Abstract:
:This study explored self concepts in matched groups of adolescents and adults with Williams syndrome (WS) and Prader-Willi syndrome (PWS), using Damon and Hart's semi-structured interview. The main findings were that the WS participants were more productive in their responses to the interview, providing more self characteristics. The WS group also used more social and psychological categories in describing their self concept, and their responses were in general at a higher level than the responses for the PWS group. There were significant age-group differences, with the adolescents offering more self descriptions that were coded as physical and active, whereas the adults gave more social and psychological responses. Different themes were emphasized in the interviews from the two groups. These themes reflected the distinct phenotypes associated with these disorders, the participants life experiences, and their overall attitudes toward their syndrome.
journal_name
Res Dev Disabiljournal_title
Research in developmental disabilitiesauthors
Plesa-Skwerer D,Sullivan K,Joffre K,Tager-Flusberg Hdoi
10.1016/j.ridd.2003.05.003subject
Has Abstractpub_date
2004-03-01 00:00:00pages
119-38issue
2eissn
0891-4222issn
1873-3379pii
S0891422204000083journal_volume
25pub_type
临床试验,杂志文章,随机对照试验abstract::Programmed training in identity matching to sample was given to six participants who had severe mental retardation, mental age-equivalent scores of 3.0 years or less, and histories of failures in prior assessments and training attempts with standard procedures. An intermediate goal of the training program was to estab...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/s0891-4222(98)00009-2
更新日期:1998-07-01 00:00:00
abstract::There is an abundance of research investigating Autism Spectrum Disorders (ASD) in children; however, little emphasis has been placed on ASD in adults, especially in regards to comorbid psychopathology. Although scales are available that measure comorbidity in adults with ID, what is needed are scales that measure com...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2009.05.004
更新日期:2009-11-01 00:00:00
abstract:BACKGROUND:Research has demonstrated evidence for increased perceptual capacity in autism: autistic people can process more information at any given time than neurotypical individuals. The implications of this for educating autistic pupils have not been investigated. For example, this ability to process more informatio...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2018.12.006
更新日期:2019-02-01 00:00:00
abstract::Toys that provoke the use of both hands are required to develop a test of bimanual performance in children 8-18 months with unilateral cerebral palsy (Mini-AHA). To choose the toys, a conceptual model based on perception-action theory and object use was used to guide a literature review. Evidence was sought for three ...
journal_title:Research in developmental disabilities
pub_type: 杂志文章,评审
doi:10.1016/j.ridd.2011.09.012
更新日期:2012-01-01 00:00:00
abstract:BACKGROUND:People with intellectual and developmental disabilities (IDD) are at risk of developing long term health conditions, and a preventative health agenda research is emerging. However, little is known about the recruitment settings, delivery contexts, intervention techniques and outcomes of health promotion prog...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2020.103592
更新日期:2020-02-05 00:00:00
abstract::Little information is available on the prevalence and determinants of lifestyle related risk factors for poor health (obesity, poor diet, physical inactivity, smoking and alcohol abuse) among people with intellectual disabilities. This study reports the prevalence of these risk factors for 500 people with intellectual...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/s0891-4222(00)00053-6
更新日期:2000-11-01 00:00:00
abstract::The current study focuses on the characteristics of older people with intellectual disabilities with the lowest frailty levels. Frailty is an increased risk of adverse health outcomes and dependency. Older adults with intellectual disabilities (ID) show more signs of early frailty than the general population. Knowledg...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2013.10.016
更新日期:2014-01-01 00:00:00
abstract::Infants born preterm and/or with low birth weight may present a clinical condition of organic instability and usually face a long period of hospitalization in the Neonatal Intensive Care Units, being exposed to biopsychosocial risk factors to their development due to decreased spontaneous movement and excessive sensor...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2014.09.018
更新日期:2015-01-01 00:00:00
abstract::The relation between psychiatric symptoms and different types of challenging behaviour in adults with mental retardation was investigated, using an instrument designed for use by non-specialist informants. A sample of 165 persons with mental retardation was surveyed for the presence of psychiatric symptoms, level of m...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/s0891-4222(03)00060-x
更新日期:2003-09-01 00:00:00
abstract::Over the last decade a significant increase in the life expectancy of people with Down syndrome (DS) has been observed, which has caused a higher incidence of morbidity as they age. However, there is a lack of literature regarding morbidity and hospitalization of adults with DS. Analysis of 297 hospitalizations of 120...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2011.09.026
更新日期:2012-03-01 00:00:00
abstract:BACKGROUND:Although adults are known to have sensory sensitivity differences, existing sensitivity scales have been mostly developed for children. The limited number of adult scales measure social/emotional features and modalities together. AIMS:To develop scales for adults that evaluate visual, auditory and somatosen...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2020.103612
更新日期:2020-05-01 00:00:00
abstract::Two young children with mental retardation displayed inconclusive patterns of destructive behavior when a functional analysis was conducted using the procedures described by Iwata et al. (1982/1994). A second functional analysis incorporated modifications to the social attention condition that were based on interview ...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/s0891-4222(98)00031-6
更新日期:1999-01-01 00:00:00
abstract::Recent studies indicate that children with intellectual disabilities have functional limitations primarily in the phonological loop of working memory (Baddeley, 1986). These findings are indicative of a specific structural deficit. Building on this research, the present study examines whether it is possible to identif...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2011.03.022
更新日期:2011-09-01 00:00:00
abstract:BACKGROUND:While pain is reportedly more prevalent in more functionally impaired children with cerebral palsy, information is scant in those with poor communication skills. METHODS:Young people (4-27 years) with severe forms of cerebral palsy were recruited from a population-based register. The Child Health Questionna...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2016.10.006
更新日期:2017-01-01 00:00:00
abstract::This study examines the views of teachers and parents on critical issues concerning their collaboration in the education of children with ASD. For the purposes of this study, a total of 171 teachers and 50 parents of children with ASD, attending mainstream or special primary school units, were randomly selected in Gre...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2016.04.011
更新日期:2016-08-01 00:00:00
abstract::Functional assessment is a method to identify the relationships between a behavior of interest and an individual's environment. Traditional methods for functional assessment have relied on experimental techniques in which analog sessions are designed to replicate conditions in the individual's environment. However, th...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/s0891-4222(00)00036-6
更新日期:2000-05-01 00:00:00
abstract::Williams-Beuren syndrome (WBS) is a genetically determined neurodevelopmental disorder caused by a heterozygous deletion of 26-28 genes on chromosome band 7q11.23. During the past few years, researchers and clinicians have significantly contributed to define the phenotype of the syndrome, including its cognitive and b...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2010.12.005
更新日期:2011-03-01 00:00:00
abstract::A high percentage of children with cerebral palsy (CP) have difficulty keeping up with the handwriting demands at school. Previous studies have addressed the effects of proper sitting and writing tool on writing performance, but less on body biomechanics. The aim of this study was to investigate the influence of lower...
