Establishing percentile charts for hip joint capsule and synovial cavity thickness in apparently healthy children.

abstract：BACKGROUND:CANDLE syndrome (an acronym for Chronic Atypical Neutrophilic Dermatosis with Lipodystrophy and Elevated Temperature) is a recently described rare autosomal recessive disorder charaterized by systemic autoinflammation. Clinical manifestations include presentation in the first year of life, episodes of fever ...

journal_title：Pediatric rheumatology online journal

authors： Boyadzhiev M,Marinov L,Boyadzhiev V,Iotova V,Aksentijevich I,Hambleton S

更新日期：2019-05-02 00:00:00

abstract：BACKGROUND:Juvenile Idiopathic Arthritis (JIA) may cause significant impairment in health-related quality of life (HrQoL), despite effective therapies. The aim of this study was to assess HrQoL during first-year treatment in patients with new-onset polyarticular JIA, and to compare treatment strategies. METHODS:In ACU...

journal_title：Pediatric rheumatology online journal

authors： Tarkiainen M,Tynjälä P,Vähäsalo P,Kröger L,Aalto K,Lahdenne P

更新日期：2019-12-16 00:00:00

abstract：BACKGROUND:Patient recruitment can be very challenging in paediatric studies, especially in relatively uncommon conditions, such as juvenile idiopathic arthritis (JIA). However, involving children and young people (CYP) in the design of such trials could promise a more rapid trajectory towards making evidence-based tre...

journal_title：Pediatric rheumatology online journal

authors： Sherratt FC,Roper L,Stones SR,McErlane F,Peak M,Beresford MW,Foster H,Ramanan AV,Rooney M,Baildam E,Young B

更新日期：2018-12-04 00:00:00

abstract：BACKGROUND:Juvenile idiopathic arthritis (JIA) is an autoimmune disease characterized by persistent chronic arthritis. Disease risk is believed to be influenced by both genetic and environmental factors. It is well established that the PTPN22 single nucleotide polymorphism (SNP) rs2476601 is associated with JIA suscept...

journal_title：Pediatric rheumatology online journal

authors： Goulielmos GN,Chiaroni-Clarke RC,Dimopoulou DG,Zervou MI,Trachana M,Pratsidou-Gertsi P,Garyfallos A,Ellis JA

更新日期：2016-04-23 00:00:00

abstract：: Although musculoskeletal ultrasound (MSUS) has emerged as an indispensible tool among physicians involved in musculoskeletal medicine in the last two decades, only recently has it become more attractive to pediatric rheumatologists. Thereafter, the use of MSUS in pediatric rheumatology has started to increase. Yet, a...

journal_title：Pediatric rheumatology online journal

authors： Tok F,Demirkaya E,Ozçakar L

更新日期：2011-09-12 00:00:00

abstract：BACKGROUND:Withholding live-attenuated vaccines in patients using interleukin (IL)-1 or IL-6 blocking agents is recommended by guidelines for both pediatric and adult rheumatic diseases, since there is a risk of infection in an immune suppressed host. However, this has never been studied. This retrospective, multicente...

journal_title：Pediatric rheumatology online journal

authors： Jeyaratnam J,Ter Haar NM,Lachmann HJ,Kasapcopur O,Ombrello AK,Rigante D,Dedeoglu F,Baris EH,Vastert SJ,Wulffraat NM,Frenkel J

更新日期：2018-03-21 00:00:00

abstract：BACKGROUND:The United States pediatric rheumatology workforce is committed to a mission of providing children access to pediatric rheumatology care. With a limited number and distribution of pediatric rheumatologists, telemedicine has been proposed as one way to meet this mission, yet the adoption of this modality has ...

journal_title：Pediatric rheumatology online journal

authors： Bullock DR,Vehe RK,Zhang L,Correll CK

更新日期：2017-07-11 00:00:00

abstract：BACKGROUND:The pathologic diagnosis of isolated myocarditis without pericardial involvement is uncommonly encountered in systemic onset Juvenile Idiopathic Arthritis (soJIA). CASE:An eleven year-old boy with soJIA died suddenly while being treated with the interleukin 1 (IL-1) receptor inhibitor, anakinra. His autopsy...

