Abstract：
INTRODUCTION:'Sword stroke' linear scleroderma, which is better known as linear scleroderma en coup de sabre (LSCS), is a rare disease with an uncertain causation that is characterised by progressive craniofacial focal atrophy and is, at least in part, different from Parry-Romberg syndrome (PRS). CASE REPORTS:Here, we report on the cases of 3 patients with LSCS (2 females and 1 male, with a mean age of 40 years). The main neurological symptoms were headache and seizures. Although different alterations were observed in the X-ray images, they were all ipsilateral to the coup de sabre. Histopathological evidence for gliosis and mixed perivascular inflammatory infiltrate was found in the study of a biopsy specimen taken from one female. Cerebrovascular involvement was seen in another patient, as highlighted by the observation of an earlier subclinical cerebellar infarct and occlusion of the superior cerebellar artery in the absence of any other possible causation. CONCLUSIONS:When it affects the central nervous system, the clinical and radiological presentation of LSCS is heterogeneous. Both the imaging studies carried out during the clinical control and the histopathological findings suggest a focal inflammatory process that can be progressive. The arterial involvement is probably due to a non-atherosclerotic, occlusive and chronic inflammatory disease of the peripheral vessels.
journal_name
Rev Neuroljournal_title
Revista de neurologiaauthors
Ruiz-Sandoval JL,Romero-Vargas S,Gutierrez-Aceves GA,Garcia-Navarro V,Bernard-Medina AG,Cerda-Camacho F,Riestra-Castaneda R,Gonzalez-Cornejo Ssubject
Has Abstractpub_date
2005-11-01 00:00:00pages
534-7issue
9eissn
0210-0010issn
1576-6578pii
rn2004554journal_volume
41pub_type
杂志文章abstract：INTRODUCTION AND OBJECTIVE:We analyze the main factors influencing the time delay between onset and admission to the hospital in acute stroke. PATIENTS AND METHODS:Consecutive series of 1,344 patients with acute stroke or transient ischemic attack admitted at two reference hospitals of Valencia and included at the sam...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：1998-12-01 00:00:00
abstract：AIMS:The aim of this work was to study the cranial trepanations and deformations carried out by the ancient Paraca, Huari, Tiahuanaco and Inca cultures. To do so, we conducted a field study involving visits to archaeological remains and anthropological museums on the Andean plateau and the Peruvian coast. DEVELOPMENT:...
journal_title：Revista de neurologia
pub_type： 历史文章,杂志文章
doi：
更新日期：2004-04-16 00:00:00
abstract：INTRODUCTION:Transcranial Doppler (TCD) is a new technique which is becoming increasingly used in neurology and is highly dependent on the user. OBJECTIVE:To evaluate the reliability of TCD in our hospital. PATIENTS AND METHODS:During a five month period, all patients who had a cerebral angiogram done, also had DTC w...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2001-09-16 00:00:00
abstract：INTRODUCTION:Clinical, electrophysiological, genetic and biochemical deficiencies variability were evaluated in 52 patients diagnosed of mitochondrial respiratory chain diseases (MRCD). PATIENTS AND METHODS:26 men and 26 women, aged 19 to 79 years, were tested by clinical examination, electrophysiological techniques, ...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2005-10-16 00:00:00
abstract：AIMS:The purpose of this study is to review different aspects of mitochondrial myopathies. DEVELOPMENT:Mitochondrial DNA is different to that found in the nucleus and is generally inherited through the mother. There are from 2 to 10 copies per mitochondrion and hundreds or thousands of mitochondria per cell. It contai...
