当前位置： SCI文献检索 > JOURNAL OF PEDIATRIC SURGERY期刊下所有文献 > Survival patterns in biliary atresia and comparison of quality of life of long-term survivors in Japan and England.

Survival patterns in biliary atresia and comparison of quality of life of long-term survivors in Japan and England.

Abstract：

BACKGROUND/PURPOSE:Portoenterostomy is an accepted method of achieving bile drainage in biliary atresia, but there is a paucity of data, including formal quality-of-life (QoL) studies, on long-term survivors. This report includes survival analysis and QoL studies from the world's largest series of cases treated in Japan (1951 to 1998). The Japanese QoL results are compared with a matched group of UK patients from King's College Hospital, London. METHODS:One hundred fifteen Japanese surviving portoenterostomy patients were studied and comparison of trends in survival calculated from 6-year period cohorts. Liver function and hematologic status in a group of 30 long-term survivors (14 to 24 years) were compared with 25 patients from England, (14 to 23 years). Twenty-five Japanese and 21 UK patients (SF-36) completed a QoL questionnaire. RESULTS:Median survival times in Japanese patients before 1975 were less than 1 year but increased to 18 years after 1975. Hematologic and liver function test results did not show any significant differences between the Japanese and UK patients. QoL studies in the UK patients showed no significant difference from normative, general population data. Japanese patients underperformed in general health (P = .01), role emotional (P = .05) and role physical (P = .07) but, overall, there was no significant difference between the Japanese and UK patients except for marginal differences in indices of general health and vitality (P = .06 and .04, respectively). CONCLUSIONS:Long-term survival rate in the Japanese patients increased dramatically from 1 year to 17 years after 1975. The QoL of survivors was comparable in Japan and England. The satisfactory comparison with normative population data suggests that we should continue to use portoenterostomy as the primary treatment for biliary atresia. J Pediatr Surg 36:892-897.

journal_name

J Pediatr Surg

journal_title

Journal of pediatric surgery

authors

Howard ER,MacLean G,Nio M,Donaldson N,Singer J,Ohi R

doi

10.1053/jpsu.2001.23965

subject

Has Abstract

pub_date

2001-06-01 00:00:00

pages

892-7

issue

6

eissn

0022-3468

issn

1531-5037

pii

S0022-3468(01)79035-5

journal_volume

36

pub_type

杂志文章

相关文献

JOURNAL OF PEDIATRIC SURGERY文献大全
  • Distension enterogenesis: increasing the size and function of small intestine.

    abstract：INTRODUCTION:The purpose of this study is to evaluate the feasibility of using saline infusion to lengthen small bowel while preserving intestinal enzymatic function. METHODS:Male Sprague-Dawley rats had a 3-cm jejunal segment taken out of continuity. A catheter was inserted in the proximal end, and the distal end was...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2006.02.017

    authors： Puapong DP,Wu BM,Lam MM,Atkinson JB,Dunn JC

    更新日期：2006-04-01 00:00:00

  • Intraoperative localization of small intestinal bleeding in an infant by methylene blue injection: a case report.

    abstract：:During the evaluation of patients with profuse gastrointestinal bleeding, it is often difficult to accurately localize bleeding sites in the small intestine. Moreover, during laparotomy, there may be no intraoperative findings to allow identification and resection of the bleeding lesion. Here the authors report a case...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/s0022-3468(98)90209-3

    authors： Mazziotti MV,Muldowney S,Darcy M,Hackett BP,Skinner MA

    更新日期：1998-05-01 00:00:00

  • Clinical features of mesenteric lymphatic malformation in children.

    abstract：BACKGROUND:Mesenteric lymphatic malformations (MLs) are a heterogeneous group of benign diseases of the lymphatic system that present with cystic dilated lymphatics of the mesentery. MLs are rare and represent less than 5% of all lymphatic malformations. The aims of this study were to analyze the characteristics of MLs...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2015.11.021

    authors： Kim SH,Kim HY,Lee C,Min HS,Jung SE

    更新日期：2016-04-01 00:00:00

  • Percutaneous inferior vena cava placement of tunneled silastic catheters for prolonged vascular access in infants.

    abstract：:In infants and children requiring prolonged and multiple central venous catheterizations, conventional cannulation sites may become thrombosed or stenotic, making inability to gain vascular access a life-threatening problem. The technique we use for the percutaneous placement of inferior vena caval tunneled silastic c...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/0022-3468(90)90341-6

    authors： Robertson LJ,Jaques PF,Mauro MA,Azizkhan RG,Robards J

    更新日期：1990-06-01 00:00:00

  • Paratesticular neuroblastoma with N-myc activation.

