Abstract:
:A patient with mixed gonadal dysgenesis showed glove and stocking-type sensory impairment and slowing of motor and sensory nerve conduction. Sural nerve biopsy revealed minifascicular formation with decreased density of myelinated fibers. As far as we are aware, this is the first report of polyneuropathy with minifascicular formation in 46XY mixed gonadal dysgenesis.
journal_name
Acta Neuropatholjournal_title
Acta neuropathologicaauthors
Umehara F,Yamaguchi N,Kodama D,Takenaga S,Kiwaki T,Sonoda Y,Arimura Y,Yamada H,Arimura K,Osame Mdoi
10.1007/s004010051085subject
Has Abstractpub_date
1999-09-01 00:00:00pages
309-12issue
3eissn
0001-6322issn
1432-0533journal_volume
98pub_type
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