journal_title：Revista de neurologia
pub_type： 杂志文章,评审
doi：
更新日期：2003-10-16 00:00:00
abstract：INTRODUCTION:Cerebral infarction (CI) can be classified aetiologically in several different ways using explicit diagnostic criteria. However, the extent to which these diagnostic criteria are actually implemented in clinical practice is unknown. Aims. The aim of this study was to analyse the management and use of diagn...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2003-03-01 00:00:00
abstract：INTRODUCTION:After Zika virus outbreak and the increase in the incidence of Guillain-Barre syndrome (GBS), the causal relationship has been studied, however a full etiological correlation has not been found. PATIENTS AND METHODS:From January 1 to December 31, 2017, patients with GBS were included. In addition to the b...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2018-09-16 00:00:00
abstract：:The aim of the study is a reflection on the current standing of giftedness research and the effectiveness of gifted education in order to facilitate its optimal developmental trajectory from potential to eminence. The necessity of rethinking high intellectual ability as a developmental process is exposed from a new pa...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2015-02-25 00:00:00
abstract：INTRODUCTION:Dystonia is defined as a sustained co-contraction of agonistic and antagonistic muscles that can cause twisting, twitching and abnormal postures. Occupational dystonias are included in a special group of pathologies that are secondary to a repeated effort related to the professional activity carried out by...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2003-10-01 00:00:00
abstract：INTRODUCTION AND DEVELOPMENT:Frontal lobe, more specifically prefrontal cortex, is one of the brain regions that undergoes more protracted ongoing development. The wider the developmental window of one brain structure, the more vulnerable the functions related to it. Hence, executive functions, which are mediated by pr...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2004-07-16 00:00:00
abstract：TITLE:GNAO1: un nuevo gen a considerar en la distonia temprana de la infancia. : ...
journal_title：Revista de neurologia
pub_type： 信件,评审
doi：
更新日期：2018-05-01 00:00:00
abstract：:Studies of vision using electrophysiological techniques are tests which record functional alterations in very early phases of a disease. Full field flash ERG evaluates the integrity of the cones, rods and bipolar cells. It is obtained by photopsic stimulation with Ganzfeld and contact lens corneal electrodes or, alter...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2003-02-15 00:00:00
abstract：INTRODUCTION:Sleep and epilepsy have strong reciprocal influences and this is true for all kinds of epilepsies. The interictal paroxysmal activity increases in slow wave sleep and the localization of the primary epileptogenic area is more reliable in paradoxical sleep. DEVELOPMENT:From a practical point of view, an al...
journal_title：Revista de neurologia
pub_type： 杂志文章,评审
doi：
更新日期：2004-01-16 00:00:00
abstract：INTRODUCTION:The hyperperfusion syndrome (HS) is described as an infrequent complication of carotid endarterectomy. It may also occur in percutaneous transluminal carotid angioplasty with a similar causal mechanism and clinical features to those seen in HS related to carotid endarterectomy. CLINICAL CASE:We describe t...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：1999-11-16 00:00:00
abstract：INTRODUCTION:We describe a patient diagnosed as suffering from a skull base osteochondroma which affected the atlantooccipital joint and originated in the occipital condyle. It also displayed a growth toward the foramen magnum, which was resected using an extreme lateral transcondylar approach. CASE REPORT:Patient age...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2003-01-16 00:00:00
abstract：INTRODUCTION:Critical illness patients may show marked weakness acquired in the Intensive Care Unit (ICU). There are some disagreements about the myopathic versus neuropathic damage in this condition, presumably due to the lack of reliable diagnostic criteria. AIMS:To report the neurophysiological findings in critical...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2010-06-16 00:00:00
abstract：AIM:To identify the clinical and psychosocial factors of a Colombian cohort of patients with juvenile myoclonic epilepsy and its relation to crisis control. PATIENTS AND METHODS:Retrospective cohort study of patients over 14 years of age with a diagnosis of juvenile myoclonic epilepsy, with 12 months of follow-up in a...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：10.33588/rn.6911.2019305
更新日期：2019-12-01 00:00:00
abstract：:Several predispocitional and genetic factors are thought to be involved in the etiology of Alzheimer s disease (AD). Except for age, there is no consensus among researchers about the factors that can best predict AD. Some studies have found that, older women, cerebrovascular risk factors (hypertension, ischemic heart ...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2003-07-16 00:00:00
abstract：INTRODUCTION:Almost three out of every four people in the world who suffer a fatal stroke live in developing countries. A number of different tropical diseases may appear in Europe in the coming years as a consequence of the demographic change that is being brought about by migratory flows. We review the main infectiou...
