Erythropoietic protoporphyria and terminal hepatic failure.

Abstract:

:We report on a 44-year-old patient with erythropoietic protoporphyria who could effectively control his photosensitivity for 22 years with oral carotinoids. The clinical course of his disorder was complicated by liver involvement, initially expressed as marginally raised serum transaminase levels for several years. Terminal hepatic failure with fatal outcome developed 22 years after manifestation of his liver function abnormalities. Hepatic involvement represents an inconstant and unpredictable feature of erythropoietic protoporphyria, determining the prognosis of an otherwise clinically benign disorder.

journal_name

Acta Derm Venereol

authors

Bruch-Gerharz D,Bolsen K,Gerharz CD,Goerz G

doi

10.2340/0001555576453456

subject

Has Abstract

pub_date

1996-11-01 00:00:00

pages

453-6

issue

6

eissn

0001-5555

issn

1651-2057

journal_volume

76

pub_type

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