[Syndromic diversities in Creutzfeldt-Jakob disease: neurophysiological and histopathological correlates].

Abstract:

:Two syndromatic forms of Creutzfeldt-Jakob disease are illustrated with data from two cases confirmed by necropsy and studied by means of electroencephalogram, evoked potential recording and neuropathological techniques. One of the cases presented the typical hypersynchronous periodic discharges through to be characteristic of this disease. The other did not exhibit epileptiform discharges, showing an evolution in which progressive diffuse slowing was the prominent feature. Cortical spongyosis, gliosis, and neuronal lose were intense in the case showing spikes, and moderate in the one without spikes. Subcortical involvement was similar in both cases. This different topography of pathological involvement might explain, in addition to electroencephalographic findings, the different behavior of somatosensory evoked potentials, which were of larger amplitude in the case showing epileptiform discharges, although in both cases deterioration of clinical state was accompanied by a progressive amplitude decrement in the evoked potential. Sleep induced by barbiturates was disrupted in the case with spikes, its pattern being closer to normal in the case with less severe cortical involvement. A Wada test demonstrated that discharges in the hemispheres were independent. Spike periodicity is discussed. It is postulated that the heavier involvement of cortical layers II to IV deprive the remaining pyramidal cells of inhibitory influences, a condition which might explain the generation of periodic spike discharges.

journal_name

Arq Neuropsiquiatr

authors

Ferrer S,Cartier L,Lolas F,Perez M

doi

10.1590/s0004-282x1982000100005

subject

Has Abstract

pub_date

1982-03-01 00:00:00

pages

39-53

issue

1

eissn

0004-282X

issn

1678-4227

journal_volume

40

pub_type

杂志文章
  • Correlation between parameters of electrophysiological, histomorphometric and sciatic functional index evaluations after rat sciatic nerve repair.

    abstract::The rat sciatic nerve is a well-established model for the study of recovery from peripheral nerve injuries. Traditional methods of assessing nerve regeneration after nerve injury and repair, such as electrophysiology and histomorphometry, despite widely used in neural regeneration experiments, do not necessarily corre...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x2006000500010

    authors: Martins RS,Siqueira MG,da Silva CF,Plese JP

    更新日期:2006-09-01 00:00:00

  • Chronic inflammatory demyelinating polyradiculoneuropathy: two cases with cervical spinal cord compression.

    abstract::Chronic inflammatory demyelinating polyradiculoneuropathy (CIDP) is a peripheral nerve disorder probably due to an immunological disturb. It evolves either in a steadily progressive or in a relapsing and fluctuating course. Weakness is mainly in the lower limbs proximally and distally. The electromyography is demyelin...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x2005000400021

    authors: Freitas MR,Nascimento OJ,Soares CN,Brito AR,Domingues RC

    更新日期:2005-09-01 00:00:00

  • Association between cognitive function and parameters of echocardiography and coronary artery angiography.

    abstract::We aimed to determine whether there is an association between cognition and the results of echocardiography and angiography, based on neuropsychological assessments. METHODS:We assessed the cognition of 85 patients who had recently undergone coronary artery angiography. We calculated the Gensini score for the coronar...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/0004-282x20180026

    authors: Hashemi M,Jervekani ZT,Mortazavi S,Maracy MR,Barekatain M

    更新日期:2018-04-01 00:00:00

  • [Meningiomas in pediatric patients: report of 2 cases].

    abstract::Meningiomas correspond to 1% - 4% of primary intracranial tumors in pediatric group, with their incidence raising according to age. There is not gender prevalence, in spite of some authors describe a male tendency opposed to female one in adulthood. At present study we describe two cases of pediatric meningiomas revie...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:

    authors: Hanel RA,Tatsui CE,Araujo JC,Grande CV,Antoniuk A,Gasparetto EL,Torres LF

    更新日期:2001-09-01 00:00:00

  • Differences in walking attainment ages between low-risk preterm and healthy full-term infants.

    abstract:OBJECTIVE:To compare gross motor development of preterm infants (PT) without cerebral palsy with healthy full-term (FT) infants, according to Alberta Infant Motor Scale (AIMS); to compare the age of walking between PT and FT; and whether the age of walking in PT is affected by neonatal variables. METHODS:Prospective s...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x2012000800007

    authors: Restiffe AP,Gherpelli JL

    更新日期:2012-08-01 00:00:00

  • Assessment of functional capacity in elderly residents of an outlying area in the hinterland of Bahia/Northeast Brazil.

