Abstract:
OBJECTIVE:To evaluate the family psycho-social outcomes of children with Down syndrome and atrioventricular septal defect, and examine the impact of these variables on the child's neurodevelopmental outcome. METHODS:This was a cross-sectional study that consisted of 57 children with Down syndrome - 20 cases and 37 controls - of ~12-14 months of age. In both groups, we assessed the development of the child, the quality of the child's home environment, and parenting stress. RESULTS:Compared with the Down syndrome without CHD group, the atrioventricular septal defect group revealed lower scores in all developmental domains, less optimal home environments, and higher parental stress. Significant differences in development were seen in the areas of cognition (p=0.04), expressive language (p=0.05), and gross motor (p<0.01). The Home Observation for Measurement of the Environment revealed significant differences in emotional and verbal responsiveness of the mother between the two groups. The Parenting Stress Index revealed that the Down syndrome with atrioventricular septal defect group had a significantly higher child demandingness subdomain scores compared with the Down syndrome without CHD group. CONCLUSIONS:The diagnosis of a CHD in addition to the diagnosis of Down syndrome may provide additional stress to the child and parents, elevating parental concern and disrupting family dynamics, resulting in further neurodevelopmental deficits. Finding that parental stress and home environment may play a role in the neurodevelopmental outcomes may prompt new family-directed interventions and anticipatory guidance for the families of children with Down syndrome who have a CHD.
journal_name
Cardiol Youngjournal_title
Cardiology in the youngauthors
Visootsak J,Huddleston L,Buterbaugh A,Perkins A,Sherman S,Hunter Jdoi
10.1017/S1047951115000062subject
Has Abstractpub_date
2016-02-01 00:00:00pages
250-6issue
2eissn
1047-9511issn
1467-1107pii
S1047951115000062journal_volume
26pub_type
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journal_title:Cardiology in the young
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journal_title:Cardiology in the young
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journal_title:Cardiology in the young
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journal_title:Cardiology in the young
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更新日期:2000-01-01 00:00:00
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pub_type: 杂志文章,多中心研究
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更新日期:2021-01-11 00:00:00
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pub_type: 杂志文章,评审
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