Abstract:
:We describe the case of a 17- year old female who developed fatal haemophagocytic syndrome (HPS) one month following acute infection caused by Epstein-Barr virus (EBV). Despite initiation of treatment and reduction of EBV load, laboratory signs of HPS as severe cytopenia, hypofibrinogenemia, hyperferritinemia and hypertriglyceridemia persisted, and the patient died of multiorgan failure. HPS is a rare, but life-threatening complication of EBV infection.
journal_name
Mediterr J Hematol Infect Disauthors
Torti L,Larocca LM,Massini G,Cuccaro A,Maiolo E,Santangelo R,Bianchi M,Pennisi MA,Hohaus S,Teofili Ldoi
10.4084/MJHID.2012.008subject
Has Abstractpub_date
2012-01-01 00:00:00pages
e2012008issue
1issn
2035-3006pii
mjhid-4-1-e2012008journal_volume
4pub_type
abstract::Therapy for hemophilia has evolved in the last 40 years from plasma-based concentrates to recombinant proteins and, more recently, to non-factor therapeutics. Along this same timeline, research in adeno-associated viral (AAV) based gene therapy vectors has provided the framework for early phase clinical trials initial...
journal_title:Mediterranean journal of hematology and infectious diseases
pub_type: 杂志文章,评审
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abstract::Developing an effective malaria vaccine has been the goal of the scientific community for many years. A malaria vaccine, added to existing tools and strategies, would further prevent infection and decrease the unacceptable malaria morbidity and mortality burden. Great progress has been made over the last decade and a ...
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pub_type: 杂志文章,评审
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abstract:OBJECTIVES:Low-dose cytarabine (LD-AraC) is still regarded as the standard of care in elderly patients with acute myeloid leukemia (AML) 'unfit' for intensive chemotherapy. In this study, we reported our experience with LD-AraC in patients ≥ 70 years old and compared the results to those of intensive chemotherapy, best...
journal_title:Mediterranean journal of hematology and infectious diseases
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更新日期:2016-01-01 00:00:00
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journal_title:Mediterranean journal of hematology and infectious diseases
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更新日期:2013-06-03 00:00:00
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journal_title:Mediterranean journal of hematology and infectious diseases
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journal_title:Mediterranean journal of hematology and infectious diseases
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更新日期:2009-12-20 00:00:00
abstract::POEMS syndrome is a rare, chronic and disabling condition. The causes of this condition remain unknown; however, chronic overproduction of proinflammatory cytokines appears to be a major contributor. Early diagnosis is essential to start treatment before the clinical state of the patient becomes compromised. A complet...
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pub_type: 杂志文章,评审
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journal_title:Mediterranean journal of hematology and infectious diseases
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更新日期:2010-01-01 00:00:00
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更新日期:2012-01-01 00:00:00
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journal_title:Mediterranean journal of hematology and infectious diseases
pub_type:
doi:10.4084/MJHID.2014.001
更新日期:2014-01-01 00:00:00
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journal_title:Mediterranean journal of hematology and infectious diseases
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更新日期:2016-10-20 00:00:00
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journal_title:Mediterranean journal of hematology and infectious diseases
pub_type: 杂志文章
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更新日期:2013-07-10 00:00:00
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journal_title:Mediterranean journal of hematology and infectious diseases
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更新日期:2015-03-01 00:00:00
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journal_title:Mediterranean journal of hematology and infectious diseases
pub_type: 杂志文章
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更新日期:2017-04-15 00:00:00
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journal_title:Mediterranean journal of hematology and infectious diseases
pub_type: 杂志文章
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更新日期:2020-05-01 00:00:00
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更新日期:2015-04-20 00:00:00
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journal_title:Mediterranean journal of hematology and infectious diseases
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abstract::Acute promyelocytic leukemia (APL) is highly curable with the combination of all-transretinoic acid (ATRA) and anthracycline based chemotherapy, but the percentage of early deaths remains high. In the present study, we report the clinical, immunophenotypic, cytogenetic and molecular characteristics and outcome of APL ...
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abstract:Background:Italy has been one of the first European countries hit by the COVID-19 pandemic, with many patients dying from severe respiratory issues, especially frail subjects. Hematology patients are generally thought to be at high risk of developing severe COVID-19-associated complications. The aim of this work was to...
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journal_title:Mediterranean journal of hematology and infectious diseases
pub_type: 杂志文章,评审
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abstract::Echinococcosis is an endemic zoonosis in the Mediterranean area, with Albania interested actually to a level that is becoming a public health concern. Authors describe preliminary data from the only tertiary (university) medical facility of Albania, positioned in the capital of the country (Tirana), with 333 new cases...
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journal_title:Mediterranean journal of hematology and infectious diseases
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abstract::The clinical presentation of β-thalassemia intermedia phenotypes are influenced by many factors. The persistence of fetal hemoglobin and several polymorphisms located in the promoters of γ- and β-globin genes are some of them. The aim of this study was to evaluate the combined effect of the -158 Gγ (C→T) polymorphism ...
journal_title:Mediterranean journal of hematology and infectious diseases
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