Abstract:
:A 5-year-old boy developed hemorrhagic mucocutaneous blisters on various parts of the body leading to fetor, dysphagia, dysuria, anal pruritus, pain on defecation, and weight loss. The histopathology showed the classic features of pemphigus vulgaris, and direct immunofluorescence showed intercellular deposition of IgG and C3 in the epidermis. Circulating pemphigus antibodies were also detected. He was treated with a combination of systemic prednisone and dapsone which induced a rapid remission and controlled the disease well. He has been in remission for 1 year and 7 months with no immunosuppressive therapy except for the use of topical agents for the oral lesions. An adjuvant to corticosteroids has been used only once before in children with pemphigus vulgaris under the age of 12 years. This is the third and the youngest child in the literature treated in this fashion.
journal_name
Pediatr Dermatoljournal_title
Pediatric dermatologyauthors
Bjarnason B,Skoglund C,Flosadóttir Edoi
10.1046/j.1525-1470.1998.1998015381.xsubject
Has Abstractpub_date
1998-09-01 00:00:00pages
381-3issue
5eissn
0736-8046issn
1525-1470journal_volume
15pub_type
杂志文章abstract::Connective tissue nevi of collagen type are now classified in four major subtypes. In addition to the clinicopathological features of papulolinear collagenoma, which is considered as a variant of isolated collagen harmatoma, the case we present has a unique arborizing pattern. ...
journal_title:Pediatric dermatology
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journal_title:Pediatric dermatology
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journal_title:Pediatric dermatology
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journal_title:Pediatric dermatology
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journal_title:Pediatric dermatology
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journal_title:Pediatric dermatology
pub_type: 杂志文章,评审
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更新日期:1996-07-01 00:00:00
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journal_title:Pediatric dermatology
pub_type: 杂志文章
doi:10.1111/pde.13779
更新日期:2019-05-01 00:00:00
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journal_title:Pediatric dermatology
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journal_title:Pediatric dermatology
pub_type: 杂志文章,评审
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更新日期:2001-03-01 00:00:00
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journal_title:Pediatric dermatology
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journal_title:Pediatric dermatology
pub_type: 杂志文章,评审
doi:10.1046/j.1525-1470.2002.00229.x
更新日期:2002-11-01 00:00:00
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journal_title:Pediatric dermatology
pub_type: 杂志文章
doi:10.1111/j.1525-1470.1992.tb00318.x
更新日期:1992-03-01 00:00:00
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journal_title:Pediatric dermatology
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doi:10.1046/j.1525-1470.2000.01727.x
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更新日期:2020-03-01 00:00:00
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journal_title:Pediatric dermatology
pub_type: 杂志文章
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更新日期:1988-05-01 00:00:00
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journal_title:Pediatric dermatology
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更新日期:2014-01-01 00:00:00
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journal_title:Pediatric dermatology
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doi:10.1111/pde.14339
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journal_title:Pediatric dermatology
pub_type: 杂志文章
doi:10.1111/pde.13778
更新日期:2019-05-01 00:00:00
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journal_title:Pediatric dermatology
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pub_type: 杂志文章,评审
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更新日期:2015-09-01 00:00:00
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journal_title:Pediatric dermatology
pub_type: 杂志文章
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更新日期:1987-11-01 00:00:00
abstract::Oral-facial-digital syndrome type 1 (OMIM #311200) is an X-linked dominant, developmental disorder. Among the 13 described clinical variants of oral-facial-digital syndrome, oral-facial-digital syndrome type 1 is of significance to dermatologists due to presence of congenital milia and hypotrichosis, not described in ...
journal_title:Pediatric dermatology
pub_type: 杂志文章
doi:10.1111/j.1525-1470.2010.01334.x
更新日期:2010-11-01 00:00:00