    abstract：:The authors describe a case of disseminated neuroblastoma discovered as a paratesticular tumor in a 7-month-old boy. The ectopic adrenal tissues adjacent to the paratesticular tumor and multiple lesions in the adrenal gland and skin suggested the possibility of multifocal primary tumors. Although infantile neuroblasto...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/0022-3468(93)90117-4

    authors： Matsunaga T,Takahashi H,Ohnuma N,Tanabe M,Yoshida H,Enomoto H,Horie H,Shirasawa H,Simizu B

    更新日期：1993-12-01 00:00:00

  • Acute acalculous cholecystitis as the initial presentation of primary Epstein-Barr virus infection.

    abstract：:The case of a 13-year-old girl with primary Epstein-Barr virus (EBV) infection and concomitant cholestatic hepatitis, which initially presented as acute acalculous cholecystitis (AAC), is described. The diagnosis of AAC was documented by clinical and ultrasonographic criteria, whereas acute EBV infection was confirmed...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2006.11.004

    authors： Prassouli A,Panagiotou J,Vakaki M,Giannatou I,Atilakos A,Garoufi A,Papaevangelou V

    更新日期：2007-01-01 00:00:00

  • Hirschsprung's disease discordant in monozygotic twins: a study of possible environmental factors in the production of colonic aganglionosis.

    abstract：:The occurrence of Hirschsprung's disease, with histologically verified colonic aganglionosis, in only 1 of 2 prematurely born and presumed identical (monozygotic) twins is reported. The occurrence of monozygotic twinning was supported by the observed sharing of a single and common placenta and by ABO and HLA identity ...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/0022-3468(79)90009-5

    authors： Moore TC,Landers DB,Lachman RS,Ament ME

    更新日期：1979-04-01 00:00:00

  • An unusual case of small bowel obstruction in a child caused by ingestion of water-storing gel beads.

    abstract：:Foreign body ingestion occurs most commonly in the pediatric population. Small bowel obstruction is a rare complication that can occur, and surgical intervention is required. We present the first report of a case of an 18-month-old child with a jejunal obstruction caused by ingestion of water-storing gel beads used fo...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2012.04.005

    authors： Moon JS,Bliss D,Hunter CJ

    更新日期：2012-09-01 00:00:00

  • Prenatal diagnosis and management of abdominal diseases in pediatric surgery.

    abstract：PURPOSE:The aim of this study was to investigate the prenatal courses and management of abdominal surgical diseases. METHODS:Of the 327 patients registered with our fetal treatment board since March 2002, 83 fetuses referred to the surgical department were enrolled for the current study. The prenatal diagnosis, sequen...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2004.08.039

    authors： Kuroda T,Kitano Y,Honna T,Sago H,Hayashi S,Saeki M

    更新日期：2004-12-01 00:00:00

  • Successful medical treatment of two patients with eosinophilic oesophagitis.

    abstract：BACKGROUND/PURPOSE:Significant oesophageal eosinophilia is associated with oesophagitis and gastroesophageal reflux (GER). Eosinophilic oesophagitis is a rare disease that causes thickening of the oesophageal wall, narrowing of the oesophageal lumen, and severe motor disturbance. METHODS AND RESULTS:Two 12 yr-old pati...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1053/jpsu.2002.30256

    authors： De Agustin JC,Sanz N,Canals MJ,Alvarez E,Morales JL,Soler J,Ollero JC,Vazquez J

    更新日期：2002-02-01 00:00:00

  • The microbial flora and antimicrobial therapy of neonatal peritonitis.

    abstract：:Data from 31 infants with gastrointestinal perforation were analyzed to determine the microorganisms usually present in the peritoneum and blood, and the antibiotic susceptibility of those organisms. Multimicrobial contamination of the peritoneal cavity was present in over one-half of the patients and 23% were found t...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/s0022-3468(80)80775-5

    authors： Bell MJ,Ternberg JL,Bower RJ

    更新日期：1980-08-01 00:00:00

  • Sacrococcygeal tumors: clinical characteristics and outcome of pediatric patients treated at South Egypt Cancer Institute. A retrospective analysis.

    abstract：BACKGROUND:Sacrococcygeal tumors (SCT) are relatively uncommon tumors affecting neonates, infants and children. The aim of this article is to clarify any special characterizations in natural history, clinical presentation and outcome of such tumors treated at South Egypt Cancer Institute, the only research center locat...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2013.04.015

    authors： Sayed HA,Ali AM,Hamza HM,Mourad AF,Eltayeb AA

    更新日期：2013-07-01 00:00:00

  • Lumbocostovertebral syndrome with associated VACTERL anomaly.

    abstract：:Lumbocostovertebral syndrome is a rare clinical association syndrome rarely accompanied by associated VACTERL anomalies. Only one similar case has been reported previously. We describe the second case, where a male neonate born at 38 weeks of gestation had an unusually high number of congenital anomalies including tho...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2010.06.005

    authors： Lyngdoh TS,Mahalik S,Naredi B,Samujh R,Khanna S

    更新日期：2010-09-01 00:00:00

  • Pathophysiology of congenital diaphragmatic hernia. XVI: Elevated pulmonary collagen in the lamb model of congenital diaphragmatic hernia.

