Alzheimer's disease neuropathologic changes in semantic dementia.

abstract：:Acute and complete ischemia of the hippocampi represents a rare cause of amnesia. This paper describes the features of four such cases presenting to a single tertiary care center over a 3-year period. Interestingly, in three instances, toxicology screening was positive for opioids at the time of presentation, while in...

journal_title：Neurocase

authors： Small JE,Butler PM,Zabar Y,Barash JA

更新日期：2016-10-01 00:00:00

abstract：:The delay between cardiac arrest and brain MRI is usually extremely different in the few cerebral imaging studies assessing the affected brain areas. We report an unusual case of loss of psychic self-activation appeared immediately after a cardiac arrest in a middle age patient. The first brain MRI, one month after th...

journal_title：Neurocase

authors： Martinaud O,Le Goff F,Carlier J,Pouliquen D,Gérardin E,Savouré A

更新日期：2019-01-01 00:00:00

abstract：:Creatine transporter deficit (CT1) is an inherited metabolic disorder that causes mental retardation, epilepsy, speech, language and behavioral deficits. Until now, no treatment has been proven to be successful for this condition. We describe 1-year follow-up study of a child, aged 9.6 years, with CT1 defect, on oral ...

journal_title：Neurocase

authors： Chilosi A,Leuzzi V,Battini R,Tosetti M,Ferretti G,Comparini A,Casarano M,Moretti E,Alessandri MG,Bianchi MC,Cioni G

更新日期：2008-01-01 00:00:00

abstract：:Patients with memory disorders have severely restricted learning and memory. For instance, patients with anterograde amnesia can learn motor procedures and retain some restricted ability to learn new words and factual information. However, such learning is inflexible and frequently inaccessible to conscious awareness....

journal_title：Neurocase

authors： Olson IR,Berryhill ME,Drowos DB,Brown L,Chatterjee A

更新日期：2010-06-01 00:00:00

abstract：:The purpose of this study was to determine if differential reading and spelling mechanisms were involved in a Japanese patient with aphasia. In our case, the patient scored low on all of the administered reading tasks, suggesting that both the reading lexical and non-lexical routes were impaired. In contrast, his writ...

journal_title：Neurocase

authors： Hashimoto K,Uno A

更新日期：2016-06-01 00:00:00

abstract：:A 68-year-old man had a cerebral infarction affecting the right parietal lobe, right insula, and the left prefrontal region. On admission, left hand tactile extinction was noted when the hands were placed both in anatomical and crossed positions, but was noted only in crossed positions from day 20 and later. Five mont...

journal_title：Neurocase

authors： Asada T,Takeda K,Okiyama R,Isozaki E,Fukuyama H

更新日期：2014-01-01 00:00:00

abstract：:We report a 4-year-old child with severe semi-lobar holoprosencephaly (HPE) not expected to survive after birth. Magnetic resonance imaging (MRI) revealed agenesis of the corpus callosum, absence of the third ventricle, fused thalami and basal ganglia. To investigate sensory function, visual, auditory and somatosensor...

journal_title：Neurocase

authors： Liasis A,Hildebrand D,Clark C,Katz X,Gunny R,Stieltjes B,Taylor D

更新日期：2009-01-01 00:00:00

abstract：:In this paper we report the results of a longitudinal study which examined memory for a single routine activity of daily living in people with dementia of the Alzheimer type. We assessed memory in a natural setting, visiting volunteers in their homes. We video-taped performance on the selected task and analysed the re...

journal_title：Neurocase

authors： Rusted J,Sheppard L

更新日期：2002-01-01 00:00:00

abstract：:Subject PI demonstrated superior memory using a variant of a Method of Loci (MOL) technique to recite the first digits of the mathematical constant pi to more than 2(16) decimal places. We report preliminary behavioral, functional magnetic resonance imaging (fMRI), and brain volumetric data from PI. fMRI data collecte...

journal_title：Neurocase

authors： Raz A,Packard MG,Alexander GM,Buhle JT,Zhu H,Yu S,Peterson BS

更新日期：2009-10-01 00:00:00

abstract：:A case report is presented detailing the successful use of awake intraoperative memory testing while using white matter stimulation in order to isolate the fornix tracks involved in memory function. The identification of the white matter tracks of the fornix that were involved in memory function was used to tailor the...

journal_title：Neurocase

authors： Brandling-Bennett EM,Bookheimer SY,Horsfall JL,Moftakhar P,Sedrak M,Barkulis CT,Gertsch JH,MacDougall MG,Boucharel W,Nuwer MR,Bergsneider M

更新日期：2012-02-01 00:00:00

abstract：:An adult female complained of enlargement of right eyes in other people. Diffusion-weighted imaging detected an abnormal high-intensity area in the region from the splenium of the corpus callosum to the major forceps on the right side. The patient reported that right eyes appeared larger in size, which suggested proso...

