Histologic changes resembling the verrucous phase of incontinentia pigmenti within epidermal nevi: report of two cases.

abstract：:Familial hyperpigmentation, or melanosis universalis hereditaria, is a rare hyperpigmentary disorder with onset in infancy. Here, we describe monozygotic twins with similar pattern of progressive hyperpigmentation with onset in early neonatal period without any family history. Histopathological examination showed incr...

journal_title：Pediatric dermatology

authors： Gupta N,Sharma MC,Ramam M,Kabra M

更新日期：2011-01-01 00:00:00

abstract：:PLACK syndrome (OMIM 616295) is a form of generalized peeling skin syndrome (GPSS; OMIM 270300). It is an autosomal recessive genodermatosis caused by pathogenic mutations in CAST, which encodes calpastatin, an endogenous specific inhibitor of calpain, a calcium-dependent cysteine protease. We present a 5-year-old gir...

journal_title：Pediatric dermatology

authors： Boggs JME,Irvine AD

更新日期：2020-10-03 00:00:00

abstract：:We cared for 124 pediatric patients with a histologic diagnosis of Langerhans' cell histiocytosis (histiocytosis X) over a period of 14 years. Clinical, laboratory, and radiographic findings were analyzed. The most frequent manifestations were bone lesions, lymph node involvement, and skin infiltration. Liver disease ...

journal_title：Pediatric dermatology

authors： Rivera-Luna R,Martinez-Guerra G,Altamirano-Alvarez E,Martinez-Avalos A,Cardenas-Cardoz R,Ayon-Cardenas A,Ruiz-Maldonado R,Lopez-Corella E

更新日期：1988-08-01 00:00:00

abstract：BACKGROUND:Acrodermatitis acidemica is a recently proposed term for the rash that is similar to acrodermatitis enteropathica, which is encountered in organic acidemias. However, acrodermatitis enteropathica-like eruption may be seen in metabolic disorders other than organic acidemias. OBJECTIVE:The aim of this study w...

journal_title：Pediatric dermatology

authors： Tabanlioğlu D,Ersoy-Evans S,Karaduman A

更新日期：2009-03-01 00:00:00

abstract：:Infantile myofibromatosis is a rare benign tumor of infancy and childhood that occurs in solitary, multiple, and generalized forms with similar histology but different clinicopathologic and prognostic implications. Even solitary tumors need follow-up, as the type of presentation will be determined over time. It is nec...

journal_title：Pediatric dermatology

authors： Jurcić V,Perković T,Pohar-Marinsek Z,Hvala A,Lazar I

更新日期：2003-07-01 00:00:00

abstract：:Juvenile xanthogranuloma is a benign, self-healing disorder with characteristic lesions mainly involving the skin. Although most patients with juvenile xanthogranuloma have only cutaneous symptoms, recent articles have documented extracutaneous manifestations: systemic involvement of many organs has been reported and ...

journal_title：Pediatric dermatology

authors： Aparicio G,Mollet J,Bartralot R,Bodet D,Heras C,Bassas P,Virós A,García-Patos V

更新日期：2008-07-01 00:00:00

abstract：:A 15-month-old girl had orange papules that formed V-shaped lines on her back. The clinical evolution and histology were compatible with the diagnosis of a lichen striatus-like eruption, adopting a special morphology by following Blaschko lines. ...

journal_title：Pediatric dermatology

authors： Jordá E,Zayas AI,Revert A,Donnini A,Ramón D,Torres V

更新日期：1991-06-01 00:00:00

abstract：:Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a rare and aggressive malignancy of the skin and hematopoietic system. There are few pediatric cases reported in the literature. Management of primary cutaneous BPDCN is challenging because, despite an apparently indolent clinical presentation, rapid disseminatio...

journal_title：Pediatric dermatology

authors： Rivas-Calderón MK,Cheirif-Wolosky O,Rosas-Romero ME,Toussaint-Caire S,Duran-Mckinster C,González-Pedroza ML,López-Santiago NC,García-Romero MT

更新日期：2020-12-04 00:00:00

abstract：:Skin prick tests were performed in 12 children with atopic eczema before and after 2 weeks of treatment with topical mometasone furoate and tacrolimus. Both treatments significantly suppressed the allergen wheal size. Mometasone furoate reduced the histamine wheal size as well. Skin prick testing in children treated w...

journal_title：Pediatric dermatology

authors： Gradman J,Wolthers OD

更新日期：2008-03-01 00:00:00

abstract：OBJECTIVES:To identify clinical factors associated with complications of periocular infantile hemangioma (IH) and monitor improvement in complication rates post-treatment. METHODS:Retrospective cohort study. Eighty-nine patients diagnosed with periocular IH at a pediatric dermatology clinic of a tertiary care center b...

