Abstract:
:The persistence of so-called spongy myocardium was first reported in humans in the 1960s. Subsequently, a few reports described the condition, utilizing inconsistent facts and terminology. In 1990 the first report appeared using the term "noncompaction", and detailed its clinical implications. Following this report, more descriptions of patients with noncompaction entered the literature. Prior to the availability of high resolution cross-sectional echocardiography, most cases of noncompacted myocardium escaped detection, as few patients underwent angiography. In this essay, I seek to adjudicate and clarify several confusions and controversies in the current literature including the acquired nature of hypertrabeculation, the fate of the so-called sinusoids, the relationship to coronary arteries, and noncompaction as another congenital malformation. The embryonic timing of cessation and reinitiation of compaction is conjectured as an explanation of the varied configurations of noncompaction as seen as a clinical entity. The clinical outcomes of decreased contractility, arrhythmia, and thromboembolism, have been stressed in the current literature, but more study is needed of the gray area between the normal variant and minimal noncompaction. A plea is made for the standardization of methods and terminology.
journal_name
Cardiol Youngjournal_title
Cardiology in the youngauthors
Lurie PRdoi
10.1017/S1047951108001972subject
Has Abstractpub_date
2008-06-01 00:00:00pages
243-9issue
3eissn
1047-9511issn
1467-1107pii
S1047951108001972journal_volume
18pub_type
杂志文章abstract::We describe the case of an 8-week-old infant with late presentation of severe refractory atypical Kawasaki disease. In addition to developing giant coronary arterial aneurysms and coronary thrombosis, she formed extensive bilateral arterial aneurysms throughout her systemic circulation. ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951116001967
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journal_title:Cardiology in the young
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951107000741
更新日期:2007-10-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951118002391
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951111000084
更新日期:2011-08-01 00:00:00
abstract::Improvements in the care of children with cardiomyopathy, CHDs, and acquired heart disease have led to an increased number of children surviving with advanced heart failure. In addition, the advent of more durable mechanical circulatory support options in children has changed the outcome for many patients who otherwis...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/S1047951116000184
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s1047951100012440
更新日期:2001-01-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951114001176
更新日期:2015-06-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951104006092
更新日期:2004-12-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/S1047951107001175
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951117001081
更新日期:2017-11-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951119001641
更新日期:2019-09-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951107000960
更新日期:2007-10-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951111002113
更新日期:2012-10-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951111000679
更新日期:2012-02-01 00:00:00
abstract::Hypereosinophilic syndrome is defined as persistent eosinophilia in the blood for more than 6 months, without any identifiable cause and with end-organ involvement evidence. Cardiac manifestations of HES include heart failure due to restrictive cardiomyopathy, arrhythmia, intraventricular thrombosis, and coronary arte...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120004862
更新日期:2021-01-25 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951118000872
更新日期:2018-08-01 00:00:00
abstract:BACKGROUND:Fungal endocarditis classically involves dense heterogenous vegetations. However, several patients with fungal infections were noted to have myocardial changes ranging from focal brightening to nodular thickening of chordae or papillary muscles. This study evaluates whether these findings are associated with...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120003674
更新日期:2020-11-13 00:00:00
abstract::Aneurysm of the sinus of Valsalva is a rare congenital cardiac anomaly. It occurs as an outpouching that progresses like a windsock, and it may rupture producing aortic regurgitation, cardiac tamponade, congestive heart failure, conduction abnormalities, and stroke. We describe a case of rupture of the sinus of Valsal...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951116001621
更新日期:2017-04-01 00:00:00
abstract:BACKGROUND:Percutaneous closure of patent ductus arteriosus has become the treatment of choice in many centres. In patients with large ducts and pulmonary hypertension, transcatheter closure has been achieved with success using the Amplatzer Duct Occluder or even the Amplatzer Muscular Ventricular Septal Defect Occlude...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951114000183
更新日期:2015-03-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951114001838
更新日期:2015-08-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 传,历史文章,杂志文章
doi:10.1017/S1047951108002771
更新日期:2008-12-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951105000090
更新日期:2005-02-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951107000819
更新日期:2007-08-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s1047951101000282
更新日期:2001-05-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章,多中心研究
doi:10.1017/S1047951115002474
更新日期:2015-12-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951117000798
更新日期:2017-10-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951110001903
更新日期:2011-08-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120000931
更新日期:2020-06-01 00:00:00