Abstract:
:A 7-year-old boy presented with adrenal insufficiency. He subsequently developed venous thrombosis in the limbs and was diagnosed with primary antiphospholipid syndrome (PAPS) based on clinical and laboratory parameters. Both adrenals were normal on imaging. He required thrombolysis and anticoagulation. The progressive course of PAPS was controlled with methylprednisolone. There are few reports of PAPS in pediatric patients, and associated adrenal involvement is rare. The unusual presentation, course and management of the patient and of four other reported children with adrenal insufficiency heralding manifestation of PAPS are discussed.
journal_name
Lupusjournal_title
Lupusauthors
Bhakhri BK,Katewa S,Sharma R,Mahajan Sdoi
10.1177/0961203310397965subject
Has Abstractpub_date
2011-10-01 00:00:00pages
1203-8issue
11eissn
0961-2033issn
1477-0962pii
0961203310397965journal_volume
20pub_type
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