Development of practice and consensus-based strategies including a treat-to-target approach for the management of moderate and severe juvenile dermatomyositis in Germany and Austria.

abstract：BACKGROUND:Recently preliminary ultrasonography (US) definitions, in B mode, for normal components of pediatric joints have been developed by the OMERACT US group. The aim of the current study was to include Doppler findings in the evaluation and definition of normal joint features that can be visualized in healthy chi...

journal_title：Pediatric rheumatology online journal

authors： Collado P,Windschall D,Vojinovic J,Magni-Manzoni S,Balint P,Bruyn GAW,Hernandez-Diaz C,Nieto JC,Ravagnani V,Tzaribachev N,Iagnocco A,D'Agostino MA,Naredo E,OMERACT ultrasound subtask force on pediatric.

更新日期：2018-04-10 00:00:00

abstract：BACKGROUND:The prediction of resistance to intravenous immunoglobulins (IVIG) is currently still one of the main research areas in Kawasaki disease (KD). Several studies have reported on the use of N-terminal pro-brain natriuretic peptide (NT-ProBNP) to this end. However, considering the age-dependency of NT-ProBNP lev...

journal_title：Pediatric rheumatology online journal

authors： Shao S,Luo C,Zhou K,Hua Y,Wu M,Liu L,Liu X,Wang C

更新日期：2019-09-18 00:00:00

abstract：BACKGROUND:Although Henoch-Schonlein purpura (HSP) is the most common form of systemic vasculitis in children, the long term effect of HSP on endothelial function is still not clear. The aim of our study was to evaluate the long term effect of HSP on endothelial function in children and adolescents. METHODS:This resea...

journal_title：Pediatric rheumatology online journal

authors： Butbul Aviel Y,Dafna L,Pilar G,Brik R

更新日期：2017-01-14 00:00:00

abstract：BACKGROUND:Transition guidelines and recommendations for developing countries are limited and best transition practices in young patients with chronic medical conditions have been poorly examined. This study evaluates transition practices from pediatric to adult rheumatology care in Brazil. METHODS:Practicing pediatri...

journal_title：Pediatric rheumatology online journal

authors： Anelli CG,Amorim ALM,Osaku FM,Terreri MT,Len CA,Reiff A

更新日期：2017-05-30 00:00:00

abstract：BACKGROUND:To characterize suicidality among youth with juvenile fibromyalgia syndrome (JFMS) receiving treatment from pediatric rheumatologists at a tertiary care center in order to determine the prevalence of suicidality in JFMS and to explore risk factors for persistent suicidal ideation. METHODS:We performed a cro...

journal_title：Pediatric rheumatology online journal

authors： Gmuca S,Sonagra M,Xiao R,Miller KS,Thomas NH,Young JF,Weiss PF,Sherry DD,Gerber JS

更新日期：2021-01-06 00:00:00

abstract：BACKGROUND:Diagnosis of Periodic Fever, Aphthous stomatitis, Pharyngitis and Cervical Adenitis (PFAPA) syndrome is currently based on the modified Marshall's criteria, but no validated evidence based classification criteria for PFAPA has been established so far. METHODS:A multistep process, based on the Delphi and Nom...

journal_title：Pediatric rheumatology online journal

authors： Vanoni F,Caorsi R,Aeby S,Cochard M,Antón J,Berg S,Brik R,Dolezalova P,Koné-Paut I,Neven B,Ozen S,Pillet P,Stojanov S,Wouters C,Gattorno M,Hofer M

更新日期：2018-09-21 00:00:00

abstract：:On March 11th, 2020 the World Health Organization declared COVID-19 a global pandemic. The infection, transmitted by 2019 novel coronavirus (2019-nCov), was first discovered in December 2019, in Wuhan, Hubei Province, and then rapidly spread worldwide. Italy was early and severely involved, with a critical spread of t...

