Progressive familial heart block type I in a korean patient.

Abstract:

:A 29-year-old man was referred to the emergency department with a complaint of abdominal pain and dizziness. He had experienced two previous syncopal episodes. His family history revealed that his mother and his two uncles had received permanent pacemaker implantation. His initial heart rate was 49 beats per minute. The electrocardiography (ECG) showed atrial flutter and right bundle branch block (RBBB) with left anterior fascicular block (LAFB). On admission, 24-hour Holter showed ventricular pause up to 16 seconds during syncope. Radio frequency catheter ablation (RFCA) of atrial flutter was performed. The ECG revealed bifascicular block (RBBB and LAFB) and first-degree atrioventricular block. He received a permanent pacemaker implantation. His brother's and his sister's ECGs also showed trifascicular block and the pedigree showed autosomal dominant inheritance. This patient was diagnosed with a progressive familial heart block (PFHB) type I. This would be the first report of a PFHB type I case documented in Korea.

journal_name

Korean Circ J

authors

Lee CK,Shin DH,Jang JK,Jang KH,Kim EK,Cheong SS,Yoo SY

doi

10.4070/kcj.2011.41.5.276

subject

Has Abstract

pub_date

2011-05-01 00:00:00

pages

276-9

issue

5

eissn

1738-5520

issn

1738-5555

journal_volume

41

pub_type

杂志文章
  • Recent Advances in Cardiac Magnetic Resonance Imaging.

    abstract::Cardiac magnetic resonance (CMR) imaging provides accurate anatomic information and advanced soft contrast, making it the reference standard for assessing cardiac volumes and systolic function. In this review, we summarize the recent advances in CMR sequences. New technical development has widened the use of CMR imagi...

    journal_title:Korean circulation journal

    pub_type: 杂志文章,评审

    doi:10.4070/kcj.2018.0246

    authors: Lee SE,Nguyen C,Xie Y,Deng Z,Zhou Z,Li D,Chang HJ

    更新日期:2019-02-01 00:00:00

  • Potential inherited causes of recurrent prosthetic mitral valve thrombosis in a pregnant patient suffering from recurrent miscarriage.

    abstract::An effective anticoagulation is critical in pregnant patients with prosthetic heart valves. Inherited disorders may interfere with the coagulation cascade and may be associated with obstetrical complications as well as with prosthetic valve-derived complications. The patient in the present case had a history of recurr...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2014.44.4.268

    authors: Kalcik M,Gursoy MO,Karakoyun S,Yesin M,Astarcioglu MA,Ozkan M

    更新日期:2014-07-01 00:00:00

  • Remote Ischemic Conditioning by Effluent Collected from a Novel Isolated Hindlimb Model Reduces Infarct Size in an Isolated Heart Model.

    abstract:BACKGROUND AND OBJECTIVES:Experimental protocols for remote ischemic conditioning (RIC) utilize models in which a tourniquet is placed around the hindlimb or effluent is collected from an isolated heart. In analyzing the humoral factors that act as signal transducers in these models, sampled blood can be influenced by ...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2017.0092

    authors: Youn YJ,Yoo BS,Son JW,Lee JW,Ahn MS,Ahn SG,Kim JY,Lee SH,Yoon J,Eom YW,Oh JE,Choi SK

    更新日期:2017-09-01 00:00:00

  • Sacubitril/Valsartan in Asian Patients with Heart Failure with Reduced Ejection Fraction.

    abstract::The Prospective comparison of Angiotensin Receptor-neprilysin inhibitor (ARNI) with Angiotensin converting enzyme inhibitor (ACEI) to Determine Impact on Global Mortality and morbidity in Heart Failure (HF) trial (PARADIGM-HF) showed that adding a neprilysin inhibitor (sacubitril) to a renin-angiotensin system blocker...

    journal_title:Korean circulation journal

    pub_type: 杂志文章,评审

    doi:10.4070/kcj.2019.0136

    authors: Dewan P,Docherty KF,McMurray JJV

    更新日期:2019-06-01 00:00:00

  • Mechanisms of Platelet Activation and Integrin αIIβ3.