journal_title：Pediatric rheumatology online journal

authors： Zeft AS,Menon SC,Miller D

更新日期：2012-04-10 00:00:00

abstract：BACKGROUND:Fibrodysplasia ossificans progressiva (FOP) is the most catastrophic form of heterotopic ossification, due to ongoing intracellular signaling through the bone morphogenic protein pathway. The paroxysmal appearance of inflammatory lumps and elevated inflammatory markers during flares, suggest that FOP is an a...

journal_title：Pediatric rheumatology online journal

authors： Haviv R,Moshe V,De Benedetti F,Prencipe G,Rabinowicz N,Uziel Y

更新日期：2019-12-21 00:00:00

abstract：BACKGROUND:There are few studies on radiographic outcome after long-term disease duration in juvenile idiopathic arthritis (JIA). We wanted to evaluate 29-year radiographic outcome in hands/wrists and predictors of damage in patients with long-term active JIA. METHODS:Patients diagnosed from 1980 to 1985, who had acti...

journal_title：Pediatric rheumatology online journal

authors： Selvaag AM,Kirkhus E,Törnqvist L,Lilleby V,Aulie HA,Flatø B

更新日期：2017-04-11 00:00:00

abstract：BACKGROUND:Depression and anxiety adversely affects outcomes in systemic lupus erythematosus (SLE) and healthcare utilization is high for pediatric SLE. We aimed to characterize the prevalence of depression and anxiety in pediatric SLE, and their association with healthcare utilization. METHODS:We conducted a cross-se...

journal_title：Pediatric rheumatology online journal

authors： Knight A,Weiss P,Morales K,Gerdes M,Gutstein A,Vickery M,Keren R

更新日期：2014-09-10 00:00:00

abstract：:Familial Mediterranean fever (FMF) is the most common monogenic autoinflammatory disease in Canada and is characterized by a clinical syndrome of episodic inflammatory symptoms. Traditionally, the disease is defined by autosomal recessive inheritance of MEFV gene variants, yet FMF also not uncommonly manifests in indi...

journal_title：Pediatric rheumatology online journal

authors： Westwell-Roper C,Niemietz I,Tucker LB,Brown KL

更新日期：2019-05-14 00:00:00

abstract：BACKGROUND:No standard treatment protocol exists for Kawasaki disease (KD) after spontaneous defervescence that does not use intravenous immunoglobulin (IVIG). Moreover, some cases present an indolent course and later develop coronary artery lesions (CALs). We aimed herein to assess the short-term prognosis of KD after...

journal_title：Pediatric rheumatology online journal

authors： Takahashi T,Sakakibara H,Morikawa Y,Miura M

更新日期：2015-11-04 00:00:00

abstract：BACKGROUND:Hemophagocytic lymphohistiocytosis (HLH) and macrophage activation syndrome (MAS) were historically thought to be distinct entities, often managed in isolation. In fact, these conditions are closely related. A collaborative approach, which incorporates expertise from subspecialties that previously treated HL...

journal_title：Pediatric rheumatology online journal

authors： Halyabar O,Chang MH,Schoettler ML,Schwartz MA,Baris EH,Benson LA,Biggs CM,Gorman M,Lehmann L,Lo MS,Nigrovic PA,Platt CD,Priebe GP,Rowe J,Sundel RP,Surana NK,Weinacht KG,Mann A,Yuen JC,Meleedy-Rey P,Starmer A,Ban

更新日期：2019-02-14 00:00:00

abstract：BACKGROUND:Currently there is no consensus agreement on the degree of enhancement in normal temporomandibular joints (TMJ) in children, which makes it difficult for clinicians to distinguish between the presence/absence of mild synovitis. Quantitative measurements of synovial and condylar enhancement may be useful addi...