    abstract:OBJECTIVE:To assess the functional capacity and to determine the difference between the means of functional capacity (basic and instrumental activities of daily living) and the age groups of elderly residents in an outlying area in the hinterland of Bahia/Northeast of Brazil. METHOD:Analytical study with cross-section...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x2010000100009

    authors: Torres Gde V,Reis LA,Reis LA

    更新日期:2010-02-01 00:00:00

  • [Hallervorden Spatz syndrome: magnetic resonance findings. Case report].

    abstract::Hallervorden-Spatz syndrome is a neurodegenerative disease, autosomic recessive with two clinical features: early and late onset. Psychiatric, pyramidal and extrapyramidal signs are present in the late subtype. We report the case of a 41-old woman with extrapyramidal signs. Magnetic resonance imaging (MRI) showed the ...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x2004000400031

    authors: Farage L,Castro MA,Macedo TA,Assis MC,Souza LP,Freitas LO

    更新日期:2004-09-01 00:00:00

  • [A cerebrospinal fluid syndrome in neurocysticercosis].

    abstract::The study is based on 371 cerebrospinal fluid (CSF) samples and 324 serum samples from 40 patients with neurocysticercosis (NC) submitted to treatment with praziquantel. The aim of the study is a critical evaluation on humoral immunity in CSF NC syndrome. The analysis of NC patients at diagnosis and in the follow-up p...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章,评审

    doi:10.1590/s0004-282x1987000300006

    authors: Livramento JA

    更新日期:1987-09-01 00:00:00

  • Margaret Dix, Charles Hallpike and the 'Lagerungs' Manoeuvre.

    abstract::The main objective of this manuscript is to describe some personal and professional aspects of two outstanding researchers and pioneers in neuro-otology. Among other achievements, Margaret Ruth Dix, and Charles Skinner Hallpike, designed the most-used provocative test for positional nystagmus for the diagnosis of lith...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 传,历史文章,杂志文章

    doi:10.1590/0004-282X20180075

    authors: Maranhão-Filho P,Nandi R,Maranhão ET

    更新日期:2018-08-01 00:00:00

  • Familial Creutzfeldt-Jakob disease associated with a point mutation at codon 210 of the prion protein gene.

    abstract::Creutzfeldt-Jakob disease (CJD), the most known human prion disease, is usually sporadic but approximately 15% of the cases are familial. To date, seven CJD cases with codon 210 mutation (GTT to ATT) have been reported in the literature. We describe a case of a 57 year-old woman who presented gait disturbances and rap...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x2001000600017

    authors: Huang N,Marie SK,Kok F,Nitrini R

    更新日期:2001-12-01 00:00:00

  • The role of sleep in migraine attacks.

    abstract::Migraine attacks may be precipitated by sleep deprivation or excessive sleep and sleep is also associated with relief of migraine attacks. In view of this variable relationship we studied the records of 159 consecutive outpatients of our Headache Unit. In 121 records there was reference to sleep involvement, in 55% by...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x1993000400001

    authors: Inamorato E,Minatti-Hannuch SN,Zukerman E

    更新日期:1993-12-01 00:00:00

  • Headache among medical and psychology students.

    abstract:UNLABELLED:Headaches occur frequently and thus are a key component of sociocentric medical education. OBJECTIVE:To study headaches among students of medicine and psychology in a single university. METHOD:This was a questionnaire-based survey of a cohort of students of medicine and psychology. RESULTS:The overall lif...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x2011000400018

    authors: Ferri-de-Barros JE,Alencar MJ,Berchielli LF,Castelhano Junior LC

    更新日期:2011-06-01 00:00:00

  • [Comparison of the neuropsychological assessment in a girl with bilateral cerebrovascular disease (moyamoya) before and after surgical intervention].

    abstract::Moyamoya is a chronic progressive cerebrovascular disease with characteristic angiographic findings and a clinical picture with episodes of transient ischemic attacks, headache, seizures, hemiparesis, which may resolve after surgical treatment. We describe the case of a girl with the typical findings of the disease, c...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x1999000600024

    authors: Ciasca SM,Alves HL,Guimarães IE,Terra AP,Moura-Ribeiro MV,Camargo EE,Etchebehere ES,Santos Ade O

    更新日期:1999-12-01 00:00:00

  • Is there a consistent association between coronary heart disease and ischemic stroke caused by intracranial atherosclerosis?