    abstract：:The pathophysiologic features of congenital diaphragmatic hernia (CDH) include pulmonary hypoplasia, pulmonary hypertension, surfactant deficiency, and decreased pulmonary compliance. When the surfactant deficiency is corrected using exogenous surfactant therapy, the pulmonary compliance improves, but does not reach n...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/0022-3468(95)90019-5

    authors： Hassett MJ,Glick PL,Karamanoukian HL,Rossman JE,Wilcox DT,Azizkhan RG

    更新日期：1995-08-01 00:00:00

  • Rectal manometry, computed tomography, and functional results of anal atresia surgery.

    abstract：:Children with anal atresia often have compromised function. This is especially common with the anatomic "high lesion." Twenty-five patients have been studied using clinical evaluation, computed tomography (CT), and manometry to make an objective evaluation. The patients were an average of 9.6 years old; the male-to-fe...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/s0022-3468(05)80274-x

    authors： Doolin EJ,Black CT,Donaldson JS,Schwartz D,Raffensperger JG

    更新日期：1993-02-01 00:00:00

  • A different type of congenital lumbar hernia associated with the lumbocostovertebral syndrome.

    abstract：:Congenital lumbar hernia is rare in infancy and childhood, and its association with the lumbocostovertebral syndrome is even more unusual. Only 20 cases have been reported in the English literature. We present the case of a child with multiple costovertebral anomalies, undescended testis, and lateral abdominal wall he...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2007.08.065

    authors： Akçora B,Temiz A,Babayiğit C

    更新日期：2008-01-01 00:00:00

  • Congenital heart disease and heterotaxy: upper gastrointestinal fluoroscopy can be misleading and surgery in an asymptomatic patient is not beneficial.

    abstract：PURPOSE:Heterotaxy syndrome is associated with intestinal abnormalities. We sought to define the gastrointestinal anatomy and determine both the risk of volvulus and benefit of screening upper gastrointestinal fluoroscopy (UGI) in these patients. METHODS:Medical records from 2003 until 2011 at Children's Hospital Los ...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2012.10.033

    authors： Papillon S,Goodhue CJ,Zmora O,Sharma SS,Wells WJ,Ford HR,Upperman JS,Wang KS,Bushman GA,Kim R,Pierce JR

    更新日期：2013-01-01 00:00:00

  • Ovarian torsion: diagnosis of inclusion mandates earlier intervention.

    abstract：PURPOSE:The treatment of ovarian torsion (OT) is often delayed because of diagnostic uncertainty and dependence on radiologic confirmation. In contrast, when testicular torsion (TT) is suspected, diagnosis and management are expedited despite lack of certainty, and operative exploration is not delayed by radiologic inv...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2012.06.011

    authors： Piper HG,Oltmann SC,Xu L,Adusumilli S,Fischer AC

    更新日期：2012-11-01 00:00:00

  • Surgical repair of combined gastroschisis and sternal cleft.

    abstract：:We present a case of prenatally diagnosed gastroschisis combined with a sternal cleft, as well as the successful surgical management of this unusual condition. Successful management of gastroschisis combined with sternal cleft has not been reported before in the literature. ...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2005.03.034

    authors： Schmidt AI,Jesch NK,Glüer S,Ure BM

    更新日期：2005-06-01 00:00:00

  • The anterior mediastinal approach for management of tracheomalacia.

    abstract：BACKGROUND:Tracheomalacia occurs as a primary developmental defect or may be secondary to vascular compression. It is common in association with esophageal atresia and tracheoesophageal fistula. Collapse of the weak trachea is a cause of recurrent respiratory symptoms but may be severe and life threatening. METHODS:Be...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1053/jpsu.2000.16413

    authors： Morabito A,MacKinnon E,Alizai N,Asero L,Bianchi A

    更新日期：2000-10-01 00:00:00

  • Wilms' tumor: transureteral intravesical extension and presentation as urinary retention.

    abstract：:The authors report an unusual case of Wilms' tumor. The tumor grew transureterally into the urinary bladder, became dislodged, and presented as recurrent urinary infection with retention of urine after the child underwent nephroureterectomy. Such a presentation has not been reported earlier. ...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/s0022-3468(03)00211-2

    authors： Gupta A,Menon P,Rao KL,Trehan A,Marwaha RK,Kakkar N

    更新日期：2003-07-01 00:00:00

  • Hepaticoportoappendicostomy.

