Amino acid and protein requirements in a preterm infant with classic phenylketonuria.

Abstract:

:A preterm infant with classic phenylketonuria required rather less than 90 mg/kg of phenylalanine and between 270 and 290 mg/kg tyrosine daily to achieve a rate of weight gain of around 20 g/kg per day. Using Lofenalac as the low phenylalanine food, the intake of tyrosine, an essential amino acid for patients with phenylketonuria seemed to be limiting in respect of growth.

journal_name

Arch Dis Child

authors

Shortland D,Smith I,Francis DE,Ersser R,Wolff OH

doi

10.1136/adc.60.3.263

subject

Has Abstract

pub_date

1985-03-01 00:00:00

pages

263-5

issue

3

eissn

0003-9888

issn

1468-2044

journal_volume

60

pub_type

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