    abstract::Coronary heart disease and ischemic stroke are frequent coexistent conditions that share risk factors and pose major burdens to global health. Even though a clear relation has been established between extracranial internal carotid artery atherosclerosis and symptomatic or asymptomatic coronary heart disease, there is ...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章,评审

    doi:10.1590/0004-282x20130028

    authors: Conforto AB,Leite Cda C,Nomura CH,Bor-Seng-Shu E,Santos RD

    更新日期:2013-05-01 00:00:00

  • Frontopolar and anterior temporal cortex activation in a moral judgment task: preliminary functional MRI results in normal subjects.

    abstract:OBJECTIVE:To study the brain areas which are activated when normal subjects make moral judgments. METHOD:Ten normal adults underwent BOLD functional magnetic resonance imaging (fMRI) during the auditory presentation of sentences that they were instructed to silently judge as either "right" or "wrong". Half of the sent...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x2001000500001

    authors: Moll J,Eslinger PJ,Oliveira-Souza R

    更新日期:2001-09-01 00:00:00

  • [EEG alpha band coherence analysis in healthy adults: preliminary results].

    abstract::We studied the occipital inter-hemispheric coherence of Electroencephalogram (electrodes O1-O2) for alpha band (alpha1--8.0 to 10.0 Hz and alpha2--10.1 to 12.5 Hz) in two groups of healthy individuals (young adults and subjects older than 50 years-old), to assess if there is significant difference between this two age...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x2005000100015

    authors: Anghinah R,Caramelli P,Takahashi DY,Nitrini R,Sameshima K

    更新日期:2005-03-01 00:00:00

  • [Charcot-Marie-Tooth disease. Electromyographic studies in 45 patients].

    abstract::The electrophysiological studies of 45 patients with Charcot-Marie-Tooth disease (CMT) are presented. The nerve conduction of the motor median and ulnar nerves permitted us to separate our patients in two types: type I (demyelinating) with motor nerve conduction (MNC) below 38 m/s (11 cases) and type II with MNC norma...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 临床试验,杂志文章

    doi:10.1590/s0004-282x1995000400002

    authors: Freitas MR,Nascimento OJ,Nevares MT,Escada TM

    更新日期:1995-09-01 00:00:00

  • Sleep habits in native Brazilian Terena children in the state of Mato Grosso do Sul, Brazil.

    abstract::Sleep habits in childhood vary in function of physiological factors. Cultural traits also influence sleep habits. This research evaluates sleep habits of Native Brazilian Terena children. The Terena group here studied live in the central region of Mato Grosso do Sul, Brazil, on the plains; they are peaceful and dedica...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x1998000500001

    authors: Reimão R,De Souza JC,Medeiros MM,Almirão RI

    更新日期:1998-12-01 00:00:00

  • Air pollution and risk of hospitalization for epilepsy: the role of farm use of nitrogen fertilizers and emissions of the agricultural air pollutant, nitrous oxide.

    abstract::The link between various air pollutants and hospitalization for epilepsy has come under scrutiny. We have proposed that exposure to air pollution and specifically the pervasive agricultural air pollutant and greenhouse gas, nitrous oxide (N2O), may provoke susceptibility to neurodevelopmental disorders. Evidence suppo...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/0004-282X20170107

    authors: Fluegge K,Fluegge K

    更新日期:2017-09-01 00:00:00

  • [Epilepsy at a psychiatric hospital].

    abstract::Epilepsy was surveyed in the largest psychiatric hospital in the Santa Catarina State, southern Brazil. This establishment was designed for one thousand long-term beds but at the time of the survey there were 1126 inpatients. Diagnosis ranged from anxiety neurosis to schizophrenia although patients with epilepsy, with...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x1990000300001

    authors: Trevisol-Bittencourt PC,Becker N,Pozzi CM,Sander JW

    更新日期:1990-09-01 00:00:00

  • Brainstem auditory pathway of children with acute lymphoid leukemia on chemotherapy with methotrexate.

    abstract:OBJECTIVE:Investigate the auditory pathway in the brainstem of children with acute lymphoblastic leukemia submitted to chemotherapy (by intravenous or intrathecal infusion). METHODS:Fourteen children aged between 2 and 12 years with diagnosis of acute lymphoid leukemia were evaluated. The following procedures were use...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/0004-282X20190139

    authors: Leite RA,Vosgrau JS,Cortez Neto L,Santos NP,Matas SLA,Odone Filho V,Matas CG

    更新日期:2020-02-01 00:00:00

  • [Ambulatory follow-up of patients with myelomeningocele in a pediatric hospital].

    abstract::Myelomeningocele is the most common congenital malformation of the nervous system and despite its complexity and involvement of multiple organs is compatible with long survival. The peculiar characteristics of this malformation expose myelomeningocele patients to acute and chronic care problems with effects in quality...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:

    authors: Salomão JF,Leibinger RD,Carvalho JG,Pinheiro JA,Lucchesi GL,Bomfim V

    更新日期:1995-09-01 00:00:00

  • Rosalie: the Brazilian female monkey of Charcot.

