Abstract:
:Hearing loss in mucopolysaccharidosis is usually both conductive and sensorineural. The conductive component is attributable to serous otitis media secondary to dysfunction of the eustachian tube and chronic thickening of the mucosa of the middle ear. The conductive component may persist after myringotomy and insertion of short-term or long-term ventilation tubes. In Hurler's syndrome, death usually occurs in the first decade of life. In our study, we present two cases, a three-year-old girl and a four-year-old boy, who were diagnosed with Hurler's syndrome. Both children have a history of otitis media with effusion requiring repeated short-term ventilation tube insertions that were unsuccessful. Permanent t-tubes were inserted in both cases. Results showed an approximate 20 dB improvement in hearing sensitivity postoperatively for each patient.
journal_name
Int J Audioljournal_title
International journal of audiologyauthors
Oghan F,Harputluoglu U,Guclu E,Guvey A,Turan N,Ozturk Odoi
10.1080/14992020600975287subject
Has Abstractpub_date
2007-02-01 00:00:00pages
94-6issue
2eissn
1499-2027issn
1708-8186pii
773174509journal_volume
46pub_type
杂志文章abstract::Confirmation of the conditions of the ossicles is essential for tympanoplasty. However, at present, ossicular mobility is experimentally estimated with palpation by a surgeon, and the results depend on the surgeon's skill. In this study, a new apparatus for quantitatively measuring ossicular mobility was developed. Wi...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020500377899
更新日期:2006-02-01 00:00:00
abstract::We evaluated the benefits of fast-acting WDRC, slow-acting AVC, and linear reference fittings for speech intelligibility and reported disability, in a within-subject within-device masked crossover design on 50 listeners with SNHL. Five hearing aid fittings were implemented having two compression channels and seven fre...
journal_title:International journal of audiology
pub_type: 杂志文章,随机对照试验
doi:10.1080/14992020500429518
更新日期:2006-03-01 00:00:00
abstract:OBJECTIVE:Evaluation of the Sennheiser HD 202 II supra-aural headphones as an alternative headphone to enable more affordable hearing screening. DESIGN:Study 1 measured the equivalent threshold sound pressure levels (ETSPL) of the Sennheiser HD 202 II. Study 2 evaluated the attenuation of the headphones. Study 3 deter...
journal_title:International journal of audiology
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doi:10.1080/14992027.2016.1214756
更新日期:2016-11-01 00:00:00
abstract::The aim of the study is to understand the implications of disclosing the results of connexin26 (Cx26) gene testing to the concerned family with hearing impaired individuals. The department of biotechnology is funding a multicentric multidisciplinary team from Jawaharlal Nehru Center for Advanced Scientific Research (B...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020701297805
更新日期:2007-07-01 00:00:00
abstract::Objective: To investigate the relationship between hearing loss (HL) and general quality of life (QoL) in adults seeking hearing aids (HAs). Design: The patients completed the European Organisation for Research and Treatment of Cancer (EORTC) Quality of Life Questionnaire's general part and a questionnaire measuring s...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992027.2019.1627010
更新日期:2019-11-01 00:00:00
abstract::A research program was undertaken to evaluate the efficacy of an audiovisual-FM system as a speechreading aid. The present study investigated the effects of the distance between the talker and the speechreader on a visual-speech perception task. Sentences were recorded simultaneously with a conventional Hi8 mm video c...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020500485718
更新日期:2006-05-01 00:00:00
abstract::Objective: To clarify the distinction between Auditory Processing Disorder (APD) and Attention Deficit Disorder (ADD) using the CHC Model.Design: A cross-sectional study compared responses of caregivers about their children's behaviour to identify characteristics of APD (CHC Model) and ADD (DSM-5).Study Sample: Caregi...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992027.2019.1682199
更新日期:2020-03-01 00:00:00
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journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020802301662
更新日期:2008-11-01 00:00:00
abstract::The objective of this study was to compare the electrically evoked compound action potentials, intra- versus post-operatively, in cochlear implant patients. In a prospective study twenty-five consecutively implanted adult patients received a multichannel cochlear implant. In all patients, electrically evoked compound ...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020600833189
更新日期:2006-10-01 00:00:00
abstract:OBJECTIVE:To estimate the prevalence of severe dual sensory loss (DSL) among older persons (aged ≥65 years) in the Swedish population, to identify the diagnoses that cause severe DSL, and to identify rehabilitation services in which the participants have been involved. DESIGN:A cross-sectional design was applied. Medi...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992027.2020.1783003
更新日期:2020-12-01 00:00:00
abstract:STUDY OBJECTIVE:This study evaluated how closely the DSL v5.0 a prescription could be approximated with hearing aids, its relationship to preferred listening levels (PLLs) of adults with acquired hearing loss, and the self-reported outcomes of the resulting fittings. PARTICIPANTS:Thirty adults with varying degrees and...
