Gorham syndrome with postoperative respiratory failure and requiring prolonged mechanical ventilation.

Abstract:

:Gorham syndrome is a rare disease that presents as progressive osteolysis, and may affect any part of the skeleton. The pathologic process involves the replacement of normal bone by aggressively expanding but non-neoplastic vascular tissue, resulting in massive osteolysis of the adjacent bone. If the spine and ribs are affected, the subsequent kyphosis and chest wall deformity may cause severe restrictive ventilatory impairment. We report a 34-year-old male with Gorham syndrome presenting as progressive kyphosis, severe back pain, unstable gait, and exertional dyspnea. Pulmonary function testing revealed severe restrictive ventilatory impairment. He underwent spinal surgery but could not be extubated after surgery. Postoperative left lower lung pneumonia and respiratory failure required prolonged mechanical ventilation. After a weaning program of pressure support ventilation and T-piece spontaneous breathing trials, he was successfully weaned from mechanical ventilation.

journal_name

Respir Care

journal_title

Respiratory care

authors

Huang SY,Lee YM,Tzeng ST,Su CP,Huang SF,Wu YK,Lan CC

doi

10.4187/respcare.02355

subject

Has Abstract

pub_date

2013-11-01 00:00:00

pages

e144-8

issue

11

eissn

0020-1324

issn

1943-3654

pii

respcare.02355

journal_volume

58

pub_type

杂志文章
  • Successful extracorporeal membrane oxygenation for respiratory failure in an infant with DiGeorge anomaly, following thymus transplantation.

    abstract::We report the first successful use of venovenous extracorporeal membrane oxygenation (ECMO) for refractory respiratory failure in an infant with DiGeorge anomaly, following thymus transplantation. A 23-month-old female with complete immune-incompetent DiGeorge anomaly 65 days after allogenic thymus transplantation was...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.01051

    authors: Hornik CP,Hartman ME,Markert ML,Lodge AJ,Cheifetz IM,Turner DA

    更新日期:2011-06-01 00:00:00

  • Cost-benefit considerations in managing oxygenation failure.

    abstract::The evaluation of new therapy poses a formidable challenge in intensive care medicine. When therapy evaluation cannot be double-blinded, as in the evaluation of extracorporeal support, the problem becomes more difficult. The result of the extracorporeal clinical trial, like that of the ECMO trial in the 1970s, is a po...

    journal_title:Respiratory care

    pub_type: 杂志文章,评审

    doi:

    authors: Morris AH

    更新日期:1993-07-01 00:00:00

  • Ventilatory adjuncts.

    abstract::A number of adjuncts to mechanical ventilation have been the focus of recent research. Automatic tube compensation (the regulation of airway pressure by estimation of tracheal pressure) appears to be an ideal approach to unloading the resistive effort imposed by the endotracheal tube. Randomized controlled trials have...

    journal_title:Respiratory care

    pub_type: 杂志文章,评审

    doi:

    authors: Kacmarek RM

    更新日期:2002-03-01 00:00:00

  • Emergency Department Airway Management for Status Asthmaticus With Respiratory Failure.

    abstract:BACKGROUND:Data are limited regarding current practice and outcomes for emergency department airway management in status asthmaticus. This paper describes the foremost methods and outcomes of airway management in patients in the emergency department who required intubation for status asthmaticus. METHODS:We analyzed a...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.07723

    authors: Godwin HT,Fix ML,Baker O,Madsen T,Walls RM,Brown CA 3rd

    更新日期:2020-12-01 00:00:00

  • The interpretation of exhaled nitric oxide values in children with asthma depends on the degree of bronchoconstriction and the levels of asthma severity.

    abstract:BACKGROUND:The clinical implications of fractional exhaled nitric oxide (F(ENO)) measurements in childhood asthma are unclear. We aimed to evaluate the relationship between the level of exhaled nitric oxide and pre-bronchodilator FEV1 and the change in FEV1 after bronchodilator in children with asthma. METHODS:This wa...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.02889

    authors: Grzelewski T,Majak P,Jerzyńska J,Stelmach W,Stelmach R,Janas A,Grzelewska A,Witkowski K,Makandjou-Ola E,Stelmach I

    更新日期:2014-09-01 00:00:00

  • Inspiratory flow-volume curve evaluation for detecting upper airway disease.

    abstract:BACKGROUND:The 2005 American Thoracic Society/European Respiratory Society guidelines on spirometry emphasize examination of the inspiratory curve of the flow-volume loop for evidence of intrathoracic or extrathoracic upper airway obstruction. We sought to determine how frequently evaluations are performed for abnormal...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:

    authors: Sterner JB,Morris MJ,Sill JM,Hayes JA

    更新日期:2009-04-01 00:00:00

  • Use of High-Flow Nasal Cannula Oxygen Therapy in Subjects With ARDS: A 1-Year Observational Study.

