Abstract:
OBJECTIVE:The policy of early repair of patients with tetralogy of Fallot, irrespective of age, as opposed to initial palliation with a shunt, remains controversial. The aim of our study was to analyze the midterm outcome of primary early correction of tetralogy of Fallot. METHODS:Between 1996 and 2005, a total of 61 consecutive patients less than 6 months of age underwent primary correction of tetralogy of Fallot in two institutions. The median age at surgery was 3.3 months, and 27 patients (44%) were younger than 3 months of age, including 12 (20%) newborns. We analyzed the patients in 2 groups: those younger than 3 months of age, and those aged between 3 and 6 months. RESULTS:There was one early (1.6%), and one late death. Actuarial survival was 98.4%, 96.7%, 96.7% at 1, 5, and 10 years respectively, with a median follow up of 4.5 years. There was no difference in survival, bypass time, lengths of ventilation, and hospital stay between the groups. A transjunctional patch was placed significantly more often in the patients younger than 3 months (p = 0.039), with no adverse effect on survival and morbidity during the follow-up. Freedom from reoperation was 98.2%, 92.2%, and 83% at 1, 5, and 10 years respectively, with no difference between the groups. CONCLUSION:Elective primary repair of tetralogy of Fallot in asymptomatic patients is delayed beyond 3 months of age. In symptomatic patients, primary repair of tetralogy of Fallot is performed irrespective of age, weight and preoperative state. This approach is safe, and provides an excellent midterm outcome with acceptable morbidity and rates of reintervention. The long-term benefits of this approach must be established by careful follow-up, with particular emphasis on arrhythmias, right ventricular function, and exercise performance.
journal_name
Cardiol Youngjournal_title
Cardiology in the youngauthors
Kantorova A,Zbieranek K,Sauer H,Lilje C,Haun C,Hraska Vdoi
10.1017/S1047951108001960subject
Has Abstractpub_date
2008-04-01 00:00:00pages
153-7issue
2eissn
1047-9511issn
1467-1107pii
S1047951108001960journal_volume
18pub_type
杂志文章abstract::This study was carried out to analyse seasonal variations in live births with congenital heart disease in the overall population of Malta. Included were all patients diagnosed as having congenital heart disease by echocardiography, cardiac catheterization, surgery or post mortem, by 1 year of age, and who were born be...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
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journal_title:Cardiology in the young
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journal_title:Cardiology in the young
pub_type: 杂志文章
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journal_title:Cardiology in the young
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journal_title:Cardiology in the young
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journal_title:Cardiology in the young
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journal_title:Cardiology in the young
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journal_title:Cardiology in the young
pub_type: 杂志文章
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journal_title:Cardiology in the young
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更新日期:2020-01-01 00:00:00
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pub_type: 杂志文章,多中心研究
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更新日期:2016-02-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:
更新日期:2003-08-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 传,历史文章,杂志文章
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更新日期:2008-12-01 00:00:00