Abstract:
:The incidence of the syndrome may be greater than is suspected. Patients present with recurrent respiratory infections and bronchiectasis. The symptoms are non-specific and indistinguishable from those of other chronic respiratory diseases. The diagnosis is often made several years after the first clinical complaints. The authors perform a brief review of the literature and report two cases of Mounier-Kuhn syndrome. One of the patients was diagnosed in childhood and the other in the fourth deca- de of life.
journal_name
Rev Port Pneumoljournal_title
Revista portuguesa de pneumologiaauthors
Marques A,Félix M,Barata F,Pires J,Estêvão MHsubject
Has Abstractpub_date
2007-09-01 00:00:00pages
721-7issue
5eissn
0873-2159issn
2172-6825journal_volume
13pub_type
杂志文章,评审abstract::Spontaneous hemothorax is a rare and potentially lethal neurofibromatosis' complication. Several pathological mechanisms may explain the associated vasculopathy: a) direct vascular invasion from adjacent tumors such as Shwannoma, neurofibroma or neurofibrosarcoma; b) vascular dysplasia with stenotic or aneurysm format...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/s0873-2159(15)30188-4
更新日期:2009-09-01 00:00:00
abstract::Male, 54 years old, with smoking habits. The patient complaints were cough, with bleeding secretions in the previous two months. Because of the persistence of the symptoms, a bronchoscopy was proposed. This exam showed multiple lesions in the trachea, nearly 2 cm above the vocal cords that compromised the airway and d...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:
更新日期:2006-05-01 00:00:00
abstract::Chronic Obstructive Pulmonary Disease (COPD) is one of the most common chronic diseases and a major cause of morbility and mortality. An imbalance between oxidants and antioxidants (oxidative stress) has been proposed as a critical event in the pathogenesis of COPD. The increased oxidative stress in patients with COPD...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/j.rppneu.2012.09.002
更新日期:2013-03-01 00:00:00
abstract::Clinical suspicion is the bedrock of a thorough clinical work-up, and a review of the clinical files with no definitive diagnosis is a must. Such a review can uncover rare diagnoses, such as Waldenstrom's macroglobulinaemia, a proliferative B-cell disease characterised by medular infiltration and monoclonocal IgM prod...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/s0873-2159(15)30292-0
更新日期:2008-11-01 00:00:00
abstract:INTRODUCTION:Surgical lung biopsy is a technique that presents a morbi-mortality rate of considerable importance. We analyze our experience with surgical lung biopsies for the diagnosis of diffuse lung disease and the effect produced on the indications for surgical biopsy in these pathologies after the publication of t...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/j.rppneu.2012.11.003
更新日期:2013-03-01 00:00:00
abstract::Amyotrophic Lateral Sclerosis (ALS) is a fast progressing neuromuscular disease that affects all but the extrinsic muscles of the eye and sphincters. The main cause of morbidity and mortality are the respiratory complications that usually start in a late stage of the diseases natural history. In a small number of case...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/s0873-2159(15)30619-x
更新日期:2004-11-01 00:00:00
abstract::Pulmonary hypertension is a rare but devastating disease, with poor prognosis and high mortality. The disease may present as Primary Pulmonary Hypertension where no clear aetiology can be identified, or be related to a variety of underlying conditions. This is a rare disease in paediatric age. The authors present the ...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/s0873-2159(15)30505-5
更新日期:2005-05-01 00:00:00
abstract::The World Health Organization (WHO) classification of lung cancers ranks the heterogeneous nonsmall cell lung cancer (N-SCLC) group, encompassing sarcoma or sarcoma-containing tumours under one heading: "carcinomas with pleomorphic, sarcomatoid or sarcomatous elements". This group contains entities such as pleomorphic...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章,评审
doi:
更新日期:2008-07-01 00:00:00
abstract::Brazil is one of the world leaders on traffic accidents. The present article studied the excessive daytime sleepiness of public transport drivers in two Brazilian's capitals and their level of attention. It was conducted here a descriptive transversal study of a convenient sample. For the evaluation were used: anthrop...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/j.rppneu.2013.01.001
