[Adult neuronal ceroid lipofuscinosis (Kufs disease)--a rare cause of dementia].

Abstract:

:Kufs' disease is a very rare type of neuronal ceroid lipofuscinosis. A case of a 52 year old man with dementia is described. The cause for patient's dementia was the adult type (Kufs' disease) of neuronal ceroid lipofuscinosis. The diagnosis based on the histopathological post mortem-examination of the brain-tissue. A brother of our patient became ill with the same symptoms and at the same age of onset. So we conclude that there is a accumulation in the family.

journal_name

Psychiatr Prax

journal_title

Psychiatrische Praxis

authors

Kozian R,Kiszka T,Peter K

subject

Has Abstract

pub_date

1994-11-01 00:00:00

pages

235-7

issue

6

eissn

0303-4259

issn

1439-0876

journal_volume

21

pub_type

杂志文章
  • [Ambulatory psychotherapy of sex offenses].

    abstract::We present the theoretical basis and results of a comprehensive research project concerning the psychotherapeutic treatment of sexual offenders in an ambulant setting. The therapeutic sample (n = 86) consists of patients with the following symptoms: exhibitionism, child molestation and sexual aggressive acts towards w...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Lohse H,Hauch M

    更新日期:1983-09-01 00:00:00

  • [Cerebral seizures in neuroleptic therapy].

    abstract::Basing on a review of the literature and on own research, the authors examine the incidence rate of convulsions under neuroleptic treatment. In addition, the authors go into the neurophysiological and neuropharmacological mechanisms of the convulsive action of neuroleptics. An attempt is made to present information on...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Bartels M,Heimann H

    更新日期:1985-11-01 00:00:00

  • [A brief instrument for the assessment of childhood abuse and neglect: the childhood trauma screener (CTS)].

    abstract:OBJECTIVE:There is a lack of a psychometrically sound screening questionnaire that assesses important dimensions of traumatic experiences during childhood and adolescence in a time-efficient way. Based on the German version of the "Childhood Trauma Questionnaire" (CTQ, 28 items) we developed a five-item self-report chi...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-0031-1298984

    authors: Grabe HJ,Schulz A,Schmidt CO,Appel K,Driessen M,Wingenfeld K,Barnow S,Spitzer C,John U,Berger K,Wersching H,Freyberger HJ

    更新日期:2012-04-01 00:00:00

  • [A psycho-educational family group for reducing stress and preventing recurrence for families of schizophrenic patients. Catamnestic results of the Tübingen family project].

    abstract::Providing information about the disease and the way of coping with it has a central position in therapeutic interventions with families. By giving basic knowledge about schizophrenia to relatives we developed the practical conception of the psychoeducative relatives' group (information-group), a structured program, wh...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Scherrmann TE,Seizer HU,Rutow R,Vieten C

    更新日期:1992-05-01 00:00:00

  • [Project HOpeS: help and orientation for students with mental health problems].

    abstract::Project HOpeS aims to establish a special support service for students with mental health problems in Hamburg, Germany, modelled on a programme designed by the university of Münster. Students with mental health problems have to cope with reduced cognitive productivity, damaged self-confidence, stigmatisation, lack of ...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2002-19675

    authors: Biermann A,Giesen AD

    更新日期:2002-01-01 00:00:00

  • [The German adaptation of the Verona Service Satisfaction Scale: an instrument for patients' satisfaction with mental health care].

    abstract:UNLABELLED:The German Adaptation of the Verona Service Satisfaction Scale: An Instrument for Patients' Satisfaction with Mental Health Care. AIM:Measuring effectiveness and quality of care became an important topic in psychiatry. Considering that objective criteria were not sufficient in the past, the subjective persp...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2001-17791

    authors: Mory C,Matschinger H,Roick C,Kilian R,Bernert S,Angermeyer MC

    更新日期:2001-10-01 00:00:00

  • [The neuronal level of motor activity: determination of motor cortex excitability by TMS].

