Abstract:
:Severe cyanosis due to pulmonary arteriovenous fistulas occurs often after a bidirectional superior cavopulmonary anastomosis (Glenn operation) and also in some congenital anomalies in which hepatic venous blood bypasses the lungs in the first passage. Relocation of hepatic flow into the lungs usually causes these fistulas to disappear. Similar pulmonary arteriovenous fistulas are observed in hereditary haemorrhagic telangiectasia, and in liver disease (hepatopulmonary syndrome). There is no convincing identification yet of a responsible hepatic factor that produces these lesions. Candidates for such a factor are reviewed, and the possibility of angiotensin or bradykinin contributing to the fistulas is discussed.
journal_name
Cardiol Youngjournal_title
Cardiology in the youngauthors
Hoffman JIdoi
10.1017/S1047951113000140subject
Has Abstractpub_date
2013-10-01 00:00:00pages
629-41issue
5eissn
1047-9511issn
1467-1107pii
S1047951113000140journal_volume
23pub_type
杂志文章,评审abstract:OBJECTIVE:Protocols for the placement of temporary pacing wires vary among institutions. Our current protocol is to selectively place temporary pacing wires in those patients who develop haemodynamically significant intra-operative arrhythmia. We wished to identify how effective our current protocol is at identifying w...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951114000043
更新日期:2015-03-01 00:00:00
abstract::We present a rare case of incidentally diagnosed Twiddler's syndrome in a child 7 years after implantation of a dual-chamber pacemaker system with epicardial leads. During revision, an insulation defect of the ventricular lead was evident, despite unremarkable prior pacemaker lead testing. The lead was repaired and a ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120001031
更新日期:2020-06-01 00:00:00
abstract:OBJECTIVE:The aim of this study is to report on the short-term and mid-term outcomes of preterm infants who underwent patent ductus arteriosus ligation through anterior mini-thoracotomy. METHODS:Data for 103 preterm infants who underwent patent ductus arteriosus clipping through an anterior mini-thoracotomy at the 2nd...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951121000032
更新日期:2021-01-28 00:00:00
abstract:OBJECTIVE:The aim of the present study was to determine the role of toxic elements and trace elements in the pathogenesis of conotruncal heart defects by measuring their concentrations in the first meconium specimens of the affected newborns. METHODS:Concentrations of lead, cadmium, iron, zinc, and copper were measure...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951116000536
更新日期:2017-03-01 00:00:00
abstract::An otherwise healthy 17-year-old adolescent boy presented with upper respiratory tract symptoms and was diagnosed with coronavirus disease 2019 infection. A haemorrhagic pericardial effusion was found in the transthoracic echocardiography. He was treated with pericardiocentesis, ibuprofen, and hydroxychloroquine. A la...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120004850
更新日期:2021-01-07 00:00:00
abstract::We report here the case of a 27-year-old woman with Noonan syndrome presenting with ventricular fibrillation. After successful defibrillation, echocardiography revealed hypertrophic cardiomyopathy associated with left ventricular outflow tract obstruction. Normal echocardiographic cardiac structure and function were r...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951110001708
更新日期:2011-04-01 00:00:00
abstract::The interest of professional medical societies in research about outcomes, mixed with the recent accessibility to management of data on the internet, has moved many societies to create national databases or registries for their specialty. In societies with procedure-based specialties such as surgery, these databases w...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/S1047951108002916
更新日期:2008-12-01 00:00:00
abstract::We report the case of a 12-day-old newborn affected by coarctation of the aorta and intraventricular defect who underwent coarctectomy and pulmonary artery banding. On post-operative day 7, the patient suffered from pulseless electric activity due to tension pneumothorax. Point-of-care ultrasound was performed during ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951115001213
更新日期:2016-02-01 00:00:00
abstract::Although extrarenal manifestations of haemolytic-uraemic syndrome are not frequent, myocardial dysfunction should be given special consideration because of the importance of proper early haemodynamic management and potential complications. We report the case of a 21-month-old child with haemolytic-uraemic syndrome who...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951115002759
更新日期:2016-06-01 00:00:00
abstract::The common respiratory syncytial virus has been associated with cardiac involvement, usually tachyarrhythmias and occasionally myocarditis. A child is described who probably developed a complete heart block following respiratory syncytial bronchiolitis. Such an association needs to be considered if the heart is struct...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951109990102
更新日期:2010-02-01 00:00:00
abstract:BACKGROUND:Postpericardiotomy syndrome has been considered a disorder induced by viral infection. This conclusion is based on serologic criterions, but these may be unreliable following either cardiopulmonary bypass or transfusion therapy. Previous studies have not verified the proposed etiology either by isolation of ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s1047951100012440
更新日期:2001-01-01 00:00:00
abstract::Adult survivors of aortic interruption is extremely rare. Diagnosis mostly depends on additional imaging with CT and MRI. We present a rare case of acquired complete interruption of the aorta that was found incidentally at the time of coronary angiography. This finding was confirmed by CT scan. ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951114001693
更新日期:2015-03-01 00:00:00
abstract:BACKGROUND:Children with congenital cardiac disease experience challenges in developing healthy patterns of physical activity due to decreased exercise capacity and parental fear and confusion about what is permissible. The purpose of this study was to describe physical activity habits in children 10-14 years of age wi...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951111000540
更新日期:2011-12-01 00:00:00
abstract:UNLABELLED:Aims This is the first autopsy study in the United Kingdom to analyse the demographic and pathological characteristics of atheroma associated with sudden cardiac death in young people. METHODS:An observational retrospective study of referred cases of sudden cardiac death in the young (⩽35 years) associated ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951115001286
