[Adult neuronal ceroid lipofuscinosis (Kufs disease)--a rare cause of dementia].

Abstract:

:Kufs' disease is a very rare type of neuronal ceroid lipofuscinosis. A case of a 52 year old man with dementia is described. The cause for patient's dementia was the adult type (Kufs' disease) of neuronal ceroid lipofuscinosis. The diagnosis based on the histopathological post mortem-examination of the brain-tissue. A brother of our patient became ill with the same symptoms and at the same age of onset. So we conclude that there is a accumulation in the family.

journal_name

Psychiatr Prax

journal_title

Psychiatrische Praxis

authors

Kozian R,Kiszka T,Peter K

subject

Has Abstract

pub_date

1994-11-01 00:00:00

pages

235-7

issue

6

eissn

0303-4259

issn

1439-0876

journal_volume

21

pub_type

杂志文章
  • [Increase of In-Patient Suicides in Psychiatric Hospitals of Bavaria and Baden-Württemberg?]

    abstract::In-patient suicide research in Germany during the 70 (th) and 80 (th) years of the last century found an overall increase of in-patient suicides in psychiatric hospitals. Nowadays, more differentiated discussions of the problem are recommended. ...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2003-39742

    authors: Wolfersdorf M,Keller F,Vogl R,Vogel R

    更新日期:2003-05-01 00:00:00

  • [Management of drug dependent patients in Offenbach/Main and experiences with after-care at the psychiatric department of urban clinics].

    abstract::The report describes the inpatient and out-patient treatment facilities for alcoholics in a defined catchment area and the experience gathered by the initiation of out-patient group therapy for a group of alcoholics at the general community hospital in Offenbach/Main. The goal of the group therapy at the hospital was ...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Fiedler D

    更新日期:1994-01-01 00:00:00

  • [Friedrich Nietzsche: history of his illness. On the 100th anniversary of the death of the poet-philosopher].

    abstract::The philosopher Friedrich Nietzsche was one of the most famous patients in the psychiatric hospital Jena. Between 1889 and 1890, Otto Binswanger und Theodor Ziehen treated the progressive paralysis of Friedrich Nietzsche whose 100th anniversary of death is on 25th August 2000. After Nietzsche's death, an animated disc...

    journal_title:Psychiatrische Praxis

    pub_type: 传,历史文章,杂志文章

    doi:

    authors: Wilkes J

    更新日期:2000-04-01 00:00:00

  • [Attitude of family to clozapine].

    abstract:AIM:Evaluations of clozapine treatment by relatives of schizophrenic patients were assessed as part of an exploratory study and compared with the patients' own assessment. METHOD:46 relatives of individuals suffering from schizophrenia were questioned by means of a problem-centred interview. RESULTS:In addition to th...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Angermeyer MC,Boitz K,Löffler W,Müller P,Priebe S

    更新日期:1999-07-01 00:00:00

  • [Interactive Health Literacy, Sociodemographic Characteristics and the Uptake of Psychotherapeutic or Pharmacological Interventions - are there Social Inequalities in the Treatment of Social Anxiety Disorder?]

    abstract:AIM:The aim is to investigate the association between sociodemographic characteristics and the interactive health literacy and the time to treatment of social anxiety disorder. METHODS:An online survey of N = 311 patients was carried out (response rate 54.1 %). Descriptive statistical analysis and a logistic regressio...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/a-1294-0950

    authors: Ernstmann N,Heuser C,Halbach S,Wegener I,Rambau S,Forstner AJ,Schumacher J,Mücke M,Geiser F,Conrad R

    更新日期:2020-11-24 00:00:00

  • [Association between fear of stigma, depressive and anxiety symptoms in patients with somatoform pain disorder].

    abstract:OBJECTIVES:There is still poor acceptance for pain without somatic causes, and patients with somatoform pain disorder carry a stigma per se. The aim of this study was to identify predictors of fear of stigma including depression, anxiety and somatisation among patients with somatoform pain disorder. METHODS:132 patien...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-0032-1305096

    authors: Freidl M,Piralic-Spitzl S,Grohe N,Aigner M

    更新日期:2012-08-01 00:00:00

  • [Art therapy in psychiatry (author's transl)].

