Abstract:
:A 5-year-old child with a Fontan circulation presented with acquired left pulmonary vein occlusion related to a previous surgical repair. We managed this lesion using a hybrid technique to perforate, dilate and stent the obstructed vessel. This approach should be considered when percutaneous access to the pulmonary veins is challenging (such as in a Fontan circulation). It also avoids the need for a high-risk redo sternotomy and cardiopulmonary bypass procedure.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Mainzer G,Rosenthal E,Austin C,Morgan Gdoi
10.1007/s00246-016-1376-9subject
Has Abstractpub_date
2016-06-01 00:00:00pages
983-5issue
5eissn
0172-0643issn
1432-1971pii
10.1007/s00246-016-1376-9journal_volume
37pub_type
杂志文章abstract::Contrary to acquired arteriovenous fistulas, the congenital malformations are very rare. Here we report a case of congenital arteriovenous fistula forming a communication between the right subclavian artery to subclavian vein. To our knowledge, there is no similar case in which an infant has been successfully operated...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010056
更新日期:2000-05-01 00:00:00
abstract::Pheochromocytoma is a rare disease, which often presents a diagnostic challenge due to a variable symptom presentation complex. We report the case of a child who presented with isolated symptoms of palpitations and was found to have junctional tachycardia with subsequent development of cardiomyopathy. Further evaluati...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9134-7
更新日期:2008-09-01 00:00:00
abstract::Cardiac rhabdomyoma (CR) is the most common cardiac tumor in newborns. Approximately 75% of cases are associated with tuberous sclerosis complex. Although these tumors usually spontaneously regress after 2 years of age, they can be life-threatening when they obstruct major cardiac inflow or outflow pathways. Everolimu...
journal_title:Pediatric cardiology
pub_type: 杂志文章
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更新日期:2017-10-01 00:00:00
abstract::This study was conducted to determine the efficacy of procainamide therapy for rapid rate control of postoperative junctional tachycardia (JT). Postoperative JT is one of the most difficult forms of tachycardia to manage. Reported success with a variety of treatments of JT in infants and children has been inconsistent...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469910018
更新日期:2000-03-01 00:00:00
abstract::The objective of this investigation was to compare how two modes of positive pressure ventilation affect cardiac output, airway pressures, oxygenation, and carbon dioxide removal in children with congenital heart disease in the immediate postoperative period. The investigation used a one group pretest-post-test study ...
journal_title:Pediatric cardiology
pub_type: 临床试验,杂志文章
doi:10.1007/s002460010210
更新日期:2001-05-01 00:00:00
abstract::The etiology and pathogenesis of Kawasaki disease (KD) is largely unknown. Certain demographic factors and laboratory findings are predictive of the development of coronary artery (CA) aneurysms. The objectives of this study were to determine the epidemiology of KD patients in an urban hospital and determine risk fact...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-0916-5
更新日期:2005-11-01 00:00:00
abstract::Anomalous origin of left pulmonary artery (ALPA) from aorta with atrial septal defect (ASD) is a rare congenital cardiac malformation. We report a case of ALPA from the aorta with ASD in a 1.8-kg baby. Repair was needed at an early age due to progressive congestive heart failure. Surgical correction was performed with...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9234-z
更新日期:2008-07-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-011-9954-3
更新日期:2011-06-01 00:00:00
abstract::Internationally, there have been isolated case reports published of children presenting with dilated cardiomyopathy (DCM) in the setting of undiagnosed rickets. Although there has been an increased prevalence of rickets in the United States, there has been only one documented case of associated DCM. At our institution...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9444-z
更新日期:2009-08-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9112-0
更新日期:2008-03-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-001-0051-x
更新日期:2002-03-01 00:00:00
abstract::Although transthoracic echocardiography (TTE) is the first-line examination for the study of coronary lesions in Kawasaki disease, CT coronary angiography (CTCA) is increasingly used and showed good results. Our aim is to evaluate the contribution of CTCA in the detection of coronary lesions and to compare its results...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-2044-z
更新日期:2019-02-01 00:00:00
abstract::Ventricular arrhythmias (VAs) are common pediatric rhythm disorders requiring comprehensive laboratory evaluation. Although usually idiopathic, implying a benign character and favorable prognosis, the initial clinical approach is still not established in all cases. Considering their prognostic significance, exercise-i...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9582-3
更新日期:2010-02-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-006-0072-6
更新日期:2007-09-01 00:00:00
abstract::The reported prenatal detection rates (PDRs) for significant congenital heart disease (sCHD) have been suboptimal, even in the current era. Changes in prenatal ultrasound policy and training may lead to improved prenatal detection of sCHD. This study analyzed the results of a policy to assess fetal cardiac outflow tra...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0526-y
更新日期:2013-03-01 00:00:00
abstract::Children with acquired and congenital heart disease (CHD) are increasingly surviving to adulthood. Our aim was to determine the prevalence of coronary artery disease (CAD) risk factors in children at known risk for early CAD or with severe CHD. We recruited children (8-19 years) at risk for early CAD-Kawasaki disease ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-017-1750-2
更新日期:2018-02-01 00:00:00
abstract::Operative survival after the Norwood procedure has significantly improved during the past 10 years. However, there remains attrition among Norwood survivors before reaching planned second-stage palliation. The purpose of this study was to evaluate potential risk factors for interstage mortality among Norwood survivors...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-004-0776-4
更新日期:2005-07-01 00:00:00
abstract::Warfarin dosing is challenging due to a multitude of factors affecting its pharmacokinetics (PK) and pharmacodynamics (PD). A novel personalised dosing algorithm predicated on a warfarin PK/PD model and incorporating CYP2C9 and VKORC1 genotype information has been developed for children. The present prospective, obser...
