A girl with extremely refractory Kawasaki disease: an instructive case with unusual course and outcome.

Abstract:

:Kawasaki disease constitutes an acute febrile vasculitis of unknown aetiology. It is considered the most common cause of acquired cardiac failure in children. Although standard treatment comprises intravenous immunoglobulin and aspirin, some children exhibit refractory disease, necessitating the use of alternative therapies such as corticosteroids and anti-tumour necrosis factor-alpha. For these cases, few controlled data are available. This report focuses on an extremely refractory classical Kawasaki disease with coronary artery aneurysms and ongoing inflammation. We discuss the therapeutic approaches and the potential pitfalls undertaken, which led to an unfavourable clinical outcome.

journal_name

Cardiol Young

journal_title

Cardiology in the young

authors

Kossiva L,Karanassios E,Papadopoulos G,Karavanaki K

doi

10.1017/S1047951111001260

subject

Has Abstract

pub_date

2012-08-01 00:00:00

pages

461-5

issue

4

eissn

1047-9511

issn

1467-1107

pii

S1047951111001260

journal_volume

22

pub_type

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