journal_title：Neurocase

authors： Ogawa K,Akimoto T,Takahashi K,Hara M,Morita A,Kamei S,Nakajima H,Fujishiro M,Suzuki Y,Soma M,Shikata E,Futamura A,Kawamura M

更新日期：2020-10-01 00:00:00

abstract：:Physical symptoms of myoclonus dystonia due to epsilon-sarcoglycan mutations are well documented; however, the progression of neuropsychiatric and cognitive symptoms remains unclear. We present a case of a 34-year-old woman with early childhood onset of myoclonic jerks, dystonic posture and developmental delay due to ...

journal_title：Neurocase

authors： Multani N,Moro E,Lang A,Zurowski M,Duff Canning S,Tartaglia MC

更新日期：2016-01-01 00:00:00

abstract：:Oculocutaneous albinism (OCA) is a group of autosomal recessive disorders characterized by impairment in the melanin synthesis. We report two siblings with OCA who presented with symptoms of autism spectrum disorder and attention deficit hyperactivity disorder (ADHD). Ocular side effects occured after methylphenidate ...

journal_title：Neurocase

authors： Ünsel Bolat G

更新日期：2020-12-01 00:00:00

abstract：:We report the case of a 71 year-old female patient (DC) with a left parietal lesion resulting in a peripheral dysgraphia essentially characterized by difficulties in letter sequences writing. The aim of our experiments was to analyze the influence of motor difficulties on the visual perception of both writing and reac...

journal_title：Neurocase

authors： Chary C,Méary D,Orliaguet JP,David D,Moreaud O,Kandel S

更新日期：2004-06-01 00:00:00

abstract：:The accurate prediction, at a pre-dementia stage of Alzheimer's disease (AD), of the subsequent clinical evolution of patients would be a major breakthrough from both therapeutic and research standpoints. Amnestic mild cognitive impairment (MCI) is presently the most common reference to address the pre-dementia stage ...

journal_title：Neurocase

authors： Chételat G,Eustache F,Viader F,De La Sayette V,Pélerin A,Mézenge F,Hannequin D,Dupuy B,Baron JC,Desgranges B

更新日期：2005-02-01 00:00:00

abstract：:We report a patient presenting with clinical features of logopenic variant primary progressive aphasia (lvPPA) who was later diagnosed with probable dementia with Lewy bodies. LvPPA is a neurodegenerative disease that is characterized by anomia, word-finding difficulty, impaired comprehension, and phonological errors....

journal_title：Neurocase

authors： Boes S,Botha H,Machulda M,Lowe V,Graff-Radford J,Whitwell JL,Utianski RL,Duffy JR,Josephs KA

更新日期：2020-10-01 00:00:00

abstract：:Recent lesion studies have shown that left hemisphere lesions often give rise to frank sign language aphasias in deaf signers, whereas right hemisphere lesions do not, suggesting similar patterns of hemispheric asymmetry for signed and spoken language. We present here a case of a left-handed, deaf, life-long signer wh...

journal_title：Neurocase

authors： Pickell H,Klima E,Love T,Kritchevsky M,Bellugi U,Hickok G

更新日期：2005-06-01 00:00:00

abstract：:Primary progressive apraxia of speech (PPAOS) is a neurodegenerative disorder in which AOS is the sole presenting complaint. We report clinical and neuroimaging data spanning 10 years from disease onset-to-death in a 49 year-old male PPAOS patient, DY, who died with corticobasal degeneration. He presented with AOS wit...

journal_title：Neurocase

authors： Tetzloff KA,Duffy JR,Strand EA,Machulda MM,Boland SM,Utianski RL,Botha H,Senjem ML,Schwarz CG,Josephs KA,Whitwell JL

更新日期：2018-04-01 00:00:00

abstract：:Topographical disorientation is usually described in patients who have lost the ability to orient themselves as a consequence of acquired focal brain damage. Here, we describe the case of a 20-year-old woman with a congenital brain malformation who has never been able to orient herself within the environment. We addre...

journal_title：Neurocase

authors： Iaria G,Incoccia C,Piccardi L,Nico D,Sabatini U,Guariglia C

更新日期：2005-12-01 00:00:00

abstract：:Dissociative identity disorder (DID) is probably the most disputed of psychiatric diagnoses and of psychological forensic evaluations in the legal arena. The iatrogenic proponents assert that DID phenomena originate from psychotherapeutic treatment while traumagenic proponents state that DID develops after severe and ...

