Severe hemorrhage from intestinal hemangiomatosis in Klippel-Trenaunay syndrome: pitfalls in diagnosis and management.

Abstract:

:A child with Klippel-Trenaunay syndrome (KTS) and severe anemia caused by bleeding from diffuse intestinal hemangiomatosis is presented. Hemangiomas of the bowel should be considered in any child with unexplained anemia and coexisting cutaneous hemangiomas. The diagnostic workup of patients with KTS and symptomatic hemangiomatosis is outlined with respect to indications for surgical management.

authors

Schmitt B,Posselt HG,Waag KL,Müller H,Bender SW

doi

10.1097/00005176-198601000-00031

subject

Has Abstract

pub_date

1986-01-01 00:00:00

pages

155-8

issue

1

eissn

0277-2116

issn

1536-4801

journal_volume

5

pub_type

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