更新日期:2013-07-01 00:00:00
abstract:INTRODUCTION:Obstructive Sleep Apnea (OSA) is associated with adverse effects in cardiovascular physiology. Some studies have connected this pathology with Cardiovascular Disease (CVD). AIM:Determine the prevalence of CVD in patients with OSA of different severity and verify the association between CVD and OSA. MATER...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/s0873-2159(15)30684-x
更新日期:2003-07-01 00:00:00
abstract:INTRODUCTION:Obesity has been associated with respiratory complications, and the majority of these complications occur in the Post-Anesthesia Care Unit (PACU). The aim of this study was to evaluate the outcome and incidence of adverse respiratory events (AREs) in obese patients during their stay in the PACU METHODS: We...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/j.rppneu.2013.04.002
更新日期:2014-01-01 00:00:00
abstract::Tuberous sclerosis (TS) is a rare, sporadic or autosomal dominant disease characterized by the triad of seizures, mental retardation and angiofibromas. Lungs are rarely involved in TS, and pulmonary involvement is almost always found in females. We report the case of a 52 year -old female, nonsmoker, with a history of...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/s0873-2159(15)30032-5
更新日期:2010-03-01 00:00:00
abstract:UNLABELLED:Amyotrophic lateral sclerosis (ALS) is a degenerative neurological disorder that affects motor neurons. Involvement of respiratory muscles causes the failure of the ventilator pump with more or less significant bulbar troubles. ALS course is highly variable but, in most cases, this disease entails a very sig...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章,多中心研究
doi:10.1016/j.rppneu.2014.03.001
更新日期:2014-07-01 00:00:00
abstract::Between 1999 and 2003 the Portuguese National Health Observatory, has conducted four telephone surveys (1998/99, 1999/00, 2001/02 and 2002/03) using the ECOS - Em Casa Observamos Saúde - panel of Portuguese families, with telephone aiming at studying the influenza vaccination coverage of the mainland Portuguese popula...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/s0873-2159(15)30572-9
更新日期:2004-03-01 00:00:00
abstract::Marfan syndrome is an autosomal dominant illness of the connective tissue, with typical skeletal, ocular and cardiovascular manifestations. Less frequently, pulmonary involvement occurs, namely spontaneous pneumothorax, which generally is recurrent and occurs in 4 -11% of cases. The authors describe a 14 -year -old bo...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/s0873-2159(15)30279-8
更新日期:2008-09-01 00:00:00
abstract:UNLABELLED:Asthma is a chronic illness of the airways that can reduce respiratory muscle strength due to the resulting hyperinflation or treatment with corticosteroids. One of the ways to evaluate this respiratory muscular weakness is the Maximal Inspiratory Pressure (PImax). METHODS:A systematic review of the databas...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章,评审
doi:
更新日期:2010-05-01 00:00:00
abstract::Acinetobacter is involved in a variety of infectious diseases primarily associated with healthcare. Recently there has been increasing evidence of the important role these pathogens play in community acquired infections. We report on the case of a previously healthy child, aged 28 months, admitted for fever, cough and...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/j.rppneu.2011.07.006
更新日期:2012-03-01 00:00:00
abstract::A 28-year-old neuromuscular patient chronically treated with nocturnal noninvasive ventilation developed pulmonary lobar atelectasis and daytime hypoxemia. Twenty four-hour 5L/min oxygen was begun, while mechanical cough assist aids were applied for seven days. In the following three days, treatment with nebulized Dor...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/j.rppneu.2012.12.002
更新日期:2014-01-01 00:00:00
abstract::The secondary hypertrophic osteoarthropathy is a systemic change that affects the bones, joints and soft tissues and is secondary to any intrathoracic pathology. It is a syndrome of chronic proliferative periostitis of the long bones, clubbing of the fingers of the hands, feet or both, and olyarthritis or polyarthriti...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:
更新日期:2009-07-01 00:00:00