    abstract::Transcranial magnetic stimulation as mapping method offers the possibility to measure aspects of motor cortex excitability painlessly and non-invasively. Using this neurophysiological tool, new insights into the effects of central-acting drugs are possible. Particularly striking seems to be the potential of this appro...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2004-828492

    authors: Eichhammer P,Langguth B,Müller J,Hajak G

    更新日期:2005-04-01 00:00:00

  • [Decisions of the psychiatric court of appeal of basle-city in the year 2000--procedure on appeal against compulsory admission in a Swiss canton].

    abstract::We present the legislation of the compulsory admission and treatment of mentally ill persons in the Swiss canton of Basle-City. We inquired retrospectively the requests of the clinic and the appointed time given by the psychiatric court of appeal in the year 2000. With 320 compulsory admissions there were 118 appeals....

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2003-38606

    authors: Eichhorn M,Zimmermann R,Kräuchi K,Finzen A

    更新日期:2003-04-01 00:00:00

  • [Psychotherapeutic responsibilities in psychiatry--and the cooperation of fields].

    abstract::In the context of discussions on the re-organisation of specialities in psychiatry and psychological therapy recent studies on the prevalence of psychogenic disorders in different psychiatric institutions are presented and compared with the communications available so far. Despite the availability of excellent psychot...

    journal_title:Psychiatrische Praxis

    pub_type: 社论,评审

    doi:

    authors: Müller P

    更新日期:1997-05-01 00:00:00

  • [Does early use of ECT reduce the hospital stay period in major depressive episodes?].

    abstract:OBJECTIVE:ECT is an effective and safe therapy with fast response for depressive disorders. Nevertheless it's mostly used for therapy resistance. In antidepressive treatments fast response may be related with antidepressive efficacy. We studied, if earlier ECT could result in a shorter hospital stay period after the tr...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-0030-1248600

    authors: Schwerthöffer D,Wolf F,Pitschel-Walz G,Bäuml J

    更新日期:2011-02-01 00:00:00

  • [Wishes and expectations of psychiatric patients in ambulatory after care--and recommendations of their physicians].

    abstract::156 patients from two psychiatric hospitals were asked about their expectations and wishes regarding their further medical care and treatment immediately prior to their discharge. Answers were analyzed according to age, sex and diagnoses. This is contrasted by the suggestions of the medical staff, which seems to be in...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Geers M,Müller P

    更新日期:1984-05-01 00:00:00

  • [Family therapy--encounters with a therapeutic fashion (author's transl)].

    abstract::Following the boom in Group Therapy, the Federal Republic of Germany now experiences a similar boom in Family Thera;y. An attempt is made in the present article to show the stepwise progress from individual to group psychotherapy and finally to family therapy, and to describe and calssify the family therapy approach. ...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Finzen A

    更新日期:1979-05-01 00:00:00

  • [The case of a 86-years old woman first diagnosed with Huntington's disease].

    abstract::This is the rare case of a woman first diagnosed with Huntington's disease at the age of 86. She was first seen at our hospital in 1999 for evaluation of dementia. Prior to her hospitalization, she had been treated with Melperone for restlessness. There was no essential psychopathology other than mild dementia (MMSE 2...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2004-828455

    authors: Jähnel M

    更新日期:2004-11-01 00:00:00

  • [About the addiction to using the telephone or a structural approach in the crisis intervention for a better work with long-term users].

    abstract::The presented document discusses the problems of psychological/psychiatric and emergency long term users. The author, director of the East Berlin Crisis Centre, describes the long-term patient phenomenon from different perspectives. He develops ideas to change the concept of acute intervention. The crisis intervention...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2002-35512

    authors: Neumann O

    更新日期:2002-11-01 00:00:00

  • ["REGRATIO" - A vocational reintegration project for psychiatric patients].

