Female pseudohermaphroditism with complete masculinisation of the external genitalia in two siblings. A new entity?

Abstract:

:Complete masculinisation of the external genitalia (type V of Prader classification) is reported in two siblings with normal internal female genitalia, normal ovaries and a 46,XX chromosome constitution in different cell lines without any detectable source of exposure to androgen during pregnancy.

journal_name

Eur J Pediatr

authors

Fryns JP,Kleczkowska A,Vandenberghe K,Haspeslagh M,Van den Berghe H

doi

10.1007/BF00445596

subject

Has Abstract

pub_date

1984-06-01 00:00:00

pages

137-8

issue

2

eissn

0340-6199

issn

1432-1076

journal_volume

142

pub_type

杂志文章
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