journal_title：Revista de neurologia
pub_type： 杂志文章,评审
doi：
更新日期：2007-06-16 00:00:00
abstract：INTRODUCTION AND OBJECTIVE:It is well known that in aged animals cognitive deficit occurs, homologous with that occurring in Alzheimer's disease in humans, and as has been shown in others species, this may be attenuated by administration of nerve growth factor (NGF). Therefore the basic aim of this study was to make an...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：1999-04-01 00:00:00
abstract：INTRODUCTION:The signals obtained during conventional needle examination are usually assessed subjectively by the neurophysiologist. Buchthal's approach allows quantification of several motor unit parameters during mild effort. DEVELOPMENT:The automatic methods of analysis of the EMG interference pattern (IP), in part...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：1999-03-16 00:00:00
abstract：INTRODUCTION:The recent discovery of the dystrophin-associated complex of glycoproteins led to the delineation of sarcoglycanopathies, a phenotypically similar to dystrophinopathies group of clinically heterogeneous and progressive muscular dystrophies. The objective of this paper is to report the clinical, biochemical...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2001-04-01 00:00:00
abstract：TITLE:Equivalente migrañoso de inicio tardío con aura prolongada y alteración de la perfusión cerebral. : ...
journal_title：Revista de neurologia
pub_type： 信件
doi：10.33588/rn.7011.2019333
更新日期：2020-06-01 00:00:00
abstract：INTRODUCTION:The current advances in the field of human genetics allow for the development of alternative therapies for the treatment of diseases affecting the central nervous system (CNS). One of the most promising new therapies is the use of therapeutic genes or gene therapy. OBJECTIVE:To briefly review the recent a...
journal_title：Revista de neurologia
pub_type： 杂志文章,评审
doi：
更新日期：2002-07-16 00:00:00
abstract：OBJECTIVE:To review the current treatment and usefulness of lamotrigine in absence seizures. DEVELOPMENT:Absence seizures are classified amongst the generalized epilepsies. They are defined as a transient loss of consciousness of sudden onset and recovery characteristically associated with generalized spike-and-wave d...
journal_title：Revista de neurologia
pub_type： 杂志文章,评审
doi：
更新日期：2001-02-01 00:00:00
abstract：OBJECTIVE:A number of studies suggest the existence of 'oxidative stress' in the substantia nigra from parkinsonian patients. If 'oxidative stress' should be relevant in the pathogenesis of Parkinson's disease (PD), the consumption of antioxidant or prooxidant substances in the diet could theoretically influence the ri...
journal_title：Revista de neurologia
pub_type： 杂志文章,评审
doi：
更新日期：1999-10-16 00:00:00
abstract：INTRODUCTION:The development of scientific advances, constantly opening new frontiers of knowledge, leads to increasing complexity and specialization. DEVELOPMENT:The conflict between the never ending medical specialization and the opposite tendency, which is based mostly on economic grounds, prevents the acquisition ...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2002-08-01 00:00:00
abstract：INTRODUCTION:Attention deficit hyperactivity disorder (ADHD) is one of the most frequent reasons for visits to neuropaediatric services. Although the clinical criteria are well established, the medical history is probably not examined with enough care and the most decisive symptoms go unnoticed. AIM. To review a clinic...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2008-01-01 00:00:00
abstract：INTRODUCTION:Progressive cerebral polidystrophy or Alpers syndrome is a clinico-pathological picture, with no specific biological marker, characterized by involvement mainly of the cerebral grey matter and which shows clinically as a rapidly progressive encephalopathy with intractable seizures, usually myoclonic. The t...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2000-12-01 00:00:00
abstract：TITLE:Actos reiterativos y ensayo-error. : ...
journal_title：Revista de neurologia
pub_type： 杂志文章
doi：
更新日期：2016-01-01 00:00:00