journal_title：Pediatric rheumatology online journal

authors： Licciardi F,Giani T,Baldini L,Favalli EG,Caporali R,Cimaz R

更新日期：2020-04-22 00:00:00

abstract：:Familial Mediterranean fever (FMF) is the most common monogenic autoinflammatory disease in Canada and is characterized by a clinical syndrome of episodic inflammatory symptoms. Traditionally, the disease is defined by autosomal recessive inheritance of MEFV gene variants, yet FMF also not uncommonly manifests in indi...

journal_title：Pediatric rheumatology online journal

authors： Westwell-Roper C,Niemietz I,Tucker LB,Brown KL

更新日期：2019-05-14 00:00:00

abstract：BACKGROUND:Kawasaki Disease (KD), the leading cause of acquired heart disease in children in the developed world, is extremely rare in neonates. We present a case of incomplete KD in a neonate and a review of the literature on neonatal KD. CASE PRESENTATION:A previously healthy full term 15 day old Caucasian male with...

journal_title：Pediatric rheumatology online journal

authors： Altammar F,Lang B

更新日期：2018-07-03 00:00:00

abstract：BACKGROUND:Children are commonly referred to a pediatric rheumatology center for the laboratory finding of an Anti-nuclear antibody (ANA) of undetermined significance. Previous studies regarding adult rheumatology patients have supported an association between ANA and anti-thyroid antibodies, with the prevalence of thy...

journal_title：Pediatric rheumatology online journal

authors： Torok KS,Arkachaisri T

更新日期：2010-05-05 00:00:00

abstract：: Xanthomatous skin lesions and arthritis in children are not a common association. We present the case of a 3 year old girl who presented with xanthomatous lesions in the periungual region of both hands, around the nares and on her forehead, associated with significant arthritis that was clinically compatible with mul...

journal_title：Pediatric rheumatology online journal

authors： Matiz C,Ferguson PJ,Zaenglein A,Groh B,Bingham CA

更新日期：2009-10-08 00:00:00

abstract：: Bullous systemic lupus erythematosus is a rare blistering condition with a distinctive combination of clinical, histological and immunopathologic features that together constitute a unique bullous disease phenotype. It is often associated with autoimmunity to type VII collagen. Here we report a child who presented wi...

journal_title：Pediatric rheumatology online journal

authors： Kumar S,Agarwal I

更新日期：2007-11-21 00:00:00

abstract：BACKGROUND:To investigate the prevalence of cumulative organ damage among Egyptian children with juvenile-onset systemic lupus erythematosus (jSLE) and the relationships between the organ damage and the demographic data, clinical variables, and disease activity. METHODS:A total of 148 patients with jSLE have been foll...

journal_title：Pediatric rheumatology online journal

authors： Salah S,Lotfy HM,Mokbel AN,Kaddah AM,Fahmy N

更新日期：2011-12-09 00:00:00

abstract：BACKGROUND:Due to an increased frequency of vasculitis in FMF patients, many investigators have studied MEFV mutations in patients with HSP. The aim of the study is to investigate the frequency and clinical significance of MEFV mutations in Egyptian children with Henoch-Schonlein purpura (HSP). Investigating MEFV mutat...

journal_title：Pediatric rheumatology online journal

authors： Salah S,Rizk S,Lotfy HM,El Houchi S,Marzouk H,Farag Y

更新日期：2014-09-09 00:00:00

abstract：BACKGROUND:Juvenile idiopathic arthritis (JIA) is the most common pediatric rheumatic disease and a leading cause of childhood disability. The objective of this study was to characterize the PK, safety, and taste acceptability of tofacitinib in patients with JIA. METHODS:This Phase 1, open-label, multiple-dose (twice ...

journal_title：Pediatric rheumatology online journal

authors： Ruperto N,Brunner HI,Zuber Z,Tzaribachev N,Kingsbury DJ,Foeldvari I,Horneff G,Smolewska E,Vehe RK,Hazra A,Wang R,Mebus CA,Alvey C,Lamba M,Krishnaswami S,Stock TC,Wang M,Suehiro R,Martini A,Lovell DJ,Pediatric Rheu

