Abstract:
:Kaposiform hemangioendothelioma (KH) is a rare tumor of vascular origin that commonly affects the cutaneous tissues of the extremities. It can, however, affect the abdomen, thorax, head, or neck. Compared with juvenile hemangiomas, which tend to regress, KH tumors are locally aggressive and usually persist. Associated morbidity and mortality rates range from 12 to 30 % and typically are related to either compressive effects on surrounding vital structures or effects of the Kasabach-Merritt phenomenon [10, 11, 13]. To our knowledge, this report is the first to describe KH presenting as a primary intracardiac tumor.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Beaton A,Kuttler T,Hassan A,Nath DS,Reyes C,Jonas RA,Martin GRdoi
10.1007/s00246-012-0280-1subject
Has Abstractpub_date
2013-01-01 00:00:00pages
194-7issue
1eissn
0172-0643issn
1432-1971journal_volume
34pub_type
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