journal_title：Pediatric rheumatology online journal

authors： Ma GM,Amirabadi A,Inarejos E,Tolend M,Stimec J,Moineddin R,Spiegel L,Doria AS

更新日期：2015-12-01 00:00:00

abstract：BACKGROUND:To assess the predictors for intravenous immunoglobulin (IVIG) resistance and coronary artery lesions (CALs) in Kawasaki disease (KD). METHODS:A total of 560 KD patients were reviewed retrospectively, including 410 complete KD (cKD) and 150 incomplete KD (iKD) patients. The laboratory data were compared bet...

journal_title：Pediatric rheumatology online journal

authors： Xie T,Wang Y,Fu S,Wang W,Xie C,Zhang Y,Gong F

更新日期：2017-03-21 00:00:00

abstract：: Autoimmunity is often observed among individuals with primary immune deficiencies; however, the frequency and role of autoimmunity in Schimke immuno-osseous dysplasia (SIOD) has not been fully assessed. SIOD, which is caused by mutations of SMARCAL1, is a rare autosomal recessive disease with its prominent features b...

journal_title：Pediatric rheumatology online journal

authors： Zieg J,Krepelova A,Baradaran-Heravi A,Levtchenko E,Guillén-Navarro E,Balascakova M,Sukova M,Seeman T,Dusek J,Simankova N,Rosik T,Skalova S,Lebl J,Boerkoel CF

更新日期：2011-09-13 00:00:00

abstract：BACKGROUND:Anti-TNF (Tumor necrosis factor) therapy is effective in treating pediatric patients with refractory rheumatic disease. There is however a concern that anti-TNF usage may increase the risk of malignancy. Reports on specific types of malignancy in this patient population have been emerging over the past decad...

journal_title：Pediatric rheumatology online journal

authors： Okihiro A,Hasija R,Fung L,Cameron B,Feldman BM,Laxer R,Schneider R,Silverman E,Spiegel L,Yeung RSM,Tse SML

更新日期：2018-03-14 00:00:00

abstract：BACKGROUND:Henoch-Schonlein Purpura (HSP) is one of the most common vasculitides of childhood, with 10-20 cases per 100,000 children. It frequently occurs following an infectious trigger and involves IgA and C3 deposition in small vessel walls. HSP is characterized by palpable purpura plus IgA deposition on biopsy, art...

journal_title：Pediatric rheumatology online journal

authors： Bloom JL,Darst JR,Prok L,Soep JB

更新日期：2018-09-04 00:00:00

abstract：BACKGROUND:To develop and test the feasibility and initial effectiveness of the Treatment and Education Approach for Childhood-onset Lupus (TEACH) protocol, a 6-session cognitive behavioral therapy (CBT) intervention for adolescents and young adults (AYA) with childhood-onset systemic lupus erythematosus (cSLE). METHO...

journal_title：Pediatric rheumatology online journal

authors： Cunningham NR,Fussner LM,Moorman E,Avar Aydin PO,Brunner HI,Kashikar-Zuck S

更新日期：2019-02-18 00:00:00

abstract：BACKGROUND:Kawasaki Disease (KD), the leading cause of acquired heart disease in children in the developed world, is extremely rare in neonates. We present a case of incomplete KD in a neonate and a review of the literature on neonatal KD. CASE PRESENTATION:A previously healthy full term 15 day old Caucasian male with...

journal_title：Pediatric rheumatology online journal

authors： Altammar F,Lang B

更新日期：2018-07-03 00:00:00

abstract：:In 2018, an international Task Force formulated recommendations for treating Juvenile Idiopathic Arthritis (JIA) to target. The Task Force has not yet resolved three issues. The first issue is the lack of a single "best" target. The Task Force decided not to recommend the use of a specific instrument to assess inactiv...

journal_title：Pediatric rheumatology online journal

authors： Schoemaker CG,Swart JF,Wulffraat NM

更新日期：2020-04-16 00:00:00

abstract：BACKGROUND:The prediction of resistance to intravenous immunoglobulins (IVIG) is currently still one of the main research areas in Kawasaki disease (KD). Several studies have reported on the use of N-terminal pro-brain natriuretic peptide (NT-ProBNP) to this end. However, considering the age-dependency of NT-ProBNP lev...

