Eruptive juvenile xanthogranuloma associated with relapsing acute lymphoblastic leukemia.

abstract：:Pustular psoriasis (PP) is rare in children. The small number of reported cases makes deciding on treatment and follow-up challenging. The current study was an evaluation of treatment approaches and courses of PP in 18 children diagnosed and followed over a 20-year period. From 1992 to 2011 we treated 1,447 children w...

journal_title：Pediatric dermatology

authors： Popadic S,Nikolic M

更新日期：2014-09-01 00:00:00

abstract：BACKGROUND/OBJECTIVES:Emollients are part of the standard treatment for atopic dermatitis (AD), although there is limited evidence that regular use of emollients as management therapy reduces the frequency of flares and corticosteroid consumption. The objective of this study was to evaluate the benefit of emollient use...

journal_title：Pediatric dermatology

authors： Tiplica GS,Kaszuba A,Malinauskienė L,Konno P,Boralevi F,Garrigue E,Saint-Aroman M,Delarue A

更新日期：2017-05-01 00:00:00

abstract：:Hemangiomas, common proliferative vascular tumors, can grow rapidly in the first months of life. Although therapy with high-dose oral glucocorticoids is standard for lesions that threaten vital functions or are disfiguring, little is known about the endocrine consequences of this treatment. Using retrospective data, w...

journal_title：Pediatric dermatology

authors： Lomenick JP,Backeljauw PF,Lucky AW

更新日期：2006-03-01 00:00:00

abstract：:Hair loss and thinning are possible complications in those undergoing endocrine therapies with aromatase inhibitors. Alopecia in pediatric patients undergoing endocrine therapy has not been previously reported. We describe two adolescents, 14 and 16 years of age, who developed androgenetic alopecia following treatment...

journal_title：Pediatric dermatology

authors： Perper M,Herskovitz I,Tosti A

更新日期：2020-11-01 00:00:00

abstract：:Trisomy 13, or Patau syndrome, is a chromosomal disorder that can occur in complete, partial, or mosaic forms. Mosaicism is observed in 6% of individuals with trisomy 13 and, in contrast to the complete form, has wide phenotypic variability, longer survival, and in some patients an unusual skin pigmentary pattern simi...

journal_title：Pediatric dermatology

authors： González-del Angel A,Estandia-Ortega B,Gaviño-Vergara A,Sáez-de-Ocariz M,Velasco-Hernández Mde L,Salas-Labadía C

更新日期：2014-09-01 00:00:00

abstract：:A wide spectrum of histopathologic changes has been reported to occur within epidermal nevi. We saw two patients with warty nevoid lesions in which histopathologic features of incontinentia pigmenti, verrucous phase, were present. The diagnosis of incontinentia pigmenti was excluded because both patients were male, la...

journal_title：Pediatric dermatology

authors： Fletcher V,Williams ML,Lane AT

更新日期：1985-11-01 00:00:00

abstract：:Early recognition of the hyperlipoproteinemias is a crucial element in preventing premature coronary artery disease. Xanthomas provide a cutaneous marker of the silent, underlying pathology. Identifying them, and understanding their relation to the inherited hyperlipoproteinemias may facilitate early diagnosis of hype...

journal_title：Pediatric dermatology

authors： Maher-Wiese VL,Marmer EL,Grant-Kels JM

更新日期：1990-09-01 00:00:00

abstract：:We describe a unique and puzzling case of a 7-month-old baby with a non-X hypertriglyceridemic histiocytoxanthomatosis. The disease was characterized by a massive nodular eruption that was clinically, histologically, and ultrastructurally consistent with juvenile xanthogranuloma, but it had a rapid, fatal evolution. ...

journal_title：Pediatric dermatology

authors： Caputo R,Ermacora E,Gelmetti C,Gianni E

更新日期：1987-11-01 00:00:00

abstract：:Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a severe variant of pityriasis lichenoides et varioliformis acuta (PLEVA). We report a case of FUMHD in an 11-year-old boy who subsequently developed neurologic symptoms and was found to have necrotizing vasculitis on brain biopsy. Over 5 years of follow-up, he...

journal_title：Pediatric dermatology

authors： Rosman IS,Liang LC,Patil S,Bayliss SJ,White AJ

更新日期：2013-01-01 00:00:00

abstract：:A 9-year-old girl newly diagnosed with systemic lupus erythematosus (SLE) developed a localized linear papulovesicular eruption over the right dorsal hand and ulnar forearm. The skin findings were clinically suggestive of herpes zoster, lichen striatus, or lichen planus-lupus erythematosus overlap. However, histologic...

