Abstract:
:Morvan syndrome is a rare autoimmune disease named after the French physician Augustin Marie Morvan. It is characterized by multiple, irregular contractions of the long muscles, weakness, pruritus, hyperhidrosis, insomnia, and delirium. Here, we describe a 17-year-old young man, previously diagnosed with B-cell lymphoma, who presented with multiple asynchronous fasciculations of the long muscles of his lower extremities accompanied by numbness. The patient responded initially to pulse corticosteroids with diminution of the fasciculations. He achieved complete remission following 7 consecutive, monthly intravenous immunoglobulin injections. The present case is described in the context of the available literature.
journal_name
J Child Neuroljournal_title
Journal of child neurologyauthors
El-Bitar MK,Muwakkit SA,Abboud MR,Sawaya RA,Boustany RMdoi
10.1177/0883073809356108subject
Has Abstractpub_date
2010-08-01 00:00:00pages
1038-41issue
8eissn
0883-0738issn
1708-8283pii
0883073809356108journal_volume
25pub_type
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