Abstract:
:In this study we evaluated the relationship between polyglucosan bodies and peripheral nerve lesions. The biopsied sural nerve from a patient with late-onset chronic sensori-motor neuropathy showed many intra-axonal polyglucosan bodies and segmental demyelination/remyelination. The formation of Schwann cell hyperplasia around the demyelinated axons was found at the sites of polyglucosan bodies. These findings suggest that demyelinating neuropathy is a part of the spectrum of the diseases characterized by the accumulation of polyglucosan bodies within cellular compartments.
journal_name
Acta Neuropatholjournal_title
Acta neuropathologicaauthors
Matsumuro K,Izumo S,Minauchi Y,Inose M,Higuchi I,Osame Mdoi
10.1007/BF00454906subject
Has Abstractpub_date
1993-01-01 00:00:00pages
95-9issue
1eissn
0001-6322issn
1432-0533journal_volume
86pub_type
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journal_title:Acta neuropathologica
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