journal_title:International journal of audiology
pub_type: 杂志文章,多中心研究
doi:10.3109/14992021003713122
更新日期:2010-08-01 00:00:00
abstract:OBJECTIVE:To evaluate the prevalence of labyrinthine ossification, and especially cochlear ossification, in a cohort of patients with unilateral sudden deafness or severe sensorineural hearing loss. DESIGN:Retrospective data collection. STUDY SAMPLE:Sixty-four consecutive patients with unilateral sudden deafness or s...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2013.786191
更新日期:2013-07-01 00:00:00
abstract::The effect of inverting electrode location and stimulus perceptibility on the presence of the mismatch negativity (MMN) evoked response was investigated in 20 normal-hearing adult females. Perceptible and imperceptible frequency contrasts were employed in an oddball paradigm. The perceptible contrast consisted of an 1...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020802283241
更新日期:2008-11-01 00:00:00
abstract:OBJECTIVE:The purpose of this study is to assess the individual effect of reverberation and noise, as well as their combined effect, on speech intelligibility by cochlear implant (CI) users. DESIGN:Sentence stimuli corrupted by reverberation, noise, and reverberation + noise are presented to 11 CI listeners for word i...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2012.658972
更新日期:2012-06-01 00:00:00
abstract::In this study, we present a new method to derive a single-number measure of the directivity of hearing aids. The method is an extension of the conventional directivity index (DI), and is called overall directivity index (ODI). The directivities of five different hearing aid styles were compared with that of the open e...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992020209101312
更新日期:2002-01-01 00:00:00
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journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2014.891057
更新日期:2014-07-01 00:00:00
abstract::In order to develop a sensitive audiometric protocol for identifying ototoxicity in children, a retrospective study of 16 children treated with cisplatin and/or carboplatin was performed. Audiometric testing was done by means of pure-tone threshold audiometry (PTA), high-frequency audiometry (HFA), and distortion prod...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020600582117
更新日期:2006-06-01 00:00:00
abstract::Children with listening difficulties, but normal audiometry, may be diagnosed with APD. The diagnosis is typically based on poor performance on tests of perception of both non-speech and speech stimuli. However, non-speech test results correlate only weakly with evaluations of speech-in-noise processing, cognitive ski...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2012.723143
更新日期:2013-01-01 00:00:00
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journal_title:International journal of audiology
pub_type: 杂志文章
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更新日期:2005-12-01 00:00:00
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journal_title:International journal of audiology
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更新日期:2012-10-01 00:00:00
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journal_title:International journal of audiology
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doi:10.1080/14992027.2017.1339129
更新日期:2017-11-01 00:00:00
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更新日期:2020-11-18 00:00:00
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journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2011.585667
更新日期:2011-10-01 00:00:00
abstract::One limitation with the Bone Anchored Hearing Aid (Baha) is too poor amplification for patients with moderate to severe sensorineural hearing losses. Therefore, we investigated if bone conducted (BC) sound transmission improves when the stimulation approaches the cochlea. Also the influence from the squamosal suture o...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020802311216
更新日期:2008-12-01 00:00:00
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journal_title:International journal of audiology
pub_type: 杂志文章
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更新日期:2016-01-01 00:00:00
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journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2015.1030510
更新日期:2015-01-01 00:00:00
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journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020701459868
更新日期:2007-11-01 00:00:00
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journal_title:International journal of audiology
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journal_title:International journal of audiology
pub_type: 杂志文章
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更新日期:2007-01-01 00:00:00
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journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992027.2019.1592250
更新日期:2019-07-01 00:00:00