journal_title：Pediatric dermatology

authors： Zhao J,Huang AH,Rainer BM,Kryatova MS,Eghrari AO,Wang J,Puttgen KB,Cohen BA

更新日期：2019-11-01 00:00:00

abstract：:A 4-year-old girl with an established diagnosis of atopic dermatitis, previously severe and treated with cyclosporine, developed widespread papules that demonstrated changes consistent with epidermodysplasia verruciformis on biopsy. Human papilloma virus (HPV) typing was performed and was consistent with epidermodyspl...

journal_title：Pediatric dermatology

authors： Fernandez KH,Rady P,Tyring S,Stone MS

更新日期：2014-05-01 00:00:00

abstract：:Two sporadic cases of Heck disease in Polish girls were associated with human papillomavirus 13. No other children and nobody from their surroundings had similar lesions. The course of the disease was chronic in both patients. The lesions regressed spontaneously in one girl within several years after some of the papul...

journal_title：Pediatric dermatology

authors： Obalek S,Janniger C,Jablonska S,Favre M,Orth G

更新日期：1993-09-01 00:00:00

abstract：:Melanotic neuroectodermal tumor of infancy (MNTI) is an uncommon lesion with remarkably consistent histopathologic features that arises primarily in the pediatric population. We describe a MNTI arising in the anterior maxilla of a 6-month-old boy. ...

journal_title：Pediatric dermatology

authors： Magliocca KR,Pfeifle RM,Bhattacharyya I,Cohen DM

更新日期：2012-09-01 00:00:00

abstract：BACKGROUND/OBJECTIVES:Epidemiologic studies of children with alopecia areata (AA) are sparse, and there are no studies that focus on the youngest children with AA. Evaluation of the clinical presentations of AA in children <4 years of age was performed in order to identify the prognostic factors for disease progression...

journal_title：Pediatric dermatology

authors： Rangu S,Rogers R,Castelo-Soccio L

更新日期：2019-11-01 00:00:00

abstract：:In contrast to adolescent acne, infantile acne (IA) is a rare condition with only a limited body of available literature. In this descriptive, retrospective study, we reviewed six cases from 2002 to 2010 treated with oral isotretinoin. The average age of onset was 6.16 months (range 0-21 mos). Consistent with the prev...

journal_title：Pediatric dermatology

authors： Miller IM,Echeverría B,Torrelo A,Jemec GB

更新日期：2013-09-01 00:00:00

abstract：:Lichen planus (LP) in children is a rare entity. We report 23 cases of childhood LP seen over a period of 7 years. Ninety-six percent of the children were of Arab ancestry. There were 52% boys and 48% girls. Classic LP was the most common clinical variant (70%), followed by eruptive generalized LP (13%). A majority of...

journal_title：Pediatric dermatology

authors： Nanda A,Al-Ajmi HS,Al-Sabah H,Al-Hasawi F,Alsaleh QA

更新日期：2001-01-01 00:00:00

abstract：:Mutations in the p63 gene have been identified in five human disorders characterized by varying degrees of limb anomalies, ectodermal dysplasia, and facial clefts. We report a new point mutation in the p63 gene in a family in which the mother was initially diagnosed with Rapp-Hodgkin syndrome and her two offspring man...

journal_title：Pediatric dermatology

authors： Steele JA,Hansen H,Arn P,Kwong PC

更新日期：2005-09-01 00:00:00

abstract：:We report an Italian prepubescent girl with the typical clinical and histologic features of prurigo pigmentosa associated with an atopic diathesis. The dermatitis disappeared after treatment with minocycline, leaving a brown, reticulated hyperpigmentation, with no recurrence. The association with an atopic diathesis c...

journal_title：Pediatric dermatology

authors： Cota C,Donati P,Amantea A

更新日期：2007-05-01 00:00:00

abstract：:Transient reactive papulotranslucent acrokeratoderma is a rare palmoplantar keratoderma seen predominantly in adolescent and young adult women. Clinically it is characterized by translucent white papules generally involving the palmar surfaces after exposure to water. The typical "hands-in-the-bucket" sign, which is n...

journal_title：Pediatric dermatology

authors： Neri I,Bianchi F,Patrizi A

更新日期：2006-01-01 00:00:00

abstract：:Demodex mites are commensal inhabitants of the pilosebaceous unit that are typically absent or at low numbers in childhood. When they are present, they can cause a primary eruption or exacerbate an underlying facial dermatosis. Here we report five cases of demodicosis occurring in childhood, the clinical presentations...