journal_title：Neurocase

authors： Reinders AA

更新日期：2008-01-01 00:00:00

abstract：:Neurodegenerative diseases are caused by aggregation of specific proteins that catalyze a cascade of changes that ultimately lead to neurodegeneration. This concept guides current diagnostic approaches, as well as clinical trials, that focus on detecting or removing amyloid or tau from the brain. The semantic variant ...

journal_title：Neurocase

authors： Caplan A,Marx G,Elofson J,Lis C,Grinberg L,Miller B,Rosen H

更新日期：2018-04-01 00:00:00

abstract：:BVR was 77 years old when he sustained a large posterior cerebral artery territory infarct. Medical, cognitive and functional data collected on four occasions over 10 years initially revealed circumscribed neurological signs, no functional or cognitive deficits. BVR became significantly impaired only after two other s...

journal_title：Neurocase

authors： Piguet O,Bennett HP,Waite LM,Kril JJ,Creasey H,Anthony Broe G,Halliday GM

更新日期：2006-04-01 00:00:00

abstract：:The psychoses of epilepsy are well recognized complications of seizure disorders, diagnosed easily from the history. However, in the absence of recognized seizures, the diagnosis can be challenging. We present a 27-year-old female, who suffered a treatment refractory psychosis for 6 years. She did not report, or dis...

journal_title：Neurocase

authors： Needham E,Hamelijnck J

更新日期：2012-01-01 00:00:00

abstract：:A 54-year-old art teacher, experienced a right putaminal hemorrhage, and thereafter suffered severe left hemiplegia and unilateral spatial neglect, and was transferred to the rehabilitation department of the University Hospital 1 month after the onset. Although the unilateral spatial neglect was improving, the patient...

journal_title：Neurocase

authors： Kondo M,Mori T,Makino K,Okazaki T,Hachisuka K

更新日期：2012-06-01 00:00:00

abstract：:Neglect dyslexia is a reading disorder often associated with right-sided brain lesions. In reading single words, errors are mostly substitutions or omissions of letters that occupy the left-sided positions. Typically, these errors have been thought to depend on a single mechanism. Conversely, we propose that they are ...

journal_title：Neurocase

authors： Martelli M,Arduino LS,Daini R

更新日期：2011-01-01 00:00:00

abstract：:Previous research suggests that the noradrenergic system modulates flexibility of access to the lexical-semantic network, with propranolol benefiting normal subjects in lexical-semantic problem solving tasks. Patients with Broca's aphasia with anomia have impaired ability to access appropriate verbal output for a give...

journal_title：Neurocase

authors： Beversdorf DQ,Sharma UK,Phillips NN,Notestine MA,Slivka AP,Friedman NM,Schneider SL,Nagaraja HN,Hillier A

更新日期：2007-08-01 00:00:00

abstract：:Chediak-Higashi syndrome (CHS) is a rare autosomal disorder characterized by immunodeficiency, albinism, and progressive neurologic abnormalities. While survivors of the childhood-onset disease are known to exhibit learning disabilities and neuropsychiatric disorders followed by middle-age dementia, we lack detailed d...

journal_title：Neurocase

authors： Yliranta A,Mäkinen J

更新日期：2020-12-09 00:00:00

abstract：:We report a case of frontotemporal dementia caused by a novel MAPT mutation (Q351R) with a remarkably long amnestic presentation mimicking familial Alzheimer's disease. Longitudinal clinical, neuropsychological and imaging data provide convergent evidence for predominantly bilateral anterior medial temporal lobe invol...

journal_title：Neurocase

authors： Liang Y,Gordon E,Rohrer J,Downey L,de Silva R,Jäger HR,Nicholas J,Modat M,Cardoso MJ,Mahoney C,Warren J,Rossor M,Fox N,Caine D

更新日期：2014-01-01 00:00:00

abstract：:It is a common finding in tests of false recognition that amnesic patients recognize fewer related lures than healthy controls, and this has led to assumptions that gist memory is damaged in these patients (Schacter, Verfaellie, & Anes, 1997, Neuropsychology, 11; Schacter, Verfaellie, Anes, & Racine, 1998, Journal of ...

journal_title：Neurocase

authors： Nissan J,Abrahams S,Sala SD

更新日期：2013-01-01 00:00:00

abstract：:A hexanucleotide repeat expansion in the chromosome 9 open reading frame 72 (C9ORF72) gene was recently discovered as the cause underlying frontotemporal degeneration (FTD) and/or amyotrophic lateral sclerosis (ALS) linked to chromosome 9 (c9FTD/ALS). In this atypical case of c9FTD/ALS, the proband presented with amne...

journal_title：Neurocase

authors： Adeli A,Savica R,Lowe VJ,Vemuri P,Knopman DS,Dejesus-Hernandez M,Rademakers R,Fields JA,Crum BA,Jack CR,Petersen RC,Boeve BF

更新日期：2014-01-01 00:00:00