Abstract:
:A 10-year-old boy with congestive heart failure died in five months in spite of comprehensive medical treatment. Autopsy showed patchy areas of endocardial fibroelastosis of the left ventricle. The sister of this patient had followed a similar course at 13 years of age with death within six months of the onset of congestive failure. Her postmortem examination also showed endocardial fibroelastosis. The clinical presentation of familial endocardial fibroelastosis in the preteen and teenage years is a rare event. Probably the endocardial fibroelastosis was secondary to a familial nonobstructive cardiomyopathy.
journal_name
Pediatricsjournal_title
Pediatricsauthors
Singh A,Doyle EF,Danilowicz DA,Finegold MJdoi
10.1542/peds.61.3.410subject
Has Abstractpub_date
1978-03-01 00:00:00pages
410-6issue
3eissn
0031-4005issn
1098-4275journal_volume
61pub_type
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