    abstract::Platelet aggregation is not only an essential part of hemostasis, but also initiates acute coronary syndrome or ischemic stroke. The precise understanding of the activation mechanism of platelet aggregation is fundamental for the development of more effective agents against platelet aggregation. Adenosine diphosphate,...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2012.42.5.295

    authors: Joo SJ

    更新日期:2012-05-01 00:00:00

  • Acute Pulmonary Embolism: Focus on the Clinical Picture.

    abstract::Acute pulmonary embolism (APE) is characterized by numerous clinical manifestations which are the result of a complex interplay between different organs; the symptoms are therefore various and part of a complex clinical picture. For this reason, it may not be easy to make an immediate diagnosis. This is a comprehensiv...

    journal_title:Korean circulation journal

    pub_type: 杂志文章,评审

    doi:10.4070/kcj.2017.0314

    authors: Morrone D,Morrone V

    更新日期:2018-05-01 00:00:00

  • Small left atrial size complicating percutaneous transcatheter device closure of secundum atrial septal defect with conventional approach.

    abstract:BACKGROUND AND OBJECTIVES:Transcatheter device closure becomes the first option for treating secundum atrial septal defect (ASD), but the conventional method is sometimes unsuccessful even when the defect size indicates the closure to be feasible. To increase the success rate, modified methods have been introduced and ...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2015.45.3.216

    authors: Ko HK,Kang SY,Yu JJ,Ko JK,Kim YH

    更新日期:2015-05-01 00:00:00

  • Temporal Trends of Cardiac Implantable Electronic Device Implantations: a Nationwide Population-based Study.

    abstract:BACKGROUND AND OBJECTIVES:Implantation of cardiac implantable electronic devices (CIED), including permanent pacemakers (PM), implantable cardioverter-defibrillators (ICD), and cardiac resynchronization therapy (CRT) devices, has increased significantly over the past several years. However, limited data exists regardin...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2018.0444

    authors: Lee JH,Lee SR,Choi EK,Jeong J,Park HD,You SJ,Lee SS,Oh S

    更新日期:2019-09-01 00:00:00

  • Prognosis and natural history of drug-related bradycardia.

    abstract:BACKGROUND AND OBJECTIVES:The prognosis and natural history of bradycardia related to drugs such as beta-blockers and non-dihydropyridine calcium channel blockers are not well known. SUBJECTS AND METHODS:We retrospectively analyzed 38 consecutive patients (age 69+/-11, 21 women) with drug-related bradycardia (DRB) bet...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2009.39.9.367

    authors: Lee JH,Ryu HM,Bae MH,Kwon YS,Lee JH,Park Y,Heo JH,Lee YS,Yang DH,Park HS,Cho Y,Chae SC,Kim YN,Jun JE,Park WH

    更新日期:2009-09-01 00:00:00

  • Stent fracture at the proximal shaft of the left main stem.

    abstract::Stent fracture is likely to be caused due to mechanical stress at the hinge point or kinking movement at the point of aneurysm formation with stent malapposition. To our knowledge, this is the first published report of stent fracture at the proximal shaft of the left main stem in a patient with acute myocardial infarc...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2011.41.12.763

    authors: Lee JH,Seo SM,Kim EO,Ahn HJ,Lee YW,Cho YH,Baek I,Oh YS,Yu J,Seung KB

    更新日期:2011-12-01 00:00:00

  • One-Year Clinical Outcomes among Patients with Metabolic Syndrome and Acute Myocardial Infarction.

    abstract:BACKGROUND AND OBJECTIVES:Metabolic syndrome (MetS) is an important risk factor for cardiovascular disease. However, the clinical outcome of acute myocardial infarction (AMI) with MetS has not been well examined. The purpose of this study was to evaluate the clinical outcomes of AMI patients with MetS. SUBJECTS AND ME...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2013.43.8.519

    authors: Ji MS,Jeong MH,Ahn Y,Kim YJ,Chae SC,Hong TJ,Seong IW,Chae JK,Kim CJ,Cho MC,Rha SW,Bae JH,Seung KB,Park SJ,Other Korea Acute Myocardial Infarction Registry Investigators.