更新日期:2016-04-01 00:00:00
abstract::A 9-month-old infant presented with fever, dyspnoea, and a murmur. Echocardiography showed a mitral vegetation with significant regurgitation. Mitral valve plasty was performed on day 6, and was polymerase chain reaction positive for Kingella kingae. The cardiac outcome was favourable. This case illustrates a subtle p...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951110000351
更新日期:2010-08-01 00:00:00
abstract::Conventional ambulatory heart rhythm monitoring is limited in its ability to provide rapid diagnosis of arrhythmias in athletes participating in water or high-intensity sports. This case report is of a 17-year-old female competitive swimmer who underwent loop recorder implantation with Confirm Rx™ ICM 3500 (Abbott, Mi...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120000232
更新日期:2020-03-01 00:00:00
abstract:AIM:Our aim was to review the outcome of ligation of the persistently patent arterial duct in neonates as performed outside a paediatric cardiothoracic centre by an outreach surgical team. METHODS:A retrospective observational study of all ligations of the persistently patent arterial duct performed in Cambridge betwe...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951107000741
更新日期:2007-10-01 00:00:00
abstract:BACKGROUND:SCN5A encodes sodium-channel α-subunit Nav1.5. The mutations of SCN5A can lead to hereditary cardiac arrhythmias such as the long-QT syndrome type 3 and Brugada syndrome. Here we sought to identify novel mutations in a family with arrhythmia. METHODS:Genomic DNA was isolated from blood of the proband, who w...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951117002980
更新日期:2018-05-01 00:00:00
abstract:BACKGROUND:The physiological importance of the lateral tunnel stenosis in the Fontan pathway for children with single ventricle physiology can be difficult to determine. The impact of the stenosis and stent implantation on total cavopulmonary connection resistance has not been characterized, and there are no clear guid...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951114002765
更新日期:2016-01-01 00:00:00
abstract::Tetralogy of Fallot is only rarely associated with aortic valvar disease. We present a child who had uncomplicated repair of tetralogy of Fallot at 16 months of age, and who developed mild aortic stenosis three years later, with mild to moderate aortic incompetence being seen two years subsequent to that event. No aor...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:
更新日期:2003-06-01 00:00:00
abstract::Paediatric heart transplantation has evolved over the last 3 decades. The research group, Pediatric Heart Transplant Study, has been in step with that evolution over the nearly 20 years of its existence by utilising its registry to contribute a wealth of clinical research to the field. The highlights of its studies wi...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/S1047951115000931
更新日期:2015-08-01 00:00:00
abstract:OBJECTIVES:We describe the structure of, and suggest an etiology for, the interatrial communication which can occur through the mouth of the coronary sinus. Based on the study of human embryos, we propose that the defect is best explained by dissolution of the wall of the coronary sinus adjacent to the left atrium, per...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s104795110001297x
更新日期:2002-07-01 00:00:00
abstract::The persistence of so-called spongy myocardium was first reported in humans in the 1960s. Subsequently, a few reports described the condition, utilizing inconsistent facts and terminology. In 1990 the first report appeared using the term "noncompaction", and detailed its clinical implications. Following this report, m...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951108001972
更新日期:2008-06-01 00:00:00
abstract::Children with a secundum atrial septal defect are usually asymptomatic and are referred for elective closure after 3-4 years of age; however, in premature infants with chronic lung disease, bronchopulmonary dysplasia, or pulmonary hypertension, increased pulmonary blood flow secondary to a left-to-right atrial shunt, ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951114002650
更新日期:2016-01-01 00:00:00
abstract:OBJECTIVE:To determine the efficacy of anatomic biventricular repair by a combination of intraatrial and intraventricular re-routing in patients with isomerism of the left atrial appendages. METHODS:Anatomic biventricular repair by means of combined intraratrial and intraventricular re-routing was achieved in 5 of the...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s1047951100012361
更新日期:2001-01-01 00:00:00
abstract::Aneurysm of the sinus of Valsalva is a rare congenital cardiac anomaly. It occurs as an outpouching that progresses like a windsock, and it may rupture producing aortic regurgitation, cardiac tamponade, congestive heart failure, conduction abnormalities, and stroke. We describe a case of rupture of the sinus of Valsal...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951116001621
更新日期:2017-04-01 00:00:00
abstract:BACKGROUND:The association between long QT interval and sudden infant death syndrome has been clearly established. Several studies have been conducted to determine the evolution of the QT interval in childhood from birth, but only in full-term newborns. However, data on the QT interval in pre-term infants are extremely...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951111001958
更新日期:2012-08-01 00:00:00
abstract::In this study, we summarise a case of a myofibroma causing mid-aortic syndrome due to obstruction of the distal thoracic and abdominal aorta leading to severe left ventricular dysfunction. The patient was managed with percutaneous intervention via balloon dilation and stent placement. On follow-up, the patient has nor...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951115001936
更新日期:2016-04-01 00:00:00
abstract:BACKGROUND:Kawasaki disease, which is characterised by systemic vasculitides accompanied by acute fever, is regularly treated by intravenous immunoglobulin to avoid lesion formation in the coronary artery; however, the mechanism of intravenous immunoglobulin therapy is unclear. Hence, we aimed to analyse the global exp...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951117001433
更新日期:2017-11-01 00:00:00
abstract::Milrinone is a drug frequently used for hemodynamic support in children during critical illness. Although the hemodynamic changes induced by milrinone in children may appear similar to those of adults, the physiologic contributors of these changes remain vastly unknown. A systematic review was conducted to identify st...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951119002865
更新日期:2020-01-01 00:00:00