[Landau-Kleffner sydnrome].

Abstract:

:The Landau-Kleffner syndrome consists of the association of paroxysmal EEG abnormalities, more marked during sleep, acquired aphasia usually of receptive type, and epileptic seizures in three quarters of cases. Additional features include behavioral disturbances that may even present with autistic features, cognitive regression of variable degree, and sometimes motor difficulties, indicating the pervasive nature of the disorder. The epileptic activity, as manifested by the EEG, seems responsible for the pervasive dysfunction. Treatment with antiepileptic drugs is often ineffective. ACTH and corticosteroids are currently regarded as the best therapy but surgical treatment by subpial transection is being actively studied.

journal_name

Rev Neurol

journal_title

Revista de neurologia

authors

Aicardi J

subject

Has Abstract

pub_date

1999-08-16 00:00:00

pages

380-5

issue

4

eissn

0210-0010

issn

1576-6578

journal_volume

29

pub_type

杂志文章,评审
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    更新日期:1999-05-16 00:00:00

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    pub_type: 指南,杂志文章

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  • [Learning in deep hypnosis. The potentiation of mental abilities?].

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    更新日期:1997-12-01 00:00:00

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  • [Barrier dysfunction and Guillain-Barre syndrome as exponents of endothelial damage in COVID-19].

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    doi:

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  • [Central hypomyelination, hypogonadotrophic hypogonadism and hypodontia: a new leukodystrophy].

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    doi:

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  • [Clinical, electrophysiological and immunological evaluation of the response to treatment with intravenous immunoglobulins in several immune-mediated neuropathies].

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  • [Neurological assessment of learning disorders].

    abstract:INTRODUCTION:The neurological concept of learning is approached from a cybernetic point of view, taking into account that a child should recognize a fact, learn it semantically and decided whether it is worth storing; the dynamic aspect of memory is the true motor of the ability to learn and all this is modulated by th...

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    pub_type: 杂志文章,评审

    doi:

    authors: Campos-Castelló J

    更新日期:1998-08-01 00:00:00

  • [On the reunion between neurology and psychiatry. An old neuropsychiatrist's reflections].

    abstract::What appears in this article is nothing more than a series of reflections on psychiatry and neurology based on my own experience as an educator, practitioner and scholar of both disciplines. It is not, therefore, a piece of research work in the usual sense of the word. Such has been my commitment to Revista de Neurolo...

    journal_title:Revista de neurologia

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    更新日期:2007-12-16 00:00:00

  • [Moya-moya disease in a child with multiple malformations].

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    journal_title:Revista de neurologia

    pub_type: 杂志文章

    doi:

    authors: Gorrotxategi P,Reguilón MJ,Gaztañaga R,Hernández Abenza J,Albisu Y

    更新日期:1995-03-01 00:00:00

  • [Clinical variability and characteristics of attention deficit hyperactivity disorder in girls].

    abstract:INTRODUCTION:Attention deficit hyperactivity disorder (ADHD) is a neurobiological condition essentially characterised by inattention, hyperactivity and impulsiveness, and has a prevalence of around 5%. Because it is a biological disorder, both boys and girls with ADHD display these same symptoms, but more boys are diag...

    journal_title:Revista de neurologia

    pub_type: 杂志文章

    doi:

    authors: Valdizán JR,Mercado E,Mercado-Undanivia A

    更新日期:2007-03-02 00:00:00

  • [Attention deficit hyperactivity disorder in teenagers: appraisal of the EDAH (a) scale].

    abstract:AIMS:To appraise the attention deficit hyperactivity disorder assessment scale for a teenage population, EDAH (a). SUBJECTS AND METHODS:From an initial sample of 3400 participants, a final sample of 2292 pupils between 12 and 16 years of age were finally selected. Of the total number, 1066 were boys (46.5%) and 1226 w...

    journal_title:Revista de neurologia

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    doi:

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  • [Spanish validation of the Iowa Rating Scale for Personality Change (IRSPC) for the appraisal of changes in personality in patients with acquired brain injury].

    abstract:INTRODUCTION:The Iowa Rating Scale for Personality Change (IRSPC) presents some features (puts an emphasis on the motivational and emotional functions; evaluates the 'cognitive' executive functions in the daily life; estimates the premorbid personality; values the informant reliability) that make it use really interest...

    journal_title:Revista de neurologia

    pub_type: 杂志文章

    doi:

    authors: Guallart-Balet M,Jiménez-Cortés MP,Tuquet-Calvo H,Pelegrín-Valero C,Olivera-Pueyo J,Benabarre-Ciria S,Tirapu-Ustárroz J

    更新日期:2015-01-01 00:00:00

  • [The effects of protein-energy malnutrition on the central nervous system in children].

    abstract:INTRODUCTION:Protein-energy malnutrition continues to affect millions of human beings in developing countries. Children suffer most from the shortage of nutrients because at early ages malnutrition has an important impact on the central nervous system. The changes that malnutrition triggers in the brains of these child...

    journal_title:Revista de neurologia

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    更新日期:2007-03-02 00:00:00

  • [Clinical and biomolecular classification of the frontotemporal dementias. A review of the literature].

    abstract:INTRODUCTION:The term 'frontotemporal lobar dementia' (FTLD) covers a group of neurodegenerative diseases that are very heterogeneous in their clinical expression, genetic component and histopathological features, and this has traditionally made it difficult to study and classify them. Patients usually present a progre...