    abstract::The author tries to convey an idea of the process which takes place during art therapy, quoting examples from her own work with mentally diseased patients. She considers the visual message resulting from the work of art created by the patient, as a process of communication which takes place between the patient and the...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Wellendorf E

    更新日期:1980-02-01 00:00:00

  • [The residential structure as a therapeutic instrument].

    abstract::The frequency of residential placements in homes and households contrasts with the scarcity of its evaluation with respect to therapeutical effects. In order to facilitate evaluative studies, relevant structural elements and suggestions for a typology are discussed as well as methodological problems. Examples of empir...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Uchtenhagen A

    更新日期:1984-09-01 00:00:00

  • [Neurobiology of violence: results of empirical and experimental studies of reactive violence].

    abstract:OBJECTIVE AND METHOD:An overview on neurobiological findings of violence is given: We present 1. neurochemical findings, 2. genetical aspects, 3. neuroanatomical correlates and 4. a functional network of violence. Even if specific neurobiological findings have not been found, impulsive violence is closely linked to ser...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2004-828431

    authors: Müller JL,Sommer M,Weber T,Hajak G

    更新日期:2004-11-01 00:00:00

  • [Cerebral seizures in neuroleptic therapy].

    abstract::Basing on a review of the literature and on own research, the authors examine the incidence rate of convulsions under neuroleptic treatment. In addition, the authors go into the neurophysiological and neuropharmacological mechanisms of the convulsive action of neuroleptics. An attempt is made to present information on...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Bartels M,Heimann H

    更新日期:1985-11-01 00:00:00

  • [Quality assurance and documentation for community mental health services cooperative (GPV). A standardized procedure for regional health care documentation and planning].

    abstract::This paper describes a standardized assessment-procedure for the so-called "Gemeindepsychiatrische Verbünde" in Germany (GPV-Documentation), which are regional combines of community-based mental health care services. It is the first procedure in Germany which puts data on psychiatric care offers, needs for care and se...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Salize HJ,Bullenkamp J,Alscher I,Wolf I

    更新日期:2000-03-01 00:00:00

  • ["If I were the department head in this case..."--interventional interview with patients and co-workers of a psychiatric department].

    abstract:OBJECTIVE:How can patients and staff participate in redesigning psychiatric procedures through survey research? METHODS:Using interviews with circular-hypothetical questioning, 58 patients and 30 staff members of a psychiatric department of a general hospital were interviewed about their preferences for change and con...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2001-13264

    authors: Scheidt P,Schweitzer J,Maischein L,Tebbe B,Hirschenberger N,Enssle M,Krause U,Voigtländer W

    更新日期:2001-05-01 00:00:00

  • [Involuntary hospital admissions of mentally ill patients--how specific are differences among the German Federal States?].

    abstract:OBJECTIVE:Estimates for the proportion of involuntary admissions and coercive measures applied in general mental health care and in residential care for the elderly were developed. Sector-specific rates and quotas for Germany as a whole and for the sixteen Federal States were calculated, and the change of these indicat...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2006-952010

    authors: Salize HJ,Spengler A,Dressing H

    更新日期:2007-04-01 00:00:00

  • [Development and validation of an overall instrument to measure craving across multiple substances: the Mannheimer Craving Scale (MaCS)].

    abstract:OBJECTIVE:Based on the Obsessive Compulsive Drinking Scale (OCDS) we developed and validated the Mannheimer Craving Scale (MaCS) for quantitative measurements of craving across different substances and suitable for multiple substance abuse. METHODS:The MaCS questionnaire measures obsessive-compulsive symptoms in the c...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2008-1067546

    authors: Nakovics H,Diehl A,Geiselhart H,Mann K

    更新日期:2009-03-01 00:00:00

  • [Work with relatives at the psychiatric admission unit--report of experiences with a mixed syndrome family group].

    abstract::Therapeutical groups for relatives of psychiatric patients meanwhile are obligatory within strategies of psychiatric treatment. Up to a now most of the recent investigations refer to relatives of patients suffering from schizophrenia. The following article deleniates experiences with a therapeutic group for relatives ...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Karschny J,Rosemeier B,Schubert M