    更新日期:2013-08-01 00:00:00

  • The Use Pattern and Clinical Impact of New Antiplatelet Agents Including Prasugrel and Ticagrelor on 30-day Outcomes after Acute Myocardial Infarction in Korea: Korean Health Insurance Review and Assessment Data.

    abstract:BACKGROUND AND OBJECTIVES:Despite the favorable efficacy of new antiplatelet agents demonstrated in randomized controlled trials, their clinical implications in Korea are unclear. The purpose of this study was to investigate trends in antiplatelet agent use for acute myocardial infarction (AMI) and their impact on 30-d...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2017.0072

    authors: Kim C,Shin DH,Ahn CM,Kim JS,Kim BK,Ko YG,Choi D,Hong MK,Park J,Lee H,Choi YJ,Choi YS,Oh SK,Jang Y

    更新日期:2017-11-01 00:00:00

  • Acute and subacute stent thrombosis in a patient with clopidogrel resistance: a case report.

    abstract::Drug-eluting stents (DES) are considered the treatment of choice for most patients with obstructive coronary artery disease when percutaneous intervention (PCI) is feasible. However, stent thrombosis seems to occur more frequently with DES and occasionally is associated with resistance to anti-platelet drugs. We have ...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2009.39.10.434

    authors: Kim SS,Jeong MH,Kim HK,Bae SY,Ryu KH,Cho KH,Kim MC,Park KH,Sim DS,Hong YJ,Kim JH,Ahn Y,Kang JC

    更新日期:2009-10-01 00:00:00

  • Safety and Efficacy of a New Ultrathin Sirolimus-Eluting Stent with Abluminal Biodegradable Polymer in Real-World Practice.

    abstract:BACKGROUND AND OBJECTIVES:Recently, Genoss drug-eluting stent (DES)™ stent comprising cobalt-chromium platform with an ultrathin strut thickness, sirolimus, and an abluminal biodegradable polymer was developed. Owing to the lack of substantial evidence for the safety and efficacy of this stent, we report 12-month resul...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2019.0258

    authors: Youn YJ,Yoo SY,Lee JW,Ahn SG,Lee SH,Yoon J,Park JH,Choi WG,Cho S,Lim SW,Jang YS,Kwon KH,Lee NH,Doh JH,Kang WC,Jeon DW,Lee BK,Heo JH,Hong BK,Choi HH

    更新日期:2020-04-01 00:00:00

  • Nitric oxide synthase inhibition attenuates cardiac response to hemodilution with viscogenic plasma expander.

    abstract:BACKGROUND AND OBJECTIVES:Increased vascular wall shear stress by elevated plasma viscosity significantly enhances the endothelial nitric oxide synthase (eNOS) activity during an acute isovolemic hemodilution. Also the modulation of plasma viscosity has effects on the cardiac function that were revealed if a left ventr...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2014.44.2.105

    authors: Chatpun S,Cabrales P

    更新日期:2014-03-01 00:00:00

  • Congenital Absence of Superior Vena Cava with no Manifestation of Superior Vena Cava Syndrome.

    abstract::Total absence of superior vena cava (SVC) is a very rare anomaly, and the patient usually suffers from SVC syndrome or conduction disturbances. We report an asymptomatic 27 year-old male, with complete absence of SVC. Transthoracic echocardiography and computed tomography demonstrated the absence of SVC and other cong...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2016.46.5.743

    authors: Park CS,Kim JJ,Park JJ

    更新日期:2016-09-01 00:00:00

  • Clopidogrel versus Aspirin after Dual Antiplatelet Therapy in Acute Myocardial Infarction Patients Undergoing Drug-Eluting Stenting.

    abstract:BACKGROUND AND OBJECTIVES:There is a paucity of data regarding the benefit of clopidogrel monotherapy after dual antiplatelet therapy (DAPT) in patients treated with drug-eluting stents (DES). This study compared outcome between clopidogrel versus aspirin as monotherapy after DES for acute myocardial infarction (MI). ...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2019.0166

    authors: Sim DS,Jeong MH,Kim HS,Gwon HC,Seung KB,Rha SW,Chae SC,Kim CJ,Cha KS,Park JS,Yoon JH,Chae JK,Joo SJ,Choi DJ,Hur SH,Seong IW,Cho MC,Kim DI,Oh SK,Ahn TH,Hwang JY,KAMIR-NIH registry investigators.