journal_title：Pediatric dermatology

authors： Douglas A,Zaenglein AL

更新日期：2019-09-01 00:00:00

abstract：BACKGROUND/OBJECTIVE:Pediatric hematopoietic stem cell transplantation (HSCT) patients are at an increased risk for skin cancers. Sun exposure is a significant modifiable environmental risk factor. While patient education on sun protection and avoidance behaviors with regular dermatology evaluations are crucial for ped...

journal_title：Pediatric dermatology

authors： Li EB,Song JS,Huang JT,Hawryluk EB,London WB,Guo D,Sridharan M,Fisher DE,Rea CJ,Lehmann LE,Duncan CN

更新日期：2019-11-01 00:00:00

abstract：:We examined a father and son affected by Ehlers-Danlos syndrome type II. Both patients had micrognathia together with ligament and skin hyperlaxity. The son exhibited complete cleft palate. Ultrastructural studies revealed abnormal collagen fibrils in the dermis of both patients. In the child the most striking alterat...

journal_title：Pediatric dermatology

authors： Rizzo R,Contri MB,Micali G,Quaglino D,Pavone L,Ronchetti IP

更新日期：1987-11-01 00:00:00

abstract：:Early recognition of the hyperlipoproteinemias is a crucial element in preventing premature coronary artery disease. Xanthomas provide a cutaneous marker of the silent, underlying pathology. Identifying them, and understanding their relation to the inherited hyperlipoproteinemias may facilitate early diagnosis of hype...

journal_title：Pediatric dermatology

authors： Maher-Wiese VL,Marmer EL,Grant-Kels JM

更新日期：1990-09-01 00:00:00

abstract：:A child born with the harlequin fetus abnormality survived and showed a surprising degree of spontaneous improvement in the first six weeks of life. At this age etretinate was instituted, producing considerable further resolution. The child is now over 2 years old. ...

journal_title：Pediatric dermatology

authors： Rogers M,Scraf C

更新日期：1989-09-01 00:00:00

abstract：:Acute genital ulcers rarely occur in nonsexually active young girls. When present, they can cause significant physical and emotional distress for the patient and her parents, and prompt an evaluation for sexual abuse and sexually transmitted diseases. With this review, we aim to further characterize acute genital ulce...

journal_title：Pediatric dermatology

authors： Rosman IS,Berk DR,Bayliss SJ,White AJ,Merritt DF

更新日期：2012-03-01 00:00:00

abstract：:Normolipemic plane xanthoma normally occurs in adults. We report the atypical instance of a 9-year-old boy who developed disseminated, flat, yellow-brown plaques up to 2 to 3 cm without any complaints. The histology showed the hallmarks of xanthoma, including the presence of CD68+ foam cells and Touton giant cells. No...

journal_title：Pediatric dermatology

authors： Hofmann M,Zappel K,Trefzer U,Audring H,Albrecht-Nebe H,Sterry W,Blume-Peytavi U

更新日期：2005-03-01 00:00:00

abstract：:Chilblains, or pernio, are cutaneous lesions that may accompany systemic illnesses including states of malnutrition and autoimmune diseases. We report an adolescent girl in whom chilblains were the chief presenting sign of celiac disease. A gluten-free diet led to weight gain and resolution of the chilblains. We specu...

journal_title：Pediatric dermatology

authors： St Clair NE,Kim CC,Semrin G,Woodward AL,Liang MG,Glickman JN,Leichtner AM,Binstadt BA

更新日期：2006-09-01 00:00:00

abstract：BACKGROUND:Children with congenital melanocytic nevi (CMN) were historically managed with surgical removal to lower the risk of malignant transformation. The evolving literature over the last decade has indicated a significantly lower risk than previously estimated. Indications for excision currently revolve around aes...

journal_title：Pediatric dermatology

authors： Mosa A,Ho ES,Heinelt M,Wong K,Neuhaus K

更新日期：2019-11-01 00:00:00

abstract：:Cutaneous histiocytosis may take two principal forms. It is either a benign proliferative process or a relentless, progressive process with a poor prognosis. In histiocytic medullary reticulosis, histiocytes demonstrate nuclear atypia and the outcome is uniformly fatal. Benign cephalic histiocytosis X causes lesions s...

journal_title：Pediatric dermatology

authors： Roper SS,Spraker MK

更新日期：1985-11-01 00:00:00

abstract：:Bullous mastocytosis (diffuse cutaneous mastocytosis) is a rare form of mast cell disease that begins during the first month of life and causes extensive blisters that mimic scalded skin syndrome or bullous erythema multiforme. Discrete pigmented macules, papules, and nodules are absent and the characteristic leathery...

journal_title：Pediatric dermatology

authors： Golitz LE,Weston WL,Lane AT

更新日期：1984-04-01 00:00:00