Abstract:
:The nosologic distinction between paramyotonia congenita and hyperkalemic periodic paralysis is somewhat blurred. Muscle membrane inexcitability induced by cooling seems to be characteristic of paramyotonia congenita. The effect of cooling on the maximal compound muscle action potential (CMAP) in patients with paramyotonia congenita was compared to that in patients with hyperkalemic periodic paralysis. Diminution in CMAP amplitude and area, which was observed in paramyotonia congenita, did not occur in hyperkalemic periodic paralysis. We suggest that this effect of cooling on the CMAP can be utilized in the differentiation of these two syndromes.
journal_name
Muscle Nervejournal_title
Muscle & nerveauthors
Subramony SH,Wee AS,Mishra SKdoi
10.1002/mus.880090804subject
Has Abstractpub_date
1986-10-01 00:00:00pages
700-3issue
8eissn
0148-639Xissn
1097-4598journal_volume
9pub_type
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