    abstract:BACKGROUND:Beneficial effects of high-flow nasal cannula (HFNC) oxygen on oxygenation and respiratory parameters have been reported in a small number of subjects with acute respiratory failure (ARF). We aimed to evaluate its effect in subjects with ARDS. METHODS:This was an observational single-center study. Prospecti...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.03423

    authors: Messika J,Ben Ahmed K,Gaudry S,Miguel-Montanes R,Rafat C,Sztrymf B,Dreyfuss D,Ricard JD

    更新日期:2015-02-01 00:00:00

  • Use of a noninvasive pulse CO-oximeter to measure blood carboxyhemoglobin levels in bingo players.

    abstract:BACKGROUND:Though smokers are known to have elevated blood carboxyhemoglobin (COHb), due to inhalation of carbon monoxide (CO) in cigarette smoke, limited data exist regarding COHb levels in nonsmokers exposed to secondhand smoke. METHODS:COHb was measured using a new noninvasive pulse CO-oximeter (Rad-57, Masimo, Irv...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:

    authors: Hampson NB,Scott KL

    更新日期:2006-07-01 00:00:00

  • Randomized controlled trial of a breath-actuated nebulizer in pediatric asthma patients in the emergency department.

    abstract:BACKGROUND:Bronchodilator treatment for asthma can be provided with various aerosol-generating devices and methods. There have been no randomized trials of a breath-actuated nebulizer versus continuous 1-hour nebulization and/or small-volume constant-output nebulizer in pediatric asthma patients. METHODS:We conducted ...

    journal_title:Respiratory care

    pub_type: 杂志文章,随机对照试验

    doi:10.4187/respcare.00142

    authors: Sabato K,Ward P,Hawk W,Gildengorin V,Asselin JM

    更新日期:2011-06-01 00:00:00

  • Physical Activity as a Predictor of Absence of Frailty in Subjects With Stable COPD and COPD Exacerbation.

    abstract:BACKGROUND:Frailty is a key issue in the care of elderly patients. Patients with COPD are more likely to be frail, with a prevalence of 57.8%. Frailty is associated with a low level of physical activity. The aim of this study was to analyze the predictive power and identify the cutoffs of physical activity in their dif...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.04118

    authors: Valenza MC,Torres-Sánchez I,Cabrera-Martos I,Rodríguez-Torres J,González-Jiménez E,Muñoz-Casaubon T

    更新日期:2016-02-01 00:00:00

  • The 2017 Global Initiative for Chronic Obstructive Lung Disease Report and Practice Implications for the Respiratory Therapist.

    abstract::Since 1998, the Global Initiative for Obstructive Lung Disease (GOLD) has worked with health care professionals, medical researchers, and public health officials around the world to optimize the prevention, treatment, and management of COPD. GOLD has continually worked to ensure COPD management strategy recommendation...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.05402

    authors: Hess MW

    更新日期:2017-11-01 00:00:00

  • Investigation of exclusive narghile smokers: deficiency and incapacity measured by spirometry and 6-minute walk test.

    abstract:BACKGROUND:Studies on the submaximal aerobic capacity of exclusive narghile smokers (ENS) seem necessary in view of effective prevention of cardiorespiratory diseases. The goal of the study was to assess, by 6-min walk test (6MWT) data, the submaximal aerobic capacity of ENS, to identify factors influencing their 6-min...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.03058

    authors: Ben Saad H,Babba M,Boukamcha R,Ghannouchi I,Latiri I,Mezghenni S,Zedini C,Rouatbi S

    更新日期:2014-11-01 00:00:00

  • Evaluation of a double-enclosure double-vacuum unit scavenging system for ribavirin administration.

    abstract:BACKGROUND:Because of our concern for the safety of bedside caregivers who care for infants receiving ribavirin for long periods of time each day for many days, we evaluated the effectiveness of a double-tent enclosure with vacuum scavengers during simulated and actual patient administration. MATERIALS & METHODS:Part ...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:

    authors: Kacmarek RM,Kratohvil J

    更新日期:1992-01-01 00:00:00

  • Inhaled Nitric Oxide: In Vitro Analysis of Continuous Flow Noninvasive Delivery via Nasal Cannula.

    abstract:BACKGROUND:Inhaled nitric oxide (NO) is most frequently delivered to mechanically ventilated patients in critical care, but it can also be administered noninvasively. The delivered dose and efficiency of continuous flow NO supplied through a nasal cannula has yet to be established. This study aimed to determine the inf...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.07737

    authors: Pillay K,Chen JZ,Finlay WH,Martin AR

    更新日期:2021-02-01 00:00:00

  • Current trends in neonatal and pediatric respiratory care: conference summary.

