Diagnostic radioimmunoassay and DNA-analysis in Swedish and Japanese patients with familial amyloidotic polyneuropathy. Homozygosity for the TTR met30 gene.

abstract：OBJECTIVE:To explore the relationship between motor subtypes and drooling, and other risk factors associated with drooling in a large cohort of Chinese patients with Parkinson's disease (PD). METHODS:A total of 586 PD patients were enrolled in this study. Unified Parkinson's disease rating scale (UPDRS) and Hoehn & Ya...

journal_title：Acta neurologica Scandinavica

authors： Mao CJ,Xiong YT,Wang F,Yang YP,Yuan W,Zhu C,Chen J,Liu CF

更新日期：2018-05-01 00:00:00

abstract：:Brain perfusion was studied interictally with 99mTc-HM-PAO SPECT in 47 adult patients with partial epilepsy and normal brain CT. Epilepsy was classified as secondarily generalized in 24 patients, as complex partial in 17 patients and as simple partial in 6 patients. In 24 patients good seizure control was not achieved...

journal_title：Acta neurologica Scandinavica

authors： Launes J,Iivanainen M,Salmi T,Nikkinen P,Lindroth L,Liewendahl K

更新日期：1992-12-01 00:00:00

abstract：OBJECTIVES:To provide an update on recent research concerning obstructive sleep apnea syndrome (OSAS) and executive functions. METHODS:A systematic review was carried out on reports drawn from MEDLINE and PSYCHLIT (January 1990-December 2005) and identified from lists of references in these reports. The selection crit...

journal_title：Acta neurologica Scandinavica

authors： Saunamäki T,Jehkonen M

更新日期：2007-01-01 00:00:00

abstract：BACKGROUND:Excessive daytime sleepiness (EDS) is a symptom frequently presented in sleep clinics. Only a paucity of data has addressed clinical courses of sleep disorders with EDS. Therefore, we sought to compare clinical outcomes of patients presenting EDS. METHODS:A retrospective observational study was performed in...

journal_title：Acta neurologica Scandinavica

authors： Kim T,Lee JH,Lee CS,Yoon IY

更新日期：2016-07-01 00:00:00

abstract：:The effect of a new peripherally acting muscle relaxant drug Dantrium, on spasticity tested on 11 hemiplegic patients. The effect was evaluated both with regular clinical examination and with electromyographic technique. The latter concerned a quantitative analysis of the patients' voluntary control of fine neuromuscu...

journal_title：Acta neurologica Scandinavica

authors： Jonsson B,Ladd H,Afzelius-Frisk I,Lindberg-Broman AM

更新日期：1975-05-01 00:00:00

abstract：:Adenylate kinase (AK) was determined in a lumbo-cisternal cerebrospinal fluid (CSF) gradient and in CSF from patients with mental deterioration. AK activity was unchanged in the gradient and different from albumin and albumin ratio (alb CSF/albumin serum), a blood-brain barrier marker in the same gradient. No differen...

journal_title：Acta neurologica Scandinavica

authors： Ahlberg J,Blomstrand C,Ronquist G,Wikkelsö C

更新日期：1985-11-01 00:00:00

abstract：:We report a case of acute Wernicke encephalopathy (WE) in which apparent diffusion coefficient maps showed areas of increased diffusion in the bilateral medial thalami that corresponded to the hyperintense lesions on T2-weighted imaging. The hyperintense lesions on T2-weighted imaging disappeared with full recovery fr...

journal_title：Acta neurologica Scandinavica

authors： Oka M,Terae S,Kobayashi R,Kudoh K,Chu BC,Kaneko K,Yoshida M,Kaneda M,Suzuki Y,Miyasaka K

更新日期：2001-09-01 00:00:00

abstract：:A case of necrotizing brain stem encephalitis due to listeria monocytogenes is described in a 48-year-old man who had brain stem encephalitis of complicated course and with selective destruction of the vasomotoric and respiratory centers. He developed that very rare Ondine's curse syndrome, being only able to breathe ...

journal_title：Acta neurologica Scandinavica

authors： Jensen TH,Hansen PB,Brodersen P

更新日期：1988-06-01 00:00:00

abstract：:The relation between angiographically determined cerebral vasospasm following a subarachnoid hemorrhage and regional cerebral blood flow (CBF) was studied in 63 investigations of 45 patients. The CBF was measured using the intra-arterial 133-Xe clearance technique within one hour of angiography. A positive correlation...

journal_title：Acta neurologica Scandinavica

authors： Jakobsen M,Overgaard J,Marcussen E,Enevoldsen EM

更新日期：1990-08-01 00:00:00

abstract：INTRODUCTION:Most studies revealing intellectual deficits in myotonic dystrophy (MyD) involved heterogeneous groups of patients with respect to intelligence and onset of disease. The present study was undertaken to investigate whether patients with early adult and adult MyD show subtle cognitive deficits despite a norm...

journal_title：Acta neurologica Scandinavica

authors： Van Spaendonck KP,Ter Bruggen JP,Weyn Banningh EW,Maassen BA,Van de Biezenbos JB,Gabreëls FJ