    更新日期:2020-02-01 00:00:00

  • Acute Hemodynamic Changes after Single Administration of Udenafil in Pulmonary Arterial Hypertension: a Phase IIa Study.

    abstract:BACKGROUND AND OBJECTIVES:Udenafil, a new phosphodiesterase-5 inhibitor (PDE5i), has been used to treat erectile dysfunction. Given the proven benefit of PDE5i in pulmonary arterial hypertension (PAH), we evaluated serial hemodynamic changes after single udenafil administration to determine the appropriate therapeutic ...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2018.0281

    authors: Chang SA,Kim HK,Chang HJ,Kim DK

    更新日期:2019-04-01 00:00:00

  • High Plasma Levels of the B-type Natriuretic Peptide in Patients Without Heart Failure: Is There Clinical Significance?

    abstract::We report a case of a 19-year-old female with an elevated plasma B-type natriuretic peptide (BNP) level, but without evidence of heart failure (HF). She presented with non-specific chest pain and a high level of the B-type natriuretic peptide, despite having unremarkable findings on physical examination, laboratory an...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2010.40.3.141

    authors: Yu LH,Kim MH,Park JS,Cha KS,Park TH,Kim YD

    更新日期:2010-03-01 00:00:00

  • Statin Therapy for Primary Prevention of Atrial Fibrillation: Guided by CHADS2/CHA2DS2VASc Score.

    abstract::Atrial fibrillation (AF) is the most common arrhythmia and is associated with increased cardiovascular morbidity and mortality. The anti-arrhythmic effect of statins on AF prevention appears to be highly significant in most clinical studies. However, some discrepancies do exist among different clinical studies. Differ...

    journal_title:Korean circulation journal

    pub_type: 杂志文章,评审

    doi:10.4070/kcj.2014.44.4.205

    authors: Hung CY,Hsieh YC,Huang JL,Lin CH,Wu TJ

    更新日期:2014-07-01 00:00:00

  • Role of Soluble ST2 as a Marker for Rejection after Heart Transplant.

    abstract:BACKGROUND AND OBJECTIVES:Endomyocardial biopsy is obligatory during the first year after heart transplant (HTx) for the surveillance of acute rejection. Previous attempts using cardiac biomarkers for the detection of rejection failed to show enough evidence to substitute endomyocardial biopsy. Therefore, this study so...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2016.46.6.811

    authors: Lee GY,Choi JO,Ju ES,Lee YJ,Jeon ES

    更新日期:2016-11-01 00:00:00

  • Anomalous separate origin of left anterior descending coronary artery: presented as acute anterior myocardial infarction.

    abstract::Coronary artery anomalies are rare presentations in primary percutaneous coronary interventions of acute myocardial infarction. Herein, we report the case of a 59-year-old man with acute anterior myocardial infarction who had anomalous separate origin of left anterior descending artery (LAD) and left circumflex artery...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2013.43.6.408

    authors: Hong MY,Shin DH,Kwon JH,Chang WS,Choi KU,Song YA,Oh KH,Lee JH

    更新日期:2013-06-01 00:00:00

  • Rationale and Design of the High Platelet Inhibition with Ticagrelor to Improve Left Ventricular Remodeling in Patients with ST-Segment Elevation Myocardial Infarction (HEALING-AMI) Trial.

    abstract:BACKGROUND AND OBJECTIVES:Impaired recovery from left ventricular (LV) dysfunction is a major prognostic factor after myocardial infarction (MI). Because P2Y₁₂ receptor blockade inhibits myocardial injury, ticagrelor with off-target properties may have myocardial protection over clopidogrel. In animal models, ticagrelo...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2018.0415

    authors: Park Y,Choi SW,Oh JH,Shin ES,Lee SY,Kim J,Kim W,Suh JW,Yang DH,Hong YJ,Chan MY,Koh JS,Hwang JY,Park JH,Jeong YH,HEALING-AMI Trial Investigators.

