Abstract：
BACKGROUND:Pulmonary alveolar proteinosis (PAP) is characterized by an abnormal accumulation of periodic acid-schiff-positive lipoproteinaceous material in the alveoli. Early diagnosis allows setting up of therapeutic lung lavages, which reduces the need for oxygen supplementation and weight gain. OBJECTIVE:To provide a description of radiological features by CT at the onset of primary PAP in children. MATERIALS AND METHODS:The clinical and radiological data of 24 patients, including 16 boys and 8 girls (median age: 12 months), diagnosed with a primary form of PAP between April 1992 and May 2012 in a tertiary referral hospital, were retrospectively reviewed. CT images were examined for the presence of alveolar and interstitial elementary lesions. Correlation between clinical and radiological findings was assessed. RESULTS:The types of elementary lesions detected were: ground-glass opacities (n = 24), intralobular lines (n = 24), thickened interlobular septa (n = 22), thickened fissures (n = 21), airspace consolidation (n = 16), hyperinflation (n = 16), cystic lesions (n = 2) and micronodules (n = 1). A crazy-paving pattern was found in 92% of cases. Consolidation and hyperinflation were especially detected in younger children (median age, 8 months, P < 0.01). A density dependent gradient was found. The distribution of the lesions was symmetrical. There was no correlation between radiological and clinical data of severity of the disease. CONCLUSION:CT findings are suggestive of diagnosis of PAP in immunocompetent children with chronic respiratory failure.
journal_name
Pediatr Radioljournal_title
Pediatric radiologyauthors
Berteloot L,Taam RA,Emond-Gonsard S,Mamou-Mani T,Lambot K,Grévent D,Elie C,Le Bourgeois M,Delacourt C,Brunelle F,de Blic Jdoi
10.1007/s00247-014-2888-1subject
Has Abstractpub_date
2014-07-01 00:00:00pages
795-802issue
7eissn
0301-0449issn
1432-1998journal_volume
44pub_type
杂志文章abstract：BACKGROUND:The optimal treatment of perforated appendicitis remains controversial, but there is a trend toward nonoperative management. CT scanning might be helpful in determining which patients could benefit from this treatment option. OBJECTIVE:To determine the value of CT imaging in predicting clinical success or f...
journal_title：Pediatric radiology
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journal_title：Pediatric radiology
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journal_title：Pediatric radiology
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