更新日期：1995-06-01 00:00:00

abstract：OBJECTIVES:To investigate eventual differences between women and men with Parkinson's disease (PD) before and after surgery, with respect to clinical status, disability and health-related quality of life (HRQoL). MATERIAL AND METHODS:Twenty-four men and 14 women with PD received a total of 46 surgical procedures (pall...

journal_title：Acta neurologica Scandinavica

authors： Hariz GM,Lindberg M,Hariz MI,Bergenheim AT

更新日期：2003-07-01 00:00:00

abstract：:The aim of this study was to ascertain whether there is an association between risk of multiple sclerosis (MS) and birth order position. Our reference population was 198,000 persons born in the period 1930-50 and recorded in the register of school health records from the school health service of the Copenhagen council...

journal_title：Acta neurologica Scandinavica

authors： Isager H,Andersen E,Hyllested K

更新日期：1980-06-01 00:00:00

abstract：:Intrathecal IgG synthesis and CSF oligoclonal bands were reexamined after 18-24 months in 66 patients with multiple sclerosis; 40 of them received azathioprine (AZA) 2.5 mg/Kg/die; all received a course of dexamethasone (DEXA) during clinical relapses. The IgG Index was significantly reduced in the group treated with ...

journal_title：Acta neurologica Scandinavica

authors： Caputo D,Zaffaroni M,Ghezzi A,Cazzullo CL

更新日期：1987-02-01 00:00:00

abstract：:The effects of L-threo-3,4-dihydroxyphenylserine (L-threo-DOPS), an unnatural norepinephrine precursor, on alpha 2-adrenergic receptors in platelet membranes were investigated in a patient with familial amyloidotic polyneuropathy, two patients with multiple system atrophy, and two patients with Parkinson's disease. Ea...

journal_title：Acta neurologica Scandinavica

authors： Azuma T,Suzuki T,Sakoda S,Mizuno R,Tsujino S,Kobayashi T,Kishimoto S,Hiraga T,Matsubara T,Yoshida S

更新日期：1991-07-01 00:00:00

abstract：:Treatment with intraventricular pentosan polysulphate (PPS) might be beneficial in patients with Creutzfeldt-Jakob disease. We report a 68-year-old woman with sporadic Creutzfeldt-Jakob disease who received continuous intraventricular PPS infusion (1-120 microg/kg/day) for 17 months starting 10 months after the onset ...

journal_title：Acta neurologica Scandinavica

authors： Terada T,Tsuboi Y,Obi T,Doh-ura K,Murayama S,Kitamoto T,Yamada T,Mizoguchi K

更新日期：2010-02-01 00:00:00

abstract：:A Chinese family with at least 3 members having the typical clinical picture of type I familial amyloid polyneuropathy is presented. The pathological features, including the immunohistochemical typing of the amyloid deposits, are described and the literature is briefly reviewed. ...

journal_title：Acta neurologica Scandinavica

authors： Chang CM,Yu YL,Wong M,Ng TH,Woo E,Huang CY

更新日期：1989-05-01 00:00:00

abstract：BACKGROUND:Persons who have suffered from acute poliomyelitis may decades later experience reduction of balance and gait capacity due to muscle weakness, fatigue and/or pain. This may affect the activity level in daily life of these persons. AIMS OF THE STUDY:The aim of this study was to describe observer assessed and...

journal_title：Acta neurologica Scandinavica

authors： Lehmann K,Sunnerhagen KS,Willén C

更新日期：2006-01-01 00:00:00

abstract：OBJECTIVES:Dopamine neurotransmission is a critical factor for executive function, which is controlled by the prefrontal cortex in humans. Although the contribution of genetic factors to the regulation of brain dopaminergic activity is widely acknowledged, identification of a genotype-phenotype association has not yet ...

journal_title：Acta neurologica Scandinavica

authors： Mitaki S,Isomura M,Maniwa K,Yamasaki M,Nagai A,Nabika T,Yamaguchi S

更新日期：2013-01-01 00:00:00

abstract：OBJECTIVES:To re-evaluate middle-aged Swedish patients diagnosed with dysequilibrium syndrome (DES) in childhood and to compare their clinical and neuroimaging features to DES with VLDLR gene mutations (DES-VLDR). MATERIALS AND METHODS:Six patients from five families underwent neurological examination and magnetic res...

journal_title：Acta neurologica Scandinavica

authors： Melberg A,Orlén H,Raininko R,Entesarian M,Dahlqvist J,Gustavson KH,Dahl N

更新日期：2011-01-01 00:00:00

abstract：OBJECTIVES:It was shown previously that low-Mg2+-induced epileptiform activity in rat entorhinal cortex slices changes with time from a pattern of serial seizure-like events (SLEs) to a state of continuously recurring epileptiform activity. Valproic acid blocked the early SLEs but not the late activity. It was proposed...

