Abstract:
:Case reports of four patients with therapy-resistant lesional partial epilepsies and additional foci of benign epileptic discharges of childhood, in addition to the usual electroencephalogram (EEG) changes, are presented. A family history of epileptic or febrile seizures in childhood was reported in all four patients. A distant relative of one patient, not manifesting seizures, demonstrated rolandic spikes on EEG. An abnormal pregnancy (polyhydramnion, premature pains, induced labor because of an abnormal CTG , placenta insufficiency) was reported in one patient, risk factors during birth (birth 14 days after term, placenta insufficiency) were reported in one, and bacterial meningitis at 4 weeks of age was reported in one. All patients manifested a retarded, partly severe, unfavorable infantile psychomotor development. An early seizure onset was observed in all patients (in three patients during the first year of life and in one patient during the second year). A hemifacial seizure symptomatology was seen, in addition to other symptoms, in two patients, possibly indicating the seizure pattern indicative of benign partial seizures; seizures occurred exclusively in sleep in one patient. The benign focus was never located in the lesional area. It was recorded over the same hemisphere in two patients and over the other hemisphere in the other two.
journal_name
Pediatr Neuroljournal_title
Pediatric neurologyauthors
Degen R,Holthausen H,Pieper T,Tuxhorn I,Wolf Pdoi
10.1016/s0887-8994(99)00004-1subject
Has Abstractpub_date
1999-05-01 00:00:00pages
354-9issue
5eissn
0887-8994issn
1873-5150pii
S0887899499000041journal_volume
20pub_type
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journal_title:Pediatric neurology
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journal_title:Pediatric neurology
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journal_title:Pediatric neurology
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更新日期:2006-01-01 00:00:00
abstract::The clinical phenotype of multiple acyl-CoA dehydrogenase deficiency in infancy is characterized by recurrent episodes of hypoketotic hypoglycemia and lipid storage myopathy. Brain damage has been described only as a consequence of severe and protracted hypoglycemia. We describe a child who experienced normal physical...
journal_title:Pediatric neurology
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journal_title:Pediatric neurology
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journal_title:Pediatric neurology
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journal_title:Pediatric neurology
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journal_title:Pediatric neurology
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journal_title:Pediatric neurology
pub_type: 杂志文章
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pub_type: 杂志文章
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更新日期:1994-05-01 00:00:00
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journal_title:Pediatric neurology
pub_type: 杂志文章
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更新日期:1996-11-01 00:00:00
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journal_title:Pediatric neurology
pub_type: 杂志文章
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更新日期:1993-01-01 00:00:00
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journal_title:Pediatric neurology
pub_type: 杂志文章
doi:10.1016/j.pediatrneurol.2005.12.006
更新日期:2006-07-01 00:00:00
abstract:OBJECTIVE:We describe the trends in antiepileptic drug (AED) use in children and adolescents with epilepsy in the United States. METHODS:We undertook a cross-sectional study based on Medicaid Analytic eXtract data set from 26 US states. Children and adolescents aged three to 18 years with at least one year continuous ...
journal_title:Pediatric neurology
pub_type: 杂志文章
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更新日期:2017-09-01 00:00:00
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更新日期:2020-03-01 00:00:00
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journal_title:Pediatric neurology
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journal_title:Pediatric neurology
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journal_title:Pediatric neurology
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更新日期:2008-12-01 00:00:00
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journal_title:Pediatric neurology
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更新日期:1988-05-01 00:00:00
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journal_title:Pediatric neurology
pub_type: 杂志文章
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journal_title:Pediatric neurology
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journal_title:Pediatric neurology
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abstract::Ketoacidosis is one of the common complications of Type I insulin-dependent diabetes mellitus. Several neurologic (cerebral) deficiencies have been associated with diabetic ketoacidosis, including cerebral edema with increased intracranial pressure resulting in coma; partial and generalized seizures; and cerebrovascul...
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pub_type: 杂志文章
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