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    pub_type: 历史文章,杂志文章,评审

    doi:

    authors: Toribio-Díaz ME,Morera-Guitart J

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  • [Upward and downward gaze palsy with a unilateral mesencephalic hemorrhage].

    abstract:INTRODUCTION:Acute vascular lesions limited to the midbrain can yield varied disturbances of eye movements. They are more often infarcts than hemorrhages. CLINICAL CASE:We present the case of a 49 year old, non-hypertensive man who presented with sudden onset of bilateral up and down gaze palsy. CT defined a unilatera...

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    pub_type: 杂志文章

    doi:

    authors: Rodríguez-Gómez J,Colás J,Aragón A,Albo MI,Casado F

    更新日期:2000-02-16 00:00:00

  • [Early attention to learning disabilities].

    abstract:INTRODUCTION:In the early stages of their development, children acquire the skills and knowledge that provide them with the foundations on which they will later add what they learn at school, including skills such as reading, writing and mathematics. The presence of learning difficulties at the infantile stage can affe...

    journal_title:Revista de neurologia

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    更新日期:2006-02-13 00:00:00

  • [Validation of a cognitive complaints questionnaire for young adults: the relation between subjective memory complaints, prefrontal symptoms and perceived stress].

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    doi:

    authors: Lozoya-Delgado P,Ruiz-Sánchez de León JM,Pedrero-Pérez EJ

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  • [Guitarist's cramp: management with sensory re-education].

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    doi:

    authors: Chaná-Cuevas P,Kunstmann-Rioseco C,Rodríguez-Riquelme T

    更新日期:2003-10-01 00:00:00

  • [Biometric analysis of the Spanish studies on neurorehabilitation in cases of stroke indexed in Medline (2008-2017)].

    abstract:TITLE:Analisis bibliometrico de las investigaciones españolas sobre neurorrehabilitacion en el ictus indizadas en Medline (2008-2017). : ...

    journal_title:Revista de neurologia

    pub_type: 信件

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    authors: Torres-Pascual C,Rodriguez-Rodriguez A,Serena-Leal J

    更新日期:2019-06-01 00:00:00

  • [Automatic analysis of interference pattern: principles and applications].

    abstract:INTRODUCTION:The signals obtained during conventional needle examination are usually assessed subjectively by the neurophysiologist. Buchthal's approach allows quantification of several motor unit parameters during mild effort. DEVELOPMENT:The automatic methods of analysis of the EMG interference pattern (IP), in part...

    journal_title:Revista de neurologia

    pub_type: 杂志文章

    doi:

    authors: Fernández JM,Saborido JG,Alvarez FJ

    更新日期:1999-03-16 00:00:00

  • [Dissection of the internal carotid artery with subarachnoid hemorrhage].

    abstract:INTRODUCTION:Dissection of the intracranial arteries is uncommon, forming less than 10% of all cranio-cervical dissections. Apart from the classical clinical findings of extracranial dissections, intracranial dissection may cause subarachnoid haemorrhage (SAH), mainly dissections involving the posterior circulation. C...

    journal_title:Revista de neurologia

    pub_type: 杂志文章

    doi:

    authors: Martín-Bermúdez R,Arenas-Cabrera C,Gil-Néciga E,Jarrín S

    更新日期:1997-06-01 00:00:00

  • [Disability and quality of life of stroke survivors: evaluation nine months after discharge].

    abstract:INTRODUCTION AND AIM:After acute episode, a great number of individuals who survive a stroke have impairments that impede them to carry out with autonomy a set of basic activities of daily life and instrumental activities of daily life. The clinical evaluation health self perception is a useful element on patient's rec...

    journal_title:Revista de neurologia

    pub_type: 杂志文章

    doi:

    authors: Martins T,Ribeiro JP,Garrett C

    更新日期:2006-06-01 00:00:00

  • [Gangliosides prevent reduction in exploratory activity and delayed neuronal death in gerbils subjected to transitory cerebral ischemia].

    abstract:INTRODUCTION:The ganglioside GM1 has been shown to be effective in the treatment of experimental cerebral ischemia. Gangliosides from bovine brain have not been used in the treatment of ischemic cerebral accidents. There is evidence suggesting that they may also be effective. RESULTS:Ten minutes of bilateral occlusion...

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    pub_type: 杂志文章

    doi:

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    更新日期:1998-10-01 00:00:00