journal_title：Pediatric dermatology

authors： Roholt NS,Lapiere JC,Wang JI,Bernstein LJ,Woodley DT,Eramo LR

更新日期：1995-06-01 00:00:00

abstract：:Trichothiodystrophy (TTD) is a hair abnormality that may be associated with a large number of alterations affecting the skin phenotype and skin appendages, nervous system, eyes, bones, and immune, gonadal, and endocrine systems. We report the first case of TTD associated with a urologic malformation and primary hyperc...

journal_title：Pediatric dermatology

authors： Malvehy J,Ferrando J,Soler J,Tuneu A,Ballesta F,Estrach T

更新日期：1997-11-01 00:00:00

abstract：:Henoch-Schönlein purpura (HSP) is the most common vasculitis of childhood. It is usually self-limiting and is characterized by an immune complex-mediated vasculitis associated with IgA deposition. We present an unusual case of HSP with mucosal lesions and coronary artery thickening. ...

journal_title：Pediatric dermatology

authors： Veetil BM,Reed AM,Mattke AC

更新日期：2012-05-01 00:00:00

abstract：:Connective tissue nevi of collagen type are now classified in four major subtypes. In addition to the clinicopathological features of papulolinear collagenoma, which is considered as a variant of isolated collagen harmatoma, the case we present has a unique arborizing pattern. ...

journal_title：Pediatric dermatology

authors： Lo LK,Tsai TF,Chen YF,Hung CM,Ko WC

更新日期：2009-01-01 00:00:00

abstract：:Cutis laxa is a rare disorder resulting from degradation and clumping of elastic fibers in dermis. Type II acquired cutis laxa, shows only cutaneous changes without any systemic involvement. We describe an infant with acquired cutis laxa type II following a generalized inflammatory dermatitis. ...

journal_title：Pediatric dermatology

authors： Haider M,Alfadley A,Kadry R,Almutawa A

更新日期：2010-01-01 00:00:00

abstract：:Bullous dermolysis of the newborn is a dominant or recessive inherited subtype of dystrophic epidermolysis bullosa characterized by the tendency to spontaneously stop blistering within the first months of life. Here we report two siblings with bullous dermolysis of the newborn who were born prematurely and have a nove...

journal_title：Pediatric dermatology

authors： Boccaletti V,Zambruno G,Castiglia D,Magnani C,Tognetti E,Fabrizi G,Cortelazzi C,Pagliarello C,Di Nuzzo S

更新日期：2015-03-01 00:00:00

abstract：:A young boy developed childhood keratosis lichenoides chronica. The eruption cleared spontaneously after 13 years. This is a rare condition, regarded by some as a variant of lichen planus. The great preponderance of cases occur in adults, whereas the disease in childhood is uncommon. ...

journal_title：Pediatric dermatology

authors： Torrelo A,Mediero IG,Zambrano A

更新日期：1994-03-01 00:00:00

abstract：:Palmoplantar eccrine hidradenitis (PEH) is characterized by painful erythematous papules and nodules of abrupt onset on the soles of young individuals. The histologic hallmark is a predominant neutrophilic infiltrate surrounding the eccrine gland apparatus. A total of 28 cases have been published since 1988, with a br...

journal_title：Pediatric dermatology

authors： Landau M,Metzker A,Gat A,Ben-Amitai D,Brenner S

更新日期：1998-03-01 00:00:00

abstract：BACKGROUND/OBJECTIVES:The association between vitiligo and congenital melanocytic nevi remains incompletely understood. The objective of this study was to investigate the frequency of depigmentation, including vitiligo, in patients with a large congenital melanocytic nevus (LCMN), which is a rare melanocytic tumor vari...

journal_title：Pediatric dermatology

authors： Polat Ekinci A,Kiliç S,Baykal C

更新日期：2016-05-01 00:00:00

abstract：:Herpes zoster is rare in otherwise healthy children, but it is more common in association with immunosuppression. Maternal varicella infection during pregnancy and varicella occurring in the newborn represent risk factors for childhood herpes zoster. However, some controversies persist about risk factors, diagnosis, a...

journal_title：Pediatric dermatology

authors： Nikkels AF,Nikkels-Tassoudji N,Piérard GE

更新日期：2004-01-01 00:00:00

abstract：:Familial cold auto-inflammatory syndrome, Muckle-Wells syndrome and chronic infantile neurologic, cutaneous, articular syndrome are related disorders associated with mutations in the CIAS1 gene. They appear to represent a continuum of one disease characterized by IL-1-mediated inflammation. Until recently, these condi...

