Abstract:
:A marked decrease in the amplitude of the evoked thenar compound muscle action potential followed brief exercise at room temperature in two patients with paramyotonia congenita. This decline was more rapid and pronounced in our patient with coexistent thyrotoxicosis. The prolonged recovery period in paramyotonia congenita differs from the brief exercise-induced decreased compound muscle action potential seen in myotonia congenita and myotonic dystrophy. These findings suggest that exercise, like cold exposure, decreases membrane excitability in paramyotonia congenita.
journal_name
Neurologyjournal_title
Neurologyauthors
Gutmann L,Riggs JE,Brick JFdoi
10.1212/wnl.36.1.130subject
Has Abstractpub_date
1986-01-01 00:00:00pages
130-2issue
1eissn
0028-3878issn
1526-632Xjournal_volume
36pub_type
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