[A child with pulmonary hypertension: from etiological study to therapeutic decisions].

Abstract:

:Pulmonary hypertension is a rare but devastating disease, with poor prognosis and high mortality. The disease may present as Primary Pulmonary Hypertension where no clear aetiology can be identified, or be related to a variety of underlying conditions. This is a rare disease in paediatric age. The authors present the clinical case of a 4 years old child, admitted in Paediatric Department of S. João Hospital for syncope episode. The diagnosis of pulmonary hypertension was made by echocardiogram. Ulterior studies revealed pulmonary disease (obliterans bronchiolitis). The treatment included a calcium channel blocker (diltiazem), an endothelin antagonist (bosentan) and supplemental oxygen. This is the first case of obliterans bronchiolitis diagnosed during etiological study for pulmonary hypertension, in our Pediatrics Department. In this case we could not determine the pulmonary disease precipitating event.

journal_name

Rev Port Pneumol

authors

Guardiano M,Maia AM,Correia C,Azevedo I,Lopes AR,da Silva ED,Moura CS,Marinho A

doi

10.1016/s0873-2159(15)30505-5

subject

Has Abstract

pub_date

2005-05-01 00:00:00

pages

327-35

issue

3

eissn

0873-2159

issn

2172-6825

pii

S0873-2159(15)30505-5

journal_volume

11

pub_type

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