    abstract::A summary of the 2-day Journal Conference on Current Trends in Neonatal and Pediatric Respiratory Care is provided. Topics included: diagnosis and management of common respiratory disorders of infants and children such as asthma, respiratory syncytial virus bronchiolitis, and cystic fibrosis; and common pediatric resp...

    journal_title:Respiratory care

    pub_type:

    doi:

    authors: Kercsmar CM

    更新日期:2003-04-01 00:00:00

  • Staffing exercise sessions in pulmonary rehabilitation.

    abstract:INTRODUCTION:There is no published standard for the ratio of staff to patients during exercise sessions in outpatient pulmonary rehabilitation. This lack of a standard raises concern about patient safety and the ability to monitor patients adequately. OBJECTIVE:Determine a staff-to-patient ratio standard by examining ...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:

    authors: Hoberty PD,Chiu CY,Hoberty RJ

    更新日期:2001-07-01 00:00:00

  • The evolution of home mechanical ventilation in poland between 2000 and 2010.

    abstract:BACKGROUND:Home mechanical ventilation (HMV) is a routine method of treatment for patients with chronic ventilatory failure. Over the last 20 y, a marked development in HMV has been noted in terms of its prevalence and the changing proportion of patients with various indications. However, data on HMV come exclusively f...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.03126

    authors: Nasiłowski J,Wachulski M,Trznadel W,Andrzejewski W,Migdał M,Drozd W,Pytel A,Suchanke R,Czajkowska-Malinowska M,Majszyk T,Szkulmowski Z,Chazan R

    更新日期:2015-04-01 00:00:00

  • Translating evidence into practice.

    abstract::Appropriately designed and conducted research is necessary for improving patient care and optimizing health outcomes, but access to best evidence is not enough to make these things happen. In respiratory care, as in other fields, patients do not benefit as much as they should from research findings and evidence-based ...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:

    authors: Pierson DJ

    更新日期:2009-10-01 00:00:00

  • Evaluation of Oxidative Damage and Antioxidant Mechanisms in COPD, Lung Cancer, and Obstructive Sleep Apnea Syndrome.

    abstract:BACKGROUND:Oxidative damage is a major contributing factor to carcinogenesis and obstructive disorders in lungs. Current evidence suggests that the inflammatory processes yield to oxidative mechanisms, which underlie COPD, lung cancer, and obstructive sleep apnea syndrome (OSAS). This study aimed to evaluate the oxidat...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.04209

    authors: Sunnetcioglu A,Alp HH,Sertogullarından B,Balaharoglu R,Gunbatar H

    更新日期:2016-02-01 00:00:00

  • Decreasing Unplanned Extubation in the Neonatal ICU With a Focus on Endotracheal Tube Tip Position.

    abstract:BACKGROUND:Unplanned extubation (UE) is an important quality metric in the neonatal ICU that is associated with hypoxia, bradycardia, and risk for airway trauma with emergent re-intubation. Initial efforts to reduce UE in our level 4 neonatal ICU included standardized securement of the endotracheal tube (ETT) and requi...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.07446

    authors: Morris HF,Schuller L,Archer J,Niesen A,Ellsworth S,Egan J,Rao R,Vesoulis ZA,Mathur AM

    更新日期:2020-11-01 00:00:00

  • The effects of pressure control versus volume control assisted ventilation on patient work of breathing in acute lung injury and acute respiratory distress syndrome.

    abstract:BACKGROUND:Patient work of breathing (WOB) during assisted ventilation is reduced when inspiratory flow (V(I)) from the ventilator exceeds patient flow demand. Patients in acute respiratory failure often have unstable breathing patterns and their requirements for V(I) may change from breath to breath. Volume control ve...

    journal_title:Respiratory care

    pub_type: 临床试验,杂志文章

    doi:

    authors: Kallet RH,Campbell AR,Alonso JA,Morabito DJ,Mackersie RC

    更新日期:2000-09-01 00:00:00

  • A review of options for treating sialorrhea in amyotrophic lateral sclerosis.

    abstract::Sialorrhea or drooling represents quite a common problem in patients with amyotrophic lateral sclerosis (ALS). In this review, we describe the possible treatments for this issue. Current medical management is not always effective: anticholinergic drugs (atropine, glycopyrrolate, amitriptyline, hyoscyamine, and transde...

