Further observation of Japanese Creutzfeldt-Jacob disease with widespread amyloid plaques.

Abstract:

:An autopsy case of Creutzfeld-Jacob disease with widespread amyloid plaques is reported. A 45-year-old Japanese man, whose father had died of a similar disease, had a 5-year illness characterized by progressive cerebellar signs. Mental changes and brain-stem signs developed in the late stage. Myoclonus frequently occurred. Akinetic mutism ensued. The autopsy revealed spongiform encephalopathy with widespread amyloid plaques and extensive degeneration of the white matter. This disease, Western Gerstmann-Sträussler-Scheinker disease and panencephalopathic type of Creutzfeld-Jacob disease are discussed.

journal_name

J Neurol

journal_title

Journal of neurology

authors

Yagishita S,Iwabuchi K,Amano N,Yokoi S

doi

10.1007/BF00314329

subject

Has Abstract

pub_date

1989-03-01 00:00:00

pages

145-8

issue

3

eissn

0340-5354

issn

1432-1459

journal_volume

236

pub_type

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