    更新日期:1991-03-01 00:00:00

  • [Changes in the provision of psychiatric services at a psychiatric district hospital].

    abstract::Changes in the provision of psychiatric services within the last decennials are probably best understood if the impact of national socialism on clinical psychiatry is regarded. Many psychiatrists took part in the "Aktion T4" the organised killing of their patients, at least they did not resist campaigns directed to ki...

    journal_title:Psychiatrische Praxis

    pub_type: 历史文章,杂志文章

    doi:10.1055/s-2004-828483

    authors: Schaub R

    更新日期:2004-11-01 00:00:00

  • [Optimized quality of care for affective disorders by health insurance-based case-management: a controlled cost-study].

    abstract:OBJECTIVE:Improvement of depression treatment by health insurance based case-management. Criteria of improvement were a higher treatment rate of patients suffering from affective disorders or depression by psychiatrists or psychotherapists than by general practitioners or family doctors and sickness fund payments. MET...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-0033-1349557

    authors: Salize HJ,Jacke C,Gallas C,Stamm K

    更新日期:2014-11-01 00:00:00

  • [Late rehabilitation of psychiatric patients].

    abstract::The results of a catamnestic study concerning patients of a psychiatric rehabilitation unit are reported. The patients were either longterm inpatients (mean duration of stay 8.5 years) or those, who had been transferred from the acute unit for lack of therapeutic progress and thus were probable to become longterm pati...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Rittmannsberger H,Schöny W

    更新日期:1986-09-01 00:00:00

  • [Promoting Self-Management in Primary Care - the Association of Motivation for Change, Self-Efficacy and Psychological Distress Prior to the Onset of Intervention].

    abstract::Anxiety, depressive and somatoform disorders are highly prevalent in primary care. Managing these disorders is time-consuming and requires strong commitment on behalf of the general practitioners (GPs). Furthermore, the resources for the management of these patients are limited by the increasing workload in primary ca...

    journal_title:Psychiatrische Praxis

    pub_type: 临床试验,杂志文章,多中心研究

    doi:10.1055/s-0034-1387686

    authors: Zimmermann T,Puschmann E,Porzelt S,Ebersbach M,Ernst A,Thomsen P,Scherer M

    更新日期:2015-07-01 00:00:00

  • [Pregabalin for the reduction of opiate withdrawal symptoms].

    abstract::Pregabalin is a substance which modulates monoamine release in "hyper-excited" neurons. It binds potently to the α2-δ subunit of calcium channels. Pilotstudies on alcohol- and benzodiazepine dependent patients reported a reduction of withdrawal symptoms through Pregabalin. To our knowledge, no studies have been conduc...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-0032-1305042

    authors: Kämmerer N,Lemenager T,Grosshans M,Kiefer F,Hermann D

    更新日期:2012-10-01 00:00:00

  • [Screening Instruments for the Detection of Male-Specific Symptoms of Unipolar Depression - A Critical Overview].

    abstract:BACKGROUND:Epidemiological studies have repeatedly pointed out gender differences in unipolar depression, whereas women have a 1.5 to 3 times higher risk of receiving a diagnosis. This however stands in sharp contrast with the 10 times higher suicide-rate of men, although depression is among the main risk-factors for s...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章,评审

    doi:10.1055/s-0043-120289

    authors: Zülke AE,Kersting A,Dietrich S,Luck T,Riedel-Heller SG,Stengler K

    更新日期:2018-05-01 00:00:00

  • [Schizophrenic patients, who still live in psychiatric hospitals despite decades of deinstitutionalization. Part 1 of the Hessian Deinstitutionalisation Study].