更新日期：2017-12-28 00:00:00

abstract：BACKGROUND:No standard treatment protocol exists for Kawasaki disease (KD) after spontaneous defervescence that does not use intravenous immunoglobulin (IVIG). Moreover, some cases present an indolent course and later develop coronary artery lesions (CALs). We aimed herein to assess the short-term prognosis of KD after...

journal_title：Pediatric rheumatology online journal

authors： Takahashi T,Sakakibara H,Morikawa Y,Miura M

更新日期：2015-11-04 00:00:00

abstract：BACKGROUND:The pathologic diagnosis of isolated myocarditis without pericardial involvement is uncommonly encountered in systemic onset Juvenile Idiopathic Arthritis (soJIA). CASE:An eleven year-old boy with soJIA died suddenly while being treated with the interleukin 1 (IL-1) receptor inhibitor, anakinra. His autopsy...

journal_title：Pediatric rheumatology online journal

authors： Zeft AS,Menon SC,Miller D

更新日期：2012-04-10 00:00:00

abstract：: There is a debate whether post-streptococcal reactive arthritis (PSRA) is a separate entity or a condition on the spectrum of acute rheumatic fever (ARF). We believe that PSRA is a distinct entity and in this paper we review the substantial differences between PSRA and ARF. We show how the demographic, clinical, gene...

journal_title：Pediatric rheumatology online journal

authors： Uziel Y,Perl L,Barash J,Hashkes PJ

更新日期：2011-10-20 00:00:00

abstract：BACKGROUND:Bisphosphonates are recommended for use as first-line therapy for the prevention and treatment of glucocorticoid-induced osteoporosis in adults. However, the appropriate usage of bisphosphonates for the prevention or treatment of glucocorticoid-induced osteoporosis in children remains unclear. METHODS:We pe...

journal_title：Pediatric rheumatology online journal

authors： Inoue Y,Mitsunaga K,Yamamoto T,Chiba K,Yamaide F,Nakano T,Morita Y,Yamaide A,Suzuki S,Arima T,Yamaguchi KI,Tomiita M,Shimojo N,Kohno Y

更新日期：2018-06-18 00:00:00

abstract：BACKGROUND:There are few studies on radiographic outcome after long-term disease duration in juvenile idiopathic arthritis (JIA). We wanted to evaluate 29-year radiographic outcome in hands/wrists and predictors of damage in patients with long-term active JIA. METHODS:Patients diagnosed from 1980 to 1985, who had acti...

journal_title：Pediatric rheumatology online journal

authors： Selvaag AM,Kirkhus E,Törnqvist L,Lilleby V,Aulie HA,Flatø B

更新日期：2017-04-11 00:00:00

abstract：:Following publication of the original article [1], we have been notified that the colour representation of the graph is not correct in Figure 6 legend. ...

journal_title：Pediatric rheumatology online journal

authors： Lee WF,Wu CY,Yang HY,Lee WI,Chen LC,Ou LS,Huang JL

更新日期：2020-02-18 00:00:00

abstract：BACKGROUND:Patient recruitment can be very challenging in paediatric studies, especially in relatively uncommon conditions, such as juvenile idiopathic arthritis (JIA). However, involving children and young people (CYP) in the design of such trials could promise a more rapid trajectory towards making evidence-based tre...

journal_title：Pediatric rheumatology online journal

authors： Sherratt FC,Roper L,Stones SR,McErlane F,Peak M,Beresford MW,Foster H,Ramanan AV,Rooney M,Baildam E,Young B

更新日期：2018-12-04 00:00:00

abstract：: Autoimmunity is often observed among individuals with primary immune deficiencies; however, the frequency and role of autoimmunity in Schimke immuno-osseous dysplasia (SIOD) has not been fully assessed. SIOD, which is caused by mutations of SMARCAL1, is a rare autosomal recessive disease with its prominent features b...