journal_title：Pediatric rheumatology online journal

authors： Shao S,Luo C,Zhou K,Hua Y,Wu M,Liu L,Liu X,Wang C

更新日期：2019-09-18 00:00:00

abstract：BACKGROUND:Muckle-Wells-syndrome (MWS) is an autoinflammatory disease characterized by systemic and organ-specific inflammation due to excessive interleukin (IL)-1 release. Inner ear inflammation results in irreversible sensorineural hearing loss, if untreated. Early recognition and therapy may prevent deafness. The ai...

journal_title：Pediatric rheumatology online journal

authors： Kuemmerle-Deschner JB,Koitschev A,Tyrrell PN,Plontke SK,Deschner N,Hansmann S,Ummenhofer K,Lohse P,Koitschev C,Benseler SM

更新日期：2015-11-04 00:00:00

abstract：:Juvenile idiopathic arthritis (JIA) is the most common rheumatic disease of childhood, with JIA-associated uveitis its most common extra-articular manifestation. JIA-associated uveitis is a potentially sight-threatening condition and thus carries a considerable risk of morbidity. The aetiology of the condition is auto...

journal_title：Pediatric rheumatology online journal

authors： Clarke SL,Sen ES,Ramanan AV

更新日期：2016-04-27 00:00:00

abstract：BACKGROUND/PURPOSE:To assess EDI-OCT (enhanced depth imaging optical coherence tomography) of choroid for inflammatory signs in children with polyarteritis nodosa (PAN) and adenosine deaminase-2 deficiency (DADA-2). METHODS:In this cross-sectional study conducted between June 2017 and September 2018, we evaluated chil...

journal_title：Pediatric rheumatology online journal

authors： Baytaroğlu A,Kadayifçilar S,Ağin A,Deliktaş Ö,Demir S,Bilginer Y,Karakaya J,Özen S,Eldem B

更新日期：2020-04-03 00:00:00

abstract：BACKGROUND:An increased concentration of plasma homocysteine (Hcy) has toxic effects on vascular endothelium. This seems to be a risk factor of cardiovascular disease, premature stroke and venous thrombosis. The risk is higher in coincidence with other factors like chronic diseases and familiar hypercholesterolemia. Th...

journal_title：Pediatric rheumatology online journal

authors： Gonçalves M,D'Almeida V,Guerra-Shinohara EM,Galdieri LC,Len CA,Hilário MO

更新日期：2007-04-02 00:00:00

abstract：: Takayasu arteritis (TA) is a rare chronic inflammatory disease of the aorta and its major branches. It is seen predominantly in females during the second and third decades of life, although it can occur in childhood. The aetiology of TA remains unknown. To date, familial cases of TA have been considered rare; however...

journal_title：Pediatric rheumatology online journal

authors： Morishita KA,Rosendahl K,Brogan PA

更新日期：2011-02-02 00:00:00

abstract：UNLABELLED: BACKGROUND:As patients with juvenile idiopathic arthritis (JIA) progress into adulthood, long-term outcome is determined by disease activity, physical and psychosocial development. Decreased aerobic capacity may play a critical role in health-related outcomes in JIA, since it has been linked with cardiovas...

journal_title：Pediatric rheumatology online journal

authors： van Pelt PA,Takken T,van Brussel M,de Witte M,Kruize AA,Wulffraat NM

更新日期：2012-08-20 00:00:00

abstract：:In the following a brief commentary is given on a new European project that aims to provide the European countries with recommendations for the care of children and yound adults with rheumatic diseases. These recommendations will be based on surveys sent to PRINTO members and systematic literature reviews. Surveys on ...

journal_title：Pediatric rheumatology online journal

authors： Wulffraat NM,Vastert B,SHARE consortium.

更新日期：2013-02-15 00:00:00