    abstract:OBJECTIVE:Theoretical background and first results of a vocational rehabilitation program for unemployed persons with chronic psychiatric disabilities will be presented. The aim of the program is job-placement in the regular labour market. METHODS:After a 3-month preparatory period the participants were given the poss...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2002-22041

    authors: Waschkowski H,Bailer J,Fischer S,Lederle K

    更新日期:2002-03-01 00:00:00

  • [Myasthenia gravis in the frontier of psychiatric diagnosis].

    abstract::Retrospectively 20% of more than 200 patients with myasthenia gravis reported being initially diagnosed as having a psychiatric disorder. Younger women are significantly most at risk of a psychiatric misdiagnosis whereas men are more often subject to somatic misdiagnoses. The sample's mean duration of the disease was ...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Rohr W

    更新日期:1992-09-01 00:00:00

  • [How to care for homeless mentally ill men in the community - a randomised intervention study].

    abstract:OBJECTIVE:The aim of the present study was to clarify whether the mediation of homeless persons identified as mentally ill into the sociopsychiatric or the help-seeking system can be facilitated by a short-term intervention. METHOD:Probands with at least one psychiatric diagnosis according to ICD-10 (73 % of the sampl...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章,随机对照试验

    doi:10.1055/s-2004-834688

    authors: Längle G,Egerter B,Petrasch M,Albrecht-Dürr F

    更新日期:2006-07-01 00:00:00

  • [Quality of life for schizophrenic patients--that is.... Results of a survey of psychiatrists].

    abstract::605 German psychiatrists were asked what they consider important ingredients of the quality of life of schizophrenic patients. Most frequently, quality of life was associated with social integration. Work, social contacts and acceptance on the part of their environment were considered particularly important in this re...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Holzinger A,Angermeyer MC,Matschinger H

    更新日期:1997-03-01 00:00:00

  • [Lowering vocational rehabilitative measures during inpatient psychiatric longterm treatment costs of patients with schizophrenia? Results of a controlled multicenter study].

    abstract:OBJECTIVE:Little is known about the effectiveness and the cost of care for patients treated in vocational rehabilitation programs,although vocational therapy is an essential part of inpatient treatment and community care of patients with schizophrenia. METHODS:As a part of a randomised controlled trial in 5 centres, t...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章,多中心研究,随机对照试验

    doi:10.1055/s-2006-951949

    authors: Salize HJ,Schuh C,Reichenbacher M,Stamm K,Längle G,KN-Schizophrenie-Projektgruppe Arbeitsrehabilitation.

    更新日期:2007-07-01 00:00:00

  • [Effects of aggression management trainings for mental health care and disability care staff--systematic review].

    abstract:BACKGROUND:Aggression management trainings for staff have been implemented in many organizations of mental health care and disability care. The efficacy of such programmes has rarely been analysed. METHODS:A systematic review was conducted which contains all published evaluation studies on aggression management traini...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章,评审

    doi:10.1055/s-2006-940063

    authors: Richter D,Needham I

    更新日期:2007-01-01 00:00:00

  • [Acute water intoxication as a complication of therapy refractory schizophrenia].

    abstract::A patient with chronic paranoid schizophrenia with delusions of infestation and of grandeur type, developed polydipsia in the course of his illness which ended up in acute life-threatening water intoxication. Apart from somatic causes like SIADH, which are discussed in literature, water-intoxication could psychodynami...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Frei A,Kolb C

    更新日期:1998-01-01 00:00:00

  • [Gamma-hydroxybutyrat (GHB)-dependence and -withdrawal in the case of previous alcohol dependence].

    abstract:OBJECTIVE:gamma-Hydroxybutyrat (GHB) is used medically for narcolepsy and as a narcotic. It is also a rare illegal drug. In this case report the development of a GHB-dependency against the background of a primary alcohol dependency is described. METHODS:Based on established alcohol withdrawal scales (AWSS by Wetterlin...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-0028-1090089

    authors: Richter C,Romanowski A,Kienast T

    更新日期:2009-10-01 00:00:00

  • [Reintegration in residential facilities--a catamnestic study].