    更新日期:2019-07-01 00:00:00

  • Clinical characteristics and prognostic factors of stress-induced cardiomyopathy.

    abstract:BACKGROUND AND OBJECTIVES:Stress-induced cardiomyopathy (SCM) is characterized by a transient left ventricular (LV) dysfunction due to emotional and physical stress. There are limited data about the clinical characteristics in Korean patients. We sought to clarify the clinical features and prognosis in patients with SC...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2010.40.6.277

    authors: Lee JW,Kim JY,Youn YJ,Sung JK,Lee NS,Lee KH,Yoo BS,Lee SH,Yoon J,Choe KH

    更新日期:2010-06-01 00:00:00

  • Effect of abciximab on the levels of circulating microparticles in patients with acute myocardial infarction treated by primary angioplasty.

    abstract:BACKGROUND AND OBJECTIVES:We investigated the effect of the additional use of abciximab during percutaneous coronary intervention (PCI) on the level of procoagulant microparticles (MPs) in patients with ST-segment elevation myocardial infarction (STEMI) who had undergone primary PCI. SUBJECTS AND METHODS:In this study...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2013.43.9.600

    authors: Cha JJ,Kim JY,Choi EY,Min PK,Cho M,Lee DL,Hong SY,Yoon YW,Lee BK,Hong BK,Rim SJ,Kwon HM

    更新日期:2013-09-01 00:00:00

  • Morbidity and Mortality of Very Low Birth Weight Infants with Congenital Heart Disease.

    abstract:BACKGROUND AND OBJECTIVES:This study aimed to provide morbidity and mortality information on very low birth weight (VLBW) infants with congenital heart disease (CHD-VLBWs). METHODS:The study used a 10-year cohort of VLBW infants from a single institution. CHD was classified according to International Classification of...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2020.0135

    authors: Song WS,Kim CY,Lee BS,Kim EAR,Kim KS,Jung E

    更新日期:2020-12-01 00:00:00

  • Revascularization for Left Main and Multivessel Coronary Artery Disease: Current Status and Future Prospects after the EXCEL and NOBLE Trials.

    abstract::Revascularization of severe left main and multivessel coronary artery disease has been shown to improve survival in both stable ischemic heart disease and acute coronary syndrome. While revascularization with coronary artery bypass surgery for these disease entities carries class I recommendation in most current guide...

    journal_title:Korean circulation journal

    pub_type: 杂志文章,评审

    doi:10.4070/kcj.2018.0078

    authors: Al-Hijji M,El Sabbagh A,Holmes DR

    更新日期:2018-06-01 00:00:00

  • Analysis of Cardiovascular Risk Factors in Adults with Congenital Heart Disease.

    abstract:BACKGROUND AND OBJECTIVES:The objective of this study was to analyze cardiovascular risk factors in adults with congenital heart disease (ACHD). SUBJECTS AND METHODS:The subjects for this study comprised 135 patients, aged 18 years and above, who visited the ACHD clinic at the Samsung Medical Center and 135 adults wit...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2015.45.5.416

    authors: Moon JR,Song J,Huh J,Kang IS,Park SW,Chang SA,Yang JH,Jun TG

    更新日期:2015-09-01 00:00:00

  • Catheter Ablation of Ventricular Arrhythmias via the Radial Artery in a Patient With Prior Myocardial Infarction and Peripheral Vascular Disease.

    abstract::Herein, we present a case of a successful catheter ablation of ventricular tachycardia (VT) using a radial artery approach in a post-myocardial infarction patient, who had an implantable cardioverter-defibrillator and peripheral artery disease. Although the patient did not use antiarrhythmic drugs, the patient experie...

    journal_title:Korean circulation journal

    pub_type: 杂志文章

    doi:10.4070/kcj.2012.42.9.632

    authors: Kim J,Han D,Sohn C,Kim JS,Park YH

    更新日期:2012-09-01 00:00:00

  • Left Ventricular Assist Devices (LVADS): History, Clinical Application and Complications.

    abstract::Congestive heart failure is a major cause of morbidity and mortality as well as a major health care cost in the developed world. Despite the introduction of highly effective heart failure medical therapies and simple devices such as cardiac resynchronization therapy that reduce mortality, improve cardiac function and ...

    journal_title:Korean circulation journal

    pub_type: 杂志文章,评审

    doi:10.4070/kcj.2019.0161

    authors: Eisen HJ

    更新日期:2019-07-01 00:00:00