    abstract::Deinstitutionalization (DI) of most of the chronic long-stay patients has taken place in the last decades in Germany. However, a "residual" group of patients often remains in psychiatric hospitals, with an ongoing controversy on an appropriate type of their care (community based vs. hospital). Clinical, functional and...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2002-32711

    authors: Franz M,Meyer T,Ehlers F,Gallhofer B

    更新日期:2002-07-01 00:00:00

  • [Antidepressants and Driving Ability]

    abstract::OBJECTIVE: The aim of our study was to investigate the influence of antidepressants on psychomotor function related to car driving abilities. METHOD: Depressive inpatients (n = 64) were investigated under steady state plasma level conditions. Data were collected with the ART 90 (Act and React Testsystem) measuring vis...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2003-39765

    authors: Brunnauer A,Laux G

    更新日期:2003-05-01 00:00:00

  • [German language psychiatry journals in Germany - a quantitative analysis].

    abstract:OBJECTIVE:Although English is medicine's lingua franca, practising physicians in Germany express the need for articles in German. This study aimed at surveying the number and characteristics of German-language psychiatric journals in Germany. METHODS:Journals were identified by the standard handbook "Fachmedien Gesund...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-0031-1276955

    authors: Heidenreich U,Baethge C

    更新日期:2012-01-01 00:00:00

  • [The regional budget for mental health care: a new approach to combine inpatient and outpatient care].

    abstract:OBJECTIVE:Due to increasing health care expenditures the discussion about advantages and disadvantages of new methods for resource allocation in mental health care has been intensified. A promising model is the Regional Budget for Mental Health Care, which is currently being examined in Schleswig-Holstein. The present ...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2004-834736

    authors: Roick C,Deister A,Zeichner D,Birker T,König HH,Angermeyer MC

    更新日期:2005-05-01 00:00:00

  • [Subjective quality of life of schizophrenic patients. Effect of treatment setting, psychopathology and extrapyramidal motor drug effects].

    abstract:OBJECTIVE:In a cross-sectional study in 79 schizophrenic patients the quality of life (QOL) of a group of community-based patients under supervision of an outpatient unit (n = 47) and a group of long-stay patients in an inpatient rehabilitation centre in the same area (n = 32) was compared. METHODS:The patients' QOL w...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Kemmler G,Meise U,Tasser A,Liensberger D,Schifferle I,Braitenberg M,Schwitzer J,Hinterhuber H

    更新日期:1999-01-01 00:00:00

  • [Heinrich von Kleist--crisis and creative overcoming].

    abstract::Heinrich von Kleist's life was shaken repeatedly by negative life-events, finally he committed suicide in his last life-crisis (1811). His work was mostly understood as descriptions of negative life-events and failed-being. In this article it will be shown that in at least two "crises" Kleist's work can be understood ...

    journal_title:Psychiatrische Praxis

    pub_type: 传,历史文章,杂志文章

    doi:10.1055/s-2001-15576

    authors: Schlimme J

    更新日期:2001-07-01 00:00:00

  • [Attachment styles in German alcoholics with or without attention-deficit hyperactivity disorder (ADHD)].

    abstract:INTRODUCTION:Attachment theory yields empirical constructs for development of human self, personality and cognition. Insecure attachment strategies were associated with various psychiatric disorders. METHOD:We investigated distribution of attachment styles in 368 adult alcoholics of German descent with or without pers...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2004-828447

    authors: Johann M,Laufkötter R,Lange K,Wodarz N

    更新日期:2004-11-01 00:00:00

  • [The German adaptation of the Verona Service Satisfaction Scale: an instrument for patients' satisfaction with mental health care].

    abstract:UNLABELLED:The German Adaptation of the Verona Service Satisfaction Scale: An Instrument for Patients' Satisfaction with Mental Health Care. AIM:Measuring effectiveness and quality of care became an important topic in psychiatry. Considering that objective criteria were not sufficient in the past, the subjective persp...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2001-17791

    authors: Mory C,Matschinger H,Roick C,Kilian R,Bernert S,Angermeyer MC

    更新日期:2001-10-01 00:00:00

  • [Acute dyskinesia as the cause of jaw dislocation].

    abstract::A case of an acute dyskinesia of a young, schizophrenic woman caused by neuroleptic therapy is reported. The acute dyskinesia was the reason for a complete luxation in the jaw-joint. The patient showed phenomenons (brain-atrophy, cognitive dysfunction, negative symptoms) which are discussed to be connected with acute ...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Kozian R,Kiszka T,Peter K,Kühne GE

    更新日期:1992-07-01 00:00:00