    abstract::A rehabilitation programme at the University Clinic of Social Psychiatry, Berne, is described. The facility includes a half-way house and sheltered home in a suburb, where 20 psychiatric long-stay patients are trained for an independent life in the community. In a follow-up study 80 patients, mostly chronic schizophre...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Hubschmid T,Pfister F,Spalinger J

    更新日期:1988-05-01 00:00:00

  • [On the importance of the geographical position of psychiatric hospitals for the admission rates and hospitalization period (author's transl)].

    abstract::Rates of admission, duration of hospitalization, chances of discharge and legal basis of admissions are analyzed with reference to the distances between the patients' domiciles and the hospital, basing on the figures which apply to the district hospitals Gabersee in Upper Bavaria. More patients from nearby are admitte...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Weyerer S,Dilling H

    更新日期:1978-02-01 00:00:00

  • [Acute dyskinesia as the cause of jaw dislocation].

    abstract::A case of an acute dyskinesia of a young, schizophrenic woman caused by neuroleptic therapy is reported. The acute dyskinesia was the reason for a complete luxation in the jaw-joint. The patient showed phenomenons (brain-atrophy, cognitive dysfunction, negative symptoms) which are discussed to be connected with acute ...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Kozian R,Kiszka T,Peter K,Kühne GE

    更新日期:1992-07-01 00:00:00

  • [Pregabalin for the reduction of opiate withdrawal symptoms].

    abstract::Pregabalin is a substance which modulates monoamine release in "hyper-excited" neurons. It binds potently to the α2-δ subunit of calcium channels. Pilotstudies on alcohol- and benzodiazepine dependent patients reported a reduction of withdrawal symptoms through Pregabalin. To our knowledge, no studies have been conduc...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-0032-1305042

    authors: Kämmerer N,Lemenager T,Grosshans M,Kiefer F,Hermann D

    更新日期:2012-10-01 00:00:00

  • [Involuntary hospital admissions of mentally ill patients--how specific are differences among the German Federal States?].

    abstract:OBJECTIVE:Estimates for the proportion of involuntary admissions and coercive measures applied in general mental health care and in residential care for the elderly were developed. Sector-specific rates and quotas for Germany as a whole and for the sixteen Federal States were calculated, and the change of these indicat...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:10.1055/s-2006-952010

    authors: Salize HJ,Spengler A,Dressing H

    更新日期:2007-04-01 00:00:00

  • [Forensic psychiatry: contradictions between clinical practice and justice].

    abstract::All the different branches in forensic psychiatry have to face identical handicaps resulting from the difficulties in cooperation with the law-court. For the psychiatrist, his identity as a therapist is contradictory to his forensic tasks. The paper deals with the resulting dilemmata (partiality v. neutrality; diagnos...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章,评审

    doi:

    authors: Küchenhoff J

    更新日期:1988-03-01 00:00:00

  • [Social support of mentally handicapped adults: effects of degree of handicap and type of residential facility].

    abstract::In a total sample of 141 mentally retarded adults the quality of social relationships was assessed by the newly developed "Interview for Social Support in Mentally Retarded Adults". Severely mentally retarded persons have close and intimate relationships to a consistently lesser extent than mildly retarded persons. Th...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Meins W

    更新日期:1993-05-01 00:00:00

  • [Behavioral rehabilitation of nonspecific symptoms occuring after craniocerbral trauma (author's transl)].

    abstract::The purpose of this study was to develop a behavioral rehabilitation program for patients with long-term nonspecific symptoms following craniocerebral trauma. In 47 patients we analyzed symptoms typical of "illness behavior" (e.g. complaining tendency, depression, irritability, psychosomatic pain, problems in job perf...

    journal_title:Psychiatrische Praxis

    pub_type: 杂志文章

    doi:

    authors: Legewie-Pertzborn H,Legewie H,Foit J,Brinkmann R

    更新日期:1977-11-01 00:00:00