Parry-Romberg syndrome: a global survey of 205 patients using the Internet.

Abstract:

:Parry-Romberg syndrome (PRS) is a rare neurocutaneous disorder characterized by progressive facial hemiatrophy. In this study, 205 patients with PRS were surveyed using the Internet. Estimates of the frequency of limb involvement (19%), epilepsy (11%), and other clinical and etiologic features were obtained. There was a wide range of age at onset and considerable diagnostic overlap with scleroderma "en coup de sabre."

journal_name

Neurology

journal_title

Neurology

authors

Stone J

doi

10.1212/wnl.61.5.674

subject

Has Abstract

pub_date

2003-09-09 00:00:00

pages

674-6

issue

5

eissn

0028-3878

issn

1526-632X

journal_volume

61

pub_type

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