    journal_title:Respiratory care

    pub_type: 杂志文章,评审

    doi:10.4187/respcare.02856

    authors: Banfi P,Ticozzi N,Lax A,Guidugli GA,Nicolini A,Silani V

    更新日期:2015-03-01 00:00:00

  • Feasibility and effectiveness of an educational program in Italian COPD patients undergoing rehabilitation.

    abstract:BACKGROUND:Self-management education is associated with improvement in quality of life and reduction of hospital admissions. Nevertheless, the data are insufficient to formulate clear recommendations regarding the type and content of education programs for COPD patients, and few data are available on knowledge of the d...

    journal_title:Respiratory care

    pub_type: 临床试验,杂志文章

    doi:10.4187/respcare.01697

    authors: Paneroni M,Clini E,Crisafulli E,Guffanti E,Fumagalli A,Bernasconi A,Cabiaglia A,Nicolini A,Brogi S,Ambrosino N,Peroni R,Bianchi L,Vitacca M

    更新日期:2013-02-01 00:00:00

  • Evaluation of an oxygen mask-based capnometry device in subjects extubated after abdominal surgery.

    abstract:BACKGROUND:For early detection of respiratory and hemodynamic changes during anesthesia, continuous end-tidal carbon dioxide concentration (PETCO2) is monitored by capnometry. However, the accuracy of CO2 monitoring during spontaneous breathing in extubated patients remains undetermined. Therefore, we aimed to compare ...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.03557

    authors: Takaki S,Mihara T,Mizutani K,Yamaguchi O,Goto T

    更新日期:2015-05-01 00:00:00

  • Flow Decay: A Novel Spirometric Index to Quantify Dynamic Airway Resistance.

    abstract:BACKGROUND:Dynamic airway resistance from obstructive disease causes a concavity in the mid-expiratory portion of the spirometric flow-volume loop. We developed a simple model to measure the exponential decay in air flow during forced exhalation to quantify the extent of dynamic airway obstruction and facilitate the de...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.04850

    authors: Oh A,Morris TA,Yoshii IT,Morris TA

    更新日期:2017-07-01 00:00:00

  • Ventilator-Associated Events: What They Are and What They Are Not.

    abstract::In 2013, the United States Centers for Disease Control and Prevention redefined surveillance for quality of care in ventilated patients by shifting from ventilator-associated pneumonia (VAP) definitions to ventilator-associated event (VAE) definitions. VAE definitions were designed to overcome many of the limitations ...

    journal_title:Respiratory care

    pub_type: 杂志文章,评审

    doi:10.4187/respcare.07059

    authors: Klompas M

    更新日期:2019-08-01 00:00:00

  • Beliefs and Attitudes Associated With Hookah Smoking Among a United States College Population.

    abstract:BACKGROUND:This study explores the differences among smokers of waterpipe tobacco in a college population to better inform campaigns to curb waterpipe use. METHODS:Participants included undergraduate and graduate students attending a liberal arts university in Florida. E-mail-based, cross-sectional surveys were collec...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.05069

    authors: Martinasek MP,Haddad LG,Wheldon CW,Barnett TE

    更新日期:2017-03-01 00:00:00

  • Effect of a Motivational Interviewing-Based Health Coaching on Quality of Life in Subjects With COPD.

    abstract:BACKGROUND:Improving quality of life (QOL) is a key goal in the care of patients with COPD. Pulmonary rehabilitation (PR) has clearly been shown to improve QOL, but is not accessible to many eligible patients. There is a need for alternative programs designed to improve patient well-being that are accessible to all pat...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.04984

    authors: Rehman H,Karpman C,Vickers Douglas K,Benzo RP

    更新日期:2017-08-01 00:00:00

  • Spirometry training does not guarantee valid results.

    abstract:BACKGROUND:Many healthcare professionals performing spirometry in primary care have had less than half a day's training in spirometry practice, and the validity of the test results is questionable. Longer training periods, with or without follow-up training, may improve test validity. OBJECTIVE:To determine if a 14-ho...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:

    authors: Borg BM,Hartley MF,Fisher MT,Thompson BR

    更新日期:2010-06-01 00:00:00

  • Dynamic Airway Driving Pressure and Outcomes in Children With Acute Hypoxemic Respiratory Failure.

    abstract:BACKGROUND:Limited adult data suggest that airway driving pressure might better reflect the potential risk for lung injury than tidal volume based on ideal body weight, and the parameter correlates with mortality in ARDS. There is a lack of data about the effect of driving pressure on mortality in pediatric ARDS. This ...

    journal_title:Respiratory care

    pub_type: 杂志文章

    doi:10.4187/respcare.08024

    authors: Rauf A,Sachdev A,Venkataraman ST,Dinand V

    更新日期:2020-10-06 00:00:00