Abstract:
:Kawasaki disease constitutes an acute febrile vasculitis of unknown aetiology. It is considered the most common cause of acquired cardiac failure in children. Although standard treatment comprises intravenous immunoglobulin and aspirin, some children exhibit refractory disease, necessitating the use of alternative therapies such as corticosteroids and anti-tumour necrosis factor-alpha. For these cases, few controlled data are available. This report focuses on an extremely refractory classical Kawasaki disease with coronary artery aneurysms and ongoing inflammation. We discuss the therapeutic approaches and the potential pitfalls undertaken, which led to an unfavourable clinical outcome.
journal_name
Cardiol Youngjournal_title
Cardiology in the youngauthors
Kossiva L,Karanassios E,Papadopoulos G,Karavanaki Kdoi
10.1017/S1047951111001260subject
Has Abstractpub_date
2012-08-01 00:00:00pages
461-5issue
4eissn
1047-9511issn
1467-1107pii
S1047951111001260journal_volume
22pub_type
杂志文章abstract::Myocarditis is an important cause of arrhythmogenic sudden cardiac arrest in the young. A strong index of suspicion is required as not only can arrhythmias be the only clinical manifestation but also because these patients can have normal cardiac biomarkers, electrocardiographic and echocardiographic findings, and inf...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120001523
更新日期:2020-08-01 00:00:00
abstract:INTRODUCTION:Although chylothorax is an uncommon complication following paediatric cardiothoracic surgery, it has significant associated morbidities and increased in-hospital mortality, as well as results in higher costs. A lack of prospective evidence or consensus guidelines for management of chylothorax further hinde...
journal_title:Cardiology in the young
pub_type: 杂志文章,多中心研究
doi:10.1017/S1047951119001525
更新日期:2019-09-01 00:00:00
abstract::We occluded a large arterial duct in a patient with atrial fibrillation, using an Amplatzer duct occluder, with no residual shunt at the end of the procedure. Follow-up revealed recanalization, which was successfully treated with a 4 mm Amplatzer ASD occluder. It is speculated the reopening of the initially occluded d...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951104003142
更新日期:2004-06-01 00:00:00
abstract::The Holt-Oram syndrome was confirmed in an asymptomatic 36-year-old man by a novel TBX5-gene mutation (exon 8 acceptor splicing site, c.663-1G greater than A). Computed tomography showed an atrial septal defect and an anomalous right coronary artery crossing between the aorta and pulmonary arteries. Surgery corrected ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951111000072
更新日期:2011-06-01 00:00:00
abstract::Children with a secundum atrial septal defect are usually asymptomatic and are referred for elective closure after 3-4 years of age; however, in premature infants with chronic lung disease, bronchopulmonary dysplasia, or pulmonary hypertension, increased pulmonary blood flow secondary to a left-to-right atrial shunt, ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951114002650
更新日期:2016-01-01 00:00:00
abstract::May-Thurner syndrome is a rare clinical entity involving venous obstruction of the left lower extremity. The May-Thurner syndrome is a phenomenon commonly described as an acquired stenosis of the left common iliac vein secondary to compression of the left common iliac vein between the right common iliac artery and the...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951114001115
更新日期:2015-04-01 00:00:00
abstract:BACKGROUND:Obesity increases the risk for various cardiovascular problems. Increase in body mass index is often an independent risk factor for the development of elevated blood pressure and clustering of various cardiovascular risk factors. OBJECTIVE:To determine early markers of left ventricular affection in obese pa...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951117001627
更新日期:2018-01-01 00:00:00
abstract:OBJECTIVE:To evaluate delivery management and outcomes in fetuses prenatally diagnosed with CHD. STUDY DESIGN:A retrospective cohort study was conducted on 6194 fetuses (born between 2013 and 2016), comparing prenatally diagnosed with CHD (170) to those with non-cardiac (234) and no anomalies (5790). Primary outcomes ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120000785
更新日期:2020-05-01 00:00:00
abstract:OBJECTIVE:To examine the current subjective state of health, and the longitudinal course of psychological well-being, in adult patients with congenital cardiac malformations. METHODS:Our study concerns the second follow-up of a cohort of patients with congenital cardiac malformations. We examined 362 consecutive patie...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951105000351
更新日期:2005-04-01 00:00:00
abstract::We assessed the thickness of the normal left ventricular wall according to gender by performing two-dimensional echocardiography in children. While a few studies have evaluated left ventricular wall thicknesses in children using two-dimensional echocardiography, there is little information related to the influence of ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s1047951102000070
更新日期:2002-01-01 00:00:00
abstract::Improvement in operative survival of patients with hypoplastic left heart syndrome has led to increasing emphasis on prevention of interstage mortality. Many centres have improved interstage results through programmes of home monitoring following discharge after the Norwood (Stage 1) operation. Experience with heighte...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/S1047951111001600
更新日期:2011-12-01 00:00:00
abstract:BACKGROUND:Risk for neurodevelopmental delay in infants and children with CHD is well established, but longer-term outcomes are equivocal. A meta-analysis was conducted to establish whether cognitive deficits remain beyond childhood - into teenage and young adult years. Methods and results A total of 18 unique samples,...
journal_title:Cardiology in the young
pub_type: 杂志文章,meta分析
doi:10.1017/S104795111700230X
更新日期:2018-03-01 00:00:00
abstract::Torsades de Pointes is an extremely rare arrhythmia in children associated to LQT syndrome. Pheochromocytomas are also extremely rare tumours in the paediatric age. We present a case of a young patient with an acquired long QT syndrome complicating with Torsades de Pointes as first clinical manifestation of a pheochro...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S104795111400033X
更新日期:2015-02-01 00:00:00
abstract::The literature has scant documentation of the relationship between the important founders of paediatric cardiology, Maude Abbott and Helen Taussig. Recently discovered entries in the diaries kept by Maude Abbott provide evidence for a close connection between them. Further evidence suggests that their association was ...