journal_title:Research in developmental disabilities
pub_type: 杂志文章,随机对照试验
doi:10.1016/j.ridd.2012.12.019
更新日期:2013-04-01 00:00:00
abstract::Adults with intellectual and developmental disabilities are frequently abused in dating and partnered relationships. The Friendships and Dating Program (FDP) was developed to prevent violence in dating and partnered relationships and to teach social skills needed to develop healthy, meaningful relationships among this...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2011.08.016
更新日期:2012-01-01 00:00:00
abstract:BACKGROUND:The present study focused on typically developing siblings (TDS) in emerging adulthood of individuals with autism spectrum disorder (ASD) and sought insight into how gender may interact with positive and negative affects in this population. In addition, we aimed to explore the gender differences as a moderat...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2020.103829
更新日期:2021-01-01 00:00:00
abstract::Information was collected from 88 staff about their observations of the occurrence and frequency of challenging behaviors in 22 individuals with developmental disabilities with whom they worked. Staff reports suggested considerable variability in challenging behavior in the presence of different staff and, from day to...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/s0891-4222(01)00069-5
更新日期:2001-05-01 00:00:00
abstract::Knowledge in the area of developmental disabilities has been expanding rapidly. One area that has received particular attention is the topic of related comorbid conditions. This phenomenon is not exclusive to the field of developmental disabilities. However, research with this population is of recent origin. The purpo...
journal_title:Research in developmental disabilities
pub_type: 杂志文章,评审
doi:10.1016/j.ridd.2013.09.043
更新日期:2014-01-01 00:00:00
abstract::Dopamine active transporter gene (DAT1) is a candidate gene associated with attention-deficit/hyperactivity disorder (ADHD). The DAT1 variable number tandem repeat (VNTR)-3' polymorphism is functional and 9R carriers have been shown to produce more DAT than 10R homozygotes. We used functional magnetic resonance imagin...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2019.103430
更新日期:2019-09-01 00:00:00
abstract:BACKGROUND:Children with autism spectrum disorder (ASD) often suffer from sleep problems that in turn correlate with behavioral problems. However, in Japan, there have been few studies of sleep problems in children with ASD. AIMS:This study compared sleep problems in preschoolers from the community and preschoolers wi...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2015.11.002
更新日期:2016-02-01 00:00:00
abstract::The oddity performance of five preschool children at risk for mental retardation was facilitated by increasing the number of nonodd elements in a visual array. A combination intrasubject reversal and multiple baseline across subjects design indicated the internal validity of interventions designed to enhance the perce...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/0891-4222(87)90044-8
更新日期:1987-01-01 00:00:00
abstract::A multiple baseline across tasks design was used to evaluate the production effects of video self-modeling on three activities of daily living tasks of an adult male with Autism Spectrum Disorder and Intellectual Disability. Results indicated large increases in task accuracy after the production of a self-modeling vid...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2017.09.012
更新日期:2017-12-01 00:00:00
abstract::This study assessed whether two people with profound multiple disabilities and minimal motor behavior would be able to control environmental stimulation using thumb poke ability with a mouse wheel and a newly developed mouse driver (i.e., a new mouse driver replacing standard mouse driver, and turning a mouse into a p...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2009.07.001
更新日期:2009-11-01 00:00:00
abstract:BACKGROUND:Caregivers of children with fetal alcohol spectrum disorders (FASD) have elevated levels of stress, which can negatively impact family functioning and caregivers' mental and physical health. Self-care is a critical resource to address caregivers' stress. AIMS:This study describes strategies and obstacles re...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2020.103578
更新日期:2020-01-31 00:00:00
abstract::We evaluated a protocol involving two types of choice presentations for assessing leisure choice-making skills of seven older adults with severe disabilities. Initially when presented with pairs of objects representing choices, choice making was validated through demonstration of an object preference. A more complex c...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/s0891-4222(96)00044-3
更新日期:1997-03-01 00:00:00
abstract::Two students with developmental disabilities were taught to request six snack items. Requesting involved giving a graphic symbol to the trainer in exchange for the matching snack item. Following acquisition, we assessed the correspondence between requests and subsequent item selections by requiring the student to sele...
journal_title:Research in developmental disabilities
pub_type: 杂志文章
doi:10.1016/j.ridd.2005.12.002
更新日期:2007-01-01 00:00:00