journal_title:Pediatric cardiology
pub_type: 杂志文章,随机对照试验
doi:10.1007/s00246-019-02215-y
更新日期:2019-12-01 00:00:00
abstract::Cardiopulmonary bypass (CPB) reduces coagulation factor levels through hemodilution and consumption. Differences in CPB-induced alterations of factor XIII (FXIII) levels in children with cyanotic and acyanotic congenital heart defects (CHDs) are not well characterized. FXIII activity (determined by Berichrom assay), p...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-014-0903-9
更新日期:2014-10-01 00:00:00
abstract::B-type natriuretic peptide (BNP) reflects volume overload on left ventricle and pulmonary hypertension (PH) in patients with ventricular septal defect (VSD). Pulmonary vascular resistance (PVR) has been reported to correlate positively with BNP in VSD patients with various degrees of PH. We aimed to investigate the re...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9037-7
更新日期:2008-01-01 00:00:00
abstract::Maintaining patency of the ductus arteriosus pending surgical intervention can be critical to the survival of the neonate with ductal dependent congenital heart disease. Spontaneously delayed ductal closure has been observed clinically and experimentally in newborns with critical pulmonic stenosis. Infants with ductal...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02263445
更新日期:1987-01-01 00:00:00
abstract:BACKGROUND:The purpose of this study was to investigate the associations between clinical factors and cardiac function as measured by pressure-volume loops (PVLs) in a pediatric heart transplant cohort. METHODS:Patients (age < 20 years) who underwent heart transplantation presenting for a clinically indicated catheter...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-017-1758-7
更新日期:2018-02-01 00:00:00
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journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02238841
更新日期:1990-07-01 00:00:00
abstract:OBJECTIVES:The aim of this article is to examine the frequency, timing of formation of aneurysm of the ventricular membranous septum (AVMS), and prognosis in patients with a perimembranous ventricular septal defect (VSD). PATIENTS:One hundred forty-eight patients were diagnosed with a perimembranous VSD within 90 days...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-003-0572-6
更新日期:2004-07-01 00:00:00
abstract::Studies of larger patient groups for systematic assessment of the anatomical accuracy of magnetic resonance imaging (MRI) for partial anomalous pulmonary venous drainage (PAPVD) have been performed so far only in adults. This study was undertaken to evaluate whether MRI can precisely depict pulmonary venous anatomy in...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9367-0
更新日期:2009-05-01 00:00:00
abstract::Long-term prostaglandin use is commonly associated with side effects such as cortical proliferation of the bones, hypertrophic pyloric stenosis, and soft tissue swelling of the extremities. We report a neonate with critical coarctation of the aorta, who developed second and third degree atrioventricular blocks associa...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-017-1633-6
更新日期:2017-10-01 00:00:00
abstract::In this report, we describe a case of coarctation of the aorta, congenital aortic stenosis with bicuspid valve, and supravalvar aortic stenosis with left coronary artery ostial stenosis. The child underwent staged treatment using a hybrid approach employing both surgical and interventional cardiology methods. A single...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002460010164
更新日期:2001-01-01 00:00:00
abstract::The epinephrine test has been shown to be a powerful tool to predict the genotype of congenital long QT syndrome (LQTS). The aim of this study was to evaluate its role in the diagnosis and management of LQTS in children. The test (using the Shimizu protocol) was conducted in patients with some evidence of LQTS but in ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9603-2
更新日期:2010-05-01 00:00:00
abstract::Embryonic development is a tightly regulated process, and many families of genes functions to provide a regulatory genetic network to achieve such a program. The homeobox genes are an extensive family that encodes transcription factors with a characteristic 60-amino acid homeodomain. Mutations in these genes or in the...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0179-x
更新日期:2012-08-01 00:00:00
abstract::While exercise stress testing (EST) is an important tool, little is known about its use for determining ischemia in patients with hypoplastic left heart syndrome (HLHS) and Fontan palliation. We sought to determine the frequency of ST segment changes during EST in HLHS patients after Fontan and examine results of furt...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-015-1312-4
更新日期:2016-03-01 00:00:00