    abstract::Jean-Martin Charcot, the father of Neurology, a very austere and reserved man that did not express affection freely for human being, had a profound affection to animals, particularly to a small female monkey, called "Rosalie", which came from Brazil and was a gift of Dom Pedro II to Charcot. ...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 传,历史文章,杂志文章

    doi:10.1590/s0004-282x2005000400031

    authors: Teive HA,Arruda WO,Werneck LC

    更新日期:2005-09-01 00:00:00

  • [The baby alarm distress scale: a validity study].

    abstract::It should take into account the psychopatologic context and the child's development moment to evaluate the baby alarm distress from a standardized instrument. We present the BADS questionnaire validation by its application in 90 children, from 0 to 2 years-old, obtaining a K=0.783 to p<0.01, with a Spearman coefficien...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x2002000100011

    authors: Assumpcao FB Jr,Kuczynski E,Rego MG,Rocca CC

    更新日期:2002-03-01 00:00:00

  • [De novo absence status: case report].

    abstract::There are few descriptions about middle-aged patients who have nonconvulsive status epilepticus, absence status. We reported the clinical case of a woman, 52-year-old, diabetic, referred to the emergency room in a confusional state. Initial electroencephalogram showed continuous typical, bilateral, symmetric and synch...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x1997000400022

    authors: Tedrus GM,Fonseca LC,De Tella LM,Viana MA

    更新日期:1997-09-01 00:00:00

  • [Guidelines for the treatment of multiple sclerosis with immunomodulatory drugs].

    abstract::The treatment of patients with multiple sclerosis (MS) with immunomodulatory drugs, and more recently, with immunosuppressive drugs, have modified the natural history of the disease in the last years. The conclusions and recommendations elaborated by several authors based upon multicenter studies make us review and up...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章,实务指引

    doi:10.1590/s0004-282x2005000500036

    authors: Academia Brasileira de Neurologia. Departamento Científico de Neuroimunologia.

    更新日期:2005-09-01 00:00:00

  • Primary headache subtypes and thyroid dysfunction: Is there any association?

    abstract:BACKGROUND:Primary headaches, and particularly migraine and tension-type headache (TTH) as well as hypothyroidism are common medical conditions. To date, numerous studies have suggested a possible bidirectional relationship between migraine and hypothyroidism, although certain studies had contradictory results. OBJECT...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/0004-282X20200070

    authors: Spanou I,Christidi F,Liakakis G,Rizonaki K,Bougea A,Anagnostou E,Kararizou E

    更新日期:2020-11-01 00:00:00

  • Basal encephalocele associated with morning glory syndrome: case report.

    abstract::The basal encephaloceles refer to rare entities and they correspond to herniation of brain tissue through defects of skull along the cribiform plate or the sphenoid bone. A rare morning glory syndrome, with characteristic retinal defect has been reported in association with basal encephaloceles. Hypophysis hormonal de...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x2007000600013

    authors: Minotto I,Abdala N,Miachon AA,Spinola e Castro AM,Imamura P,Nogueira RG

    更新日期:2007-12-01 00:00:00

  • Different outcomes of phonemic verbal fluency in Parkinson's disease patients with subthalamic nucleus deep brain stimulation.

    abstract::Subthalamic nucleus deep brain stimulation (STN-DBS) is a surgical technique to treat motor symptoms in patients with Parkinson's disease (PD). Studies have shown that STN-DBS may cause a decline in verbal fluency performance. We aimed to verify the effects of STN-DBS on the performance of phonemic verbal fluency in B...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/0004-282X20170024

    authors: Romann AJ,Beber BC,Olchik MR,Rieder CRM

    更新日期:2017-04-01 00:00:00

  • L4-L5-S1 human dermatomes: a clinical, electromyographical, imaging and surgical findings.

    abstract::There is substantial controversy in literature about human dermatomes. We studied L4, L5, and S1 inferior limb dermatomes by comparing clinical signs and symptoms with conduction studies, electromyographical data, neurosurgical findings, and imaging data from computerized tomography (CT) or magnetic resonance imaging ...

    journal_title:Arquivos de neuro-psiquiatria

    pub_type: 杂志文章

    doi:10.1590/s0004-282x2009000200017

    authors: Faleiros AT,Resende LA,Zanini MA,Castro HA,Gabarra RC

    更新日期:2009-06-01 00:00:00