journal_title：Pediatric dermatology

authors： O'Connell SM,O'Regan GM,Bolger T,Hoffman HM,Cant A,Irvine AD,Watson RM

更新日期：2007-01-01 00:00:00

abstract：:PLACK syndrome (OMIM 616295) is a form of generalized peeling skin syndrome (GPSS; OMIM 270300). It is an autosomal recessive genodermatosis caused by pathogenic mutations in CAST, which encodes calpastatin, an endogenous specific inhibitor of calpain, a calcium-dependent cysteine protease. We present a 5-year-old gir...

journal_title：Pediatric dermatology

authors： Boggs JME,Irvine AD

更新日期：2020-10-03 00:00:00

abstract：:Cerebriform intradermal nevus is a rare form of cutis verticis gyrata. Clinically it manifests as a scalp deformity resembling the surface of the brain, with cerebriform morphologic characteristics. Degeneration into malignant melanoma has been reported. Herein, a cerebriform intradermal nevus of the scalp in a 7-year...

journal_title：Pediatric dermatology

authors： Yazici AC,Ikizoglu G,Baz K,Polat A,Ustunsoy D

更新日期：2007-03-01 00:00:00

abstract：:Congenital nevi both small and large are frequently removed. We attempted to study the removal rate and etiologic aspects of congenital nevi as well as their psychosocial effects through the use of a quality test. A questionnaire sent to a sample population of individuals with congenital nevocytic nevi (n=192) collect...

journal_title：Pediatric dermatology

authors： Berg P,Lindelöf B

更新日期：2002-07-01 00:00:00

abstract：:Erythema nodosum (EN) in association with kerion celsi is a rare condition in children, with only 11 cases having been reported in the English literature. We describe a new case in a 7-year-old boy in whom the disorder had begun 2 months before. He had many inflamed, boggy, suppurative nodules over the left occipitopa...

journal_title：Pediatric dermatology

authors： Zaraa I,Trojjet S,El Guellali N,El Euch D,Chelly I,Mokni M,Zitouna M,Osman AB

更新日期：2012-07-01 00:00:00

abstract：:Amniotic band syndrome is one of the many causes of aplasia cutis congenita. It is usually seen as a constriction band surrounding a limb or as a membrane that adheres to some part of the body. This syndrome can be associated with various malformations. An infant with amniotic adhesions producing aplasia cutis, radial...

journal_title：Pediatric dermatology

authors： Nagore E,Sánchez-Motilla JM,Febrer MI,Cremades B,Aleu M,Aliaga A

更新日期：1999-05-01 00:00:00

abstract：:Onychomycosis is widespread in the adult population, but considered to be rare in children. A number of studies in recent years show a rise in the prevalence of toenail onychomycosis in children. Of these, only a few were population-based. Here, we present a comprehensive cross-sectional population-based survey of toe...

journal_title：Pediatric dermatology

authors： Leibovici V,Evron R,Dunchin M,Westerman M,Ingber A

更新日期：2009-01-01 00:00:00

abstract：:Striated muscle hamartoma is a rare entity which was described only recently. It is a congenital malformation characterized by the presence of striated, mature muscle fibers in the reticular dermis and hypodermis. We describe a striated muscle hamartoma of the perianal region in a female infant associated with an hema...

journal_title：Pediatric dermatology

authors： Scrivener Y,Petiau P,Rodier-Bruant C,Cribier B,Heid E,Grosshans E

更新日期：1998-07-01 00:00:00

abstract：:We describe a bullous-hemorrhagic reaction of the ear lobes in a child with nephrosis after levamisole intake. This drug is used in children as an alternative treatment of corticosteroid-responsive nephrotic syndrome. Histologic evaluation of a lesion revealed necrotizing vasculitis involving mainly the large vessels ...

journal_title：Pediatric dermatology

authors： Menni S,Pistritto G,Gianotti R,Ghio L,Edefonti A

更新日期：1997-11-01 00:00:00

abstract：:In 1980 a syndrome was first described in two adult males, consisting of macrocephaly, pigmented macules on the glans and shaft of the penis, and hamartomatous intestinal polyps. Since then, 10 additional cases have been identified. Herein, we present two new cases and review the cutaneous manifestations as well as ad...

journal_title：Pediatric dermatology

authors： Gretzula JC,Hevia O,Schachner LS,DiLiberti JH,Ruvalcaba RH,Schimschock JR,Weleber RG,Halal F,Lipson MH,Blumberg B

更新日期：1988-02-01 00:00:00

abstract：:We report a case of a young man with perforating folliculitis and cystic fibrosis with complications including chronic obstructive pulmonary disease, insulin dependent diabetes mellitus, and liver cirrhosis. We demonstrate increased TGF-β1 immunohistochemical staining in the perforating folliculitis lesions of our pat...

journal_title：Pediatric dermatology

authors： Tuttle MS,Kwon EJ,Tamburro J,Honda K

更新日期：2010-11-01 00:00:00