    abstract：:In one case of extrabiliary atresia, reconstruction of the biliary tract was performed by using the appendix. The child, who was 2 years old, is doing well without ascending cholangitis. This operation seems simple and satisfying because it seems to be more anatomic and more physiologic than the standard Kasai operati...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/s0022-3468(88)80030-7

    authors： Valla JS

    更新日期：1988-11-01 00:00:00

  • Does esophageal atresia influence the mother-infant interaction?

    abstract：PURPOSE:Chronic illness in infancy may influence parent-infant interaction. We assessed quality of mother-infant interaction in children with esophageal atresia (EA) and searched for predictors for impaired interaction. METHODS:The study group comprised 37 one-year-old infants with EA born in 1999 to 2002 and their mo...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2008.04.011

    authors： Faugli A,Emblem R,Veenstra M,Bjørnland K,Diseth TH

    更新日期：2008-10-01 00:00:00

  • Medial thickening of hepatic artery branches in biliary atresia. A morphometric study.

    abstract：BACKGROUND/PURPOSE:Medial layer hypertrophy of hepatic arterial branches may be associated with biliary atresia (BA) pathogenesis. This study aimed at evaluating medial layer thickness in hepatic arterial branches at portoenterostomy and liver transplantation. METHODS:The authors evaluated 1274 arterial branches both ...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2004.12.002

    authors： dos Santos JL,da Silveira TR,da Silva VD,Cerski CT,Wagner MB

    更新日期：2005-04-01 00:00:00

  • Magnetic resonance imaging of abdominal masses in children.

    abstract：:Seventeen children with abdominal masses (16 solid and 1 complex cystic) were evaluated by magnetic resonance imaging (MRI). Computed tomography (CT) was also performed in 12 cases. MRI findings were correlated with CT and histopathologic findings. In 10 cases MRI provided more specific diagnostic information than CT....

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/s0022-3468(05)80362-8

    authors： Vade A,Azienstein R

    更新日期：1993-01-01 00:00:00

  • Successful surgical treatment of two cases of congenital chylous ascites.

    abstract：:The authors report on 2 patients with congenital chylous ascites who underwent successful lymphatic duct ligation after a laparoscopic lymphoid dye test. Fetal ascites had been detected in both cases, and both babies were born with marked abdominal swelling. Given that conservative treatment by medium-chain triglyceri...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1053/jpsu.2001.27973

    authors： Mitsunaga T,Yoshida H,Iwai J,Matsunaga T,Kouchi K,Ohtsuka Y,Okada T,Hishiki T,Ohnuma N

    更新日期：2001-11-01 00:00:00

  • Castleman disease: surgical cure in pediatric patients.

    abstract：:Castleman disease is a rare disorder characterized by lymphoid hyperplasia which rarely manifests in children. We present 2 cases which highlight both histologic variants of this disease, and provide suggestions regarding workup and treatment with the goal of making practitioners aware of Castleman disease in the diff...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2008.09.024

    authors： Buesing K,Perry D,Reyes C,Abdessalam S

    更新日期：2009-01-01 00:00:00

  • Multiple segmental absence of intestinal musculature presenting as spontaneous isolated perforation in an extremely low-birth-weight infant.

    abstract：:Defect of the intestinal musculature is a rare condition. It may cause intestinal perforation or obstruction. It manifests itself mainly in the neonatal period and usually affects preterm infants. We describe one such case, which was first diagnosed as a spontaneous isolated intestinal perforation. Emergency laparotom...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2010.05.029

    authors： Oretti C,Bussani R,Janes A,Demarini S

    更新日期：2010-08-01 00:00:00

  • Age at presentation of common pediatric surgical conditions: Reexamining dogma.

    abstract：PURPOSE:The commonly cited ages at presentation of many pediatric conditions have been based largely on single center or outdated epidemiologic evidence. Thus, we sought to examine the ages at presentation of common pediatric surgical conditions using cases from large national databases. METHODS:A retrospective analys...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章,多中心研究

    doi：10.1016/j.jpedsurg.2014.01.039

    authors： Aboagye J,Goldstein SD,Salazar JH,Papandria D,Okoye MT,Al-Omar K,Stewart D,Lukish J,Abdullah F

    更新日期：2014-06-01 00:00:00

  • Midterm follow-up study of high-type imperforate anus after laparoscopically assisted anorectoplasty.

    abstract：PURPOSE:The aim of this study was to evaluate postoperative anal function of high-type imperforate anus after laparoscopically assisted anorectoplasty (LAARP). METHODS:Between 2000 and 2002, LAARP was performed in 13 patients with high-type imperforate anus. Clinical data of the LAARP group were compared with the post...

    journal_title：Journal of pediatric surgery

    pub_type： 杂志文章

    doi：10.1016/j.jpedsurg.2005.08.008

    authors： Kudou S,Iwanaka T,Kawashima H,Uchida H,Nishi A,Yotsumoto K,Kaneko M

    更新日期：2005-12-01 00:00:00