abstract::Immigrants are a tuberculosis risk group. In Portugal, in 2000, they had an incidence rate 3.6 times higher than the global incidence, and were native, predominantly, from Angola and Cabo Verde. Being the Chest Disease Center of Venda Nova located in a residential area with a great number of immigrants, most of them l...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/s0873-2159(15)30677-2
更新日期:2003-05-01 00:00:00
abstract::Healthcare workers (HCWs) have an increased risk of tuberculosis (TB). Screening for latent tuberculosis infection and active TB is therefore essential in infection control programs. Tuberculin skin test (TST) and Interferon -gamma Release Assay (IGRA) were used simultaneously in 1686 HCWs between May 2007 and April 2...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:
更新日期:2010-03-01 00:00:00
abstract:INTRODUCTION:The Fiberoptic bronchoscopy (BRF) is an essential tool in diagnosis and therapy of respiratory diseases. The occurrence of transient fever after BRF has been documented in some studies. Its meaning hasn't yet been clarified. AIM:Determine the incidence of fever and bacteriemia in the 24 hours after BRF an...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/s0873-2159(15)30557-2
更新日期:2004-01-01 00:00:00
abstract::Lower lung lobe tuberculosis is less common than the classical radiological forms of pulmonary tuberculosis. However this radiological presentation has a particular relevance in patients with some associated pathological conditions, such as diabetes mellitus, HIV infection and chronic alcoholism. We make a review of t...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/s0873-2159(15)30112-4
更新日期:2009-01-01 00:00:00
abstract::Bronchiectasis is defined as an abnormal persistent bronchial dilatation usually associated with inflammation in the bronchial tree and lung parenchyma. The disease remains a common cause of significant morbidity and mortality, especially when associated with hereditary disorders such as cystic fibrosis, ciliary dyski...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章,评审
doi:10.1016/s0873-2159(15)30057-x
更新日期:2010-07-01 00:00:00
abstract::The differential diagnosis of Mycobacterium bovis is important in the control of transmission to the human population and also for treatment since M. bovis is naturally resistant to pyrazinamide. Eleven clinical isolates from the Fernando Fonseca Hospital with Spoligotypes indicative of M. bovis, through the absence o...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/s0873-2159(15)30528-6
更新日期:2005-11-01 00:00:00
abstract::The doctor-patient relationship should be established in ethical principles. The codes of conduct that guide the relation between the doctor and the patient are addressed to the physician (principle of beneficence and non-maleficence) or oriented to the patient (principle of autonomy). As such, in certain circumstance...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/s0873-2159(15)30151-3
更新日期:2009-05-01 00:00:00
abstract::Oxidative stress is a risk factor for bronchopulmonary dysplasia in the preterm newborn. Antioxidant defense is impaired in the preterm newborn. Oxidative stress is also involved in cell growth and development. The relationship between oxidative stress and cell growth needs to be understood before antioxidant therapy ...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章,评审
doi:10.1016/s0873-2159(15)30221-x
更新日期:2008-01-01 00:00:00
abstract:PURPOSE:Expression of ERCC1 has not been well described in fine-needle aspiration biopsies (FNABs) in patients with non-small cell lung cancer (NSCLC). We investigated the expression of ERCC1 in correlation with EGFR expression and clinicopathological factors in patients with NSCLC in order to determine if these play a...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/j.rppneu.2013.11.002
更新日期:2014-07-01 00:00:00
abstract:BACKGROUND:Long-term low frequency noise exposure (LFN) (< or = 500 Hz, including infrasound) may lead to the development of vibroacoustic disease (VAD), a systemic pathology characterized by the abnormal growth of extra-cellular matrices. The respiratory system is a target for LFN. Fibrosis of the respiratory tract ep...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:
更新日期:2006-07-01 00:00:00
abstract::We present four patients with non-small cell lung cancer treated in second and third line with Erlotinib. These are selected patients that obtained a good clinical response. Almost all presented cutaneous side effects. Rev Port Pneumol 2008; XIV (Supl 3): S65-S69. ...
journal_title:Revista portuguesa de pneumologia
pub_type: 杂志文章
doi:10.1016/S0873-2159(15)30324-X
更新日期:2008-10-01 00:00:00