Accelerated phase of Chédiak-Higashi syndrome diffuse white-matter-enhancing lesions.

Abstract:

:We present the CT and MRI findings of a patient with Chédiak-Higashi syndrome in the accelerated phase with marked white-matter abnormalities. Pathologic and clinical features allow diagnosis of this condition, which in this case had dramatic neuroradiographic manifestations not well described in previous reports.

journal_name

Pediatr Radiol

journal_title

Pediatric radiology

authors

Herman TE,Lee BC

doi

10.1007/s002470050637

keywords:

subject

Has Abstract

pub_date

1999-07-01 00:00:00

pages

527-9

issue

7

eissn

0301-0449

issn

1432-1998

pii

90290527.247

journal_volume

29

pub_type

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