journal_title：Pediatric rheumatology online journal

authors： Zieg J,Krepelova A,Baradaran-Heravi A,Levtchenko E,Guillén-Navarro E,Balascakova M,Sukova M,Seeman T,Dusek J,Simankova N,Rosik T,Skalova S,Lebl J,Boerkoel CF

更新日期：2011-09-13 00:00:00

abstract：BACKGROUND:Muckle-Wells-syndrome (MWS) is an autoinflammatory disease characterized by systemic and organ-specific inflammation due to excessive interleukin (IL)-1 release. Inner ear inflammation results in irreversible sensorineural hearing loss, if untreated. Early recognition and therapy may prevent deafness. The ai...

journal_title：Pediatric rheumatology online journal

authors： Kuemmerle-Deschner JB,Koitschev A,Tyrrell PN,Plontke SK,Deschner N,Hansmann S,Ummenhofer K,Lohse P,Koitschev C,Benseler SM

更新日期：2015-11-04 00:00:00

abstract：PURPOSE:To present the case of a 14-year-old boy with clinical and radiographic features of pseudorheumatoid chondrodyspalsia with additional, potentially serious, cervical malformations. METHODS:Detailed clinical and radiological examinations were undertaken with emphasis on the usefulness of 3D-CT scanning. RESULTS...

journal_title：Pediatric rheumatology online journal

authors： Al Kaissi A,Ben Chehida F,Ben Ghachem M,Grill F,Klaushofer K

更新日期：2007-09-27 00:00:00

abstract：OBJECTIVE:To follow up the refractory juvenile dermatomyositis (JDM) with autologous hematopoietic stem cell transplantation (AHSCT) in a long time and to investigate whether AHSCT is effective and safe to treat refractory JDM. METHODS:We collected the AHSCT and follow-up data of three patients with refractory JDM who...

journal_title：Pediatric rheumatology online journal

authors： Zhu J,Su G,Lai J,Dong B,Kang M,Li S,Zhou Z,Wu F

更新日期：2018-11-20 00:00:00

abstract：BACKGROUND:Because pediatric antineutrophil cytoplasmic antibody-associated vasculitis is rare, management generally relies on adult data. We assessed treatment practices, uptake of existing clinical assessment tools, and interest in pediatric treatment protocols among rheumatologists caring for children with granuloma...

journal_title：Pediatric rheumatology online journal

authors： Westwell-Roper C,Lubieniecka JM,Brown KL,Morishita KA,Mammen C,Wagner-Weiner L,Yen E,Li SC,O'Neil KM,Lapidus SK,Brogan P,Cimaz R,Cabral DA,for ARChiVe Investigators Network within the PedVas initiative.

更新日期：2017-08-07 00:00:00

abstract：OBJECTIVES:To examine the prescribing habits of NSAIDs among pediatric medical and surgical practitioners, and to examine concerns and barriers to their use. METHODS:A sample of 1289 pediatricians, pediatric rheumatologists, sports medicine physicians, pediatric surgeons and pediatric orthopedic surgeons in the United...

journal_title：Pediatric rheumatology online journal

authors： Levy DM,Imundo LF

更新日期：2010-02-04 00:00:00

abstract：:In the following a brief commentary is given on a new European project that aims to provide the European countries with recommendations for the care of children and yound adults with rheumatic diseases. These recommendations will be based on surveys sent to PRINTO members and systematic literature reviews. Surveys on ...

journal_title：Pediatric rheumatology online journal

authors： Wulffraat NM,Vastert B,SHARE consortium.

更新日期：2013-02-15 00:00:00

abstract：BACKGROUND:Temporomandibular joint (TMJ) arthritis and involvement is commonly seen in Juvenile Idiopathic Arthritis (JIA). Therapy includes conservative measures, but also includes intraarticular corticosteroid injections (IASI) and systemic immunosuppressive therapy. Despite aggressive medical therapy, some patients ...

journal_title：Pediatric rheumatology online journal

authors： Lypka M,Shah K,Jones J

更新日期：2020-09-04 00:00:00