journal_title：Acta neurologica Scandinavica

authors： Dreier JP,Zhang CL,Heinemann U

更新日期：1998-09-01 00:00:00

abstract：:A total of 43 patients with multiple sclerosis (MS) consecutively admitted to the Multiple Sclerosis Rehabilitation Hospital in Haslev completed a Danish version of the Laman & Lankhorst Questionnaire (LLQ) on quality of life (qol), and the Beck Depression Inventory (BDI). Twenty-one of the 43 pts completed the questi...

journal_title：Acta neurologica Scandinavica

authors： Jønsson A,Dock J,Ravnborg MH

更新日期：1996-04-01 00:00:00

abstract：OBJECTIVES:To explore (1) effects of test and subject variables in determining euphoric and dysphoric responses during unilateral amobarbital anesthesia and (2) which cerebral areas contribute to the emotional responses. METHOD:Incidence of euphoric and dysphoric reactions during left- and right-sided amobarbital anes...

journal_title：Acta neurologica Scandinavica

authors： Stabell KE,Andresen S,Bakke SJ,Bjørnaes H,Borchgrevink HM,Heminghyt E,Røste GK

更新日期：2004-11-01 00:00:00

abstract：OBJECTIVES:We used an electrical conditioning stimulation followed by transcranial magnetic stimulation (TMS) to facilitate the occurrence of long latency potentials (LLPs) in order to study the relationship between primary motor evoked potentials (MEPs) and LLPs in the lower limbs. MATERIALS AND METHODS:The study gro...

journal_title：Acta neurologica Scandinavica

authors： Chen JT,Chen CC,Kao KP,Wu ZA,Liao KK

更新日期：1998-12-01 00:00:00

abstract：BACKGROUND:Multiple sclerosis (MS) is associated with Epstein-Barr virus (EBV) infection, but the relationship between the virus and the disease is not clear. As many different types of EBV exist, it is possible that MS is caused by one particular type of EBV. Objectives - The aim of this study was to determine whether...

journal_title：Acta neurologica Scandinavica

authors： Lindsey JW,Patel S,Zou J

更新日期：2008-02-01 00:00:00

abstract：:The effect of methylprednisolone (MP) on neurologic recovery and spinal cord blood flow (SCBF) was investigated up to 4 days after a spinal cord compression injury in rats. The injury was produced at midthoracic level by applying a load of 35 g on a 2.2 x 5.0 mm compression plate for 5 min, which resulted in transient...

journal_title：Acta neurologica Scandinavica

authors： Holtz A,Nyström B,Gerdin B

更新日期：1990-07-01 00:00:00

abstract：OBJECTIVES:Botulinum neurotoxin (BoNT) injections in the salivary glands and radiotherapy (RT) on these glands are commonly used to alleviate severe drooling in patients with amyotrophic lateral sclerosis (ALS). This study compares BoNT type A with RT based on patient-rated evaluations. MATERIALS & METHODS:A prospecti...

journal_title：Acta neurologica Scandinavica

authors： Weikamp JG,Schinagl DA,Verstappen CC,Schelhaas HJ,de Swart BJ,Kalf JG

更新日期：2016-09-01 00:00:00

abstract：:A three generation family is presented in which rapidly progressive, early-onset Creutzfeldt-Jakob disease without typical EEG changes segregates as an autosomal dominant disease. An aspartic acid to asparagine mutation at codon 178 of the prion gene, PRNP, co-segregates with the disease. As expected, the disease alle...

journal_title：Acta neurologica Scandinavica

authors： Holm IE,Abelskov K,Bojsen-Møller M,Nielsen AL,Jørgensen AL

更新日期：2001-03-01 00:00:00

abstract：:Decompressive craniectomy is a neurosurgical technique in which a portion of the skull is removed to reduce intracranial pressure. The rationale for this procedure is based on the Monro-Kellie Doctrine; expanding the physical space confining edematous brain tissue after traumatic brain injury will reduce intracranial ...

journal_title：Acta neurologica Scandinavica

authors： Quinn TM,Taylor JJ,Magarik JA,Vought E,Kindy MS,Ellegala DB

更新日期：2011-04-01 00:00:00

abstract：:Regional cerebral blood flow (rCBF) was measured in 23 patients with brain tumors using the 133Xe intra-carotid injection method and a 254 channel gamma camera. The glioblastomas (4) and astrocytomas (4) all showed hyperemia in the tumor and tumor-near region. This was also seen in several meningiomas (4 of 7 cases) i...

journal_title：Acta neurologica Scandinavica

authors： Kuroda K,Skyhøj Olsen T,Lassen NA

更新日期：1982-08-01 00:00:00

abstract：:We tested the validity of a self-administered version of the minimal record of disability (MRD) for multiple sclerosis (MS) by measuring the agreement level between patients' self-assessment and neurologists' independent ratings. 96 MS patients and 4 neurologists took part in the experiment; the agreement level was me...

journal_title：Acta neurologica Scandinavica

authors： Solari A,Amato MP,Bergamaschi R,Logroscino G,Citterio A,Bochicchio D,Filippini G

更新日期：1993-01-01 00:00:00