journal_title:Cardiology in the young
pub_type: 传,历史文章,杂志文章
doi:10.1017/S1047951108002771
更新日期:2008-12-01 00:00:00
abstract::D is an 8-year-old boy brought to his paediatrician for evaluation. His mother is concerned as his teacher has been frequently complaining that he is very restless and often disturbs the rest of the class by getting up on some pretext or the other. He is unable to concentrate on his work and gets distracted very easil...
journal_title:Cardiology in the young
pub_type: 信件
doi:10.1017/S1047951115001274
更新日期:2016-01-01 00:00:00
abstract:OBJECTIVE:The aim of this study was to investigate the relations between the P-wave dispersion and diastolic functions in type 1 diabetic children. PATIENTS:A total of 33 diabetic patients without any cardiovascular disease, with a mean age of 12.3 plus or minus 4.2 years, and 29 healthy controls, with a mean age of 1...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S104795110999031X
更新日期:2010-04-01 00:00:00
abstract::A two-year-old boy with a background history of Down syndrome and partial atrioventricular septal defect presented with acute respiratory distress requiring intubation and mechanical ventilation. He continued to deteriorate, despite ventilation; direct laryngoscopy, bronchoscopy, and computed tomography demonstrated s...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951114000468
更新日期:2015-03-01 00:00:00
abstract::We present a case of a 31-year-old male with a large atrial septal defect, who was found to have interrupted inferior caval vein with azygous continuation to the superior caval vein, which precluded transcutaneous closure by device. The defect was successfully closed with a 33 mm Occlutech Figula septal occluder using...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S104795112000092X
更新日期:2020-06-01 00:00:00
abstract:BACKGROUND:Neonates and infants with congenital and acquired cardiac disease often require placement of central venous lines for extended intravenous therapy. It may be advantageous to avoid the larger venous vessels of the head and neck and lower extremities in order to preserve these for future interventions and ther...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951110000090
更新日期:2010-06-01 00:00:00
abstract::A hyperinflammatory response to COVID-19 is being described in children. While this presents, and responds to management, similar to that of Kawasaki Disease it is being coined a new entity. But is it really? We explore how this phenomenon may be Kawasaki Disease with a new trigger. ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120001432
更新日期:2020-07-01 00:00:00
abstract::Atrioventricular valve regurgitation is widely known as a risk factor for Fontan completion in patients with univentricular physiology. To date, indications and timing for atrioventricular valve repair remain unclear and different surgical techniques have been advocated. Since 2013, 50 consecutive patients underwent e...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951114002352
更新日期:2015-10-01 00:00:00
abstract:OBJECTIVE:To describe endovascular stent placement using partially covered stents to preserve flow in head and neck vessels. BACKGROUND:Endovascular stent placement has become established as a first-line therapy for native coarctation of the aorta or re-coarctation in older children and adults. Increasingly covered st...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951112000236
更新日期:2012-10-01 00:00:00
abstract::Common arterial trunk with arch obstruction is a rare conotruncal abnormality. We report, with confirmatory images, a neonate with this anomaly and additional supracardiac partial anomalous pulmonary venous connection, as well as phenylketonuria. ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951115000128
更新日期:2015-06-01 00:00:00
abstract:BACKGROUND:In patients with tricuspid atresia palliated by construction of a total cavopulmonary connection, both pulmonary and systemic circulations depend on the performance of the dominant left ventricle. When estimating the volume of such ventricles using cross-sectional echocardiography, it is necessary to make as...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s1047951100006521
更新日期:2000-03-01 00:00:00
abstract:OBJECTIVE:Increasing rates of survival have raised the question of medical and psychosocial factors contributing to quality of life of patients with congenital cardiac disease. We investigated the impact of the severity of disease, and social disadvantage, on the quality of life of patients and their primary caregivers...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951105002118
更新日期:2006-02-01 00:00:00
abstract::Tracheobronchial compression of cardiovascular origin is an uncommon and frequently unrecognised cause of respiratory distress in children. The compression may be due to encircling vessels or dilated neighbouring cardiovascular structures. Bronchoscopy and detailed radiography, especially computed tomography and magne...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951112000765
更新日期:2013-04-01 00:00:00
abstract::Dysfunction of the autonomic nervous system, or dysautonomia, is an uncommon disease. Postural orthostatic tachycardia syndrome is one of the several types of dysautonomia. Postural orthostatic tachycardia syndrome, also known as chronic orthostatic intolerance, is the most common but least severe of the dysautonomic ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951110001198
更新日期:2010-12-01 00:00:00
abstract::Supravalvular aortic stenosis is associated with the Williams-Beuren syndrome, but it also occurs in a non-syndromatic congenital form. An elastin gene mutation of chromosome 7q11.23 is responsible in both cases. The vascular features are identical. These patients have a higher risk of sudden death, particularly when ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951110001563
更新日期:2011-02-01 00:00:00
abstract:BACKGROUND:Children with congenital cardiac disease experience challenges in developing healthy patterns of physical activity due to decreased exercise capacity and parental fear and confusion about what is permissible. The purpose of this study was to describe physical activity habits in children 10-14 years of age wi...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951111000540
更新日期:2011-12-01 00:00:00
abstract::IntroductionDiagnostic and interventional catheter angiography of the heart is frequently used in paediatric cardiology. It is also possible to detect urinary system anomalies with cineurography images that may be obtained during angiocardiography. In this study, the aim was to determine the frequency, distribution, a...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951118001828
更新日期:2019-02-01 00:00:00