Restrictive dermopathy.

Abstract:

:Restrictive dermopathy is an inherited syndrome characterized clinically by severe growth retardation, abnormal skin, characteristic facies, and multiple congenital contractures. Distinctive radiologic features include deficient mineralization of the clavicles and the skull, overtubulation and frequent modeling defects of the long bones, and occasional abnormalities of the ribs and scapulae.

journal_name

Pediatr Radiol

journal_title

Pediatric radiology

authors

Reed MH,Chudley AE,Kroeker M,Wilmot DM

doi

10.1007/BF02014983

subject

Has Abstract

pub_date

1993-01-01 00:00:00

pages

617-9

issue

8

eissn

0301-0449

issn

1432-1998

journal_volume

23

pub_type

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