Epilepsy with myoclonic absences.

Abstract:

:The cases are described of eight children, five of them girls, who had epilepsy with myoclonic absences. The mean age of onset was 4.9 years. Brief episodes of loss of awareness with bilateral clonic jerking of the upper limbs were associated with rhythmic 3 cycles/second spike-wave discharges on electroencephalogram. Generalised tonic-clonic or astatic seizures, or both, also occurred in seven patients. All now have learning difficulties, and seven have behavioural problems. Conventional treatment for absences was effective in only two children. Of six patients treated with lamotrigine, five have improved substantially, but only one is in sustained complete remission. One recently diagnosed patient continues to have frequent myoclonic absences. As the response to treatment and long term outcome are much poorer, it is important to differentiate myoclonic absences from typical childhood absence epilepsy.

journal_name

Arch Dis Child

authors

Manonmani V,Wallace SJ

doi

10.1136/adc.70.4.288

subject

Has Abstract

pub_date

1994-04-01 00:00:00

pages

288-90

issue

4

eissn

0003-9888

issn

1468-2044

journal_volume

70

pub_type

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