01 00:00:00

pages

476-9

issue

6

eissn

8755-6863

issn

1099-0496

pii

10.1002/(SICI)1099-0496(200006)29:6<476::AID-PPUL1

journal_volume

29

pub_type

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