Abstract：
BACKGROUND:We recently reported that electrocardiographic abnormalities are common in adults with monosomy X (Turner syndrome), but this issue has not been investigated in girls with Turner syndrome. PATIENTS AND METHODS:We analyzed electrocardiograms in 78 girls with Turner syndrome and 50 age-matched control girls. The girls with Turner syndrome had additional cardiac and metabolic evaluations. RESULTS:Girls with Turner syndrome were more likely to demonstrate > or = 1 electrocardiographic findings including right axis deviation, right ventricular hypertrophy, accelerated atrioventricular conduction, T-wave abnormalities, and a prolonged rate-corrected QT interval. The right-sided findings were associated with partial anomalous pulmonary venous connection, but the etiology of the other findings remains unknown. The rate-corrected QT interval was significantly longer in girls with Turner syndrome (431 +/- 22 vs 407 +/- 21 milliseconds). Twenty-eight girls with Turner syndrome but only 2 controls had a rate-corrected QT interval above the reference range. We found no correlation between body habitus, cardiac dimensions, or metabolic parameters and the rate-corrected QT interval duration in girls with Turner syndrome. CONCLUSIONS:Cardiac conduction and repolarization abnormalities seem to affect both young girls and adults with Turner syndrome equally, suggesting that electrophysiologic defects are intrinsic to the syndrome and indicating that electrocardiogram analysis should be included in evaluating and monitoring even the youngest patients with Turner syndrome. Attention to the rate-corrected QT interval is important, because some common medications may further prolong this interval and increase the risk of arrhythmias.
journal_name
Pediatricsjournal_title
Pediatricsauthors
Bondy CA,Ceniceros I,Van PL,Bakalov VK,Rosing DRdoi
10.1542/peds.2006-0776subject
Has Abstractpub_date
2006-10-01 00:00:00pages
e1220-5issue
4eissn
0031-4005issn
1098-4275pii
118/4/e1220journal_volume
118pub_type
杂志文章相关文献
PEDIATRICS文献大全abstract：:Three Laotian refugee children with chronic pulmonary complaints and findings were found to have pulmonary paragonimiasis during a one-year period in Chicago. These patients ranged from 8 to 11 years of age and the diagnosis was delayed five to six months in two children because of the unfamiliarity of American physic...
journal_title：Pediatrics
pub_type： 杂志文章
doi：
更新日期：1982-08-01 00:00:00
abstract：OBJECTIVES:Severe neonatal jaundice is a common clinical manifestation of glucose-6-phosphate dehydrogenase (G-6-PD) deficiency and the most difficult to manage; kernicterus is not an uncommon outcome. We assessed in healthy, direct Coombs test-negative Greek newborns of >/=38 weeks' gestational age 1) the current burd...
journal_title：Pediatrics
pub_type： 杂志文章
doi：10.1542/peds.108.1.25
更新日期：2001-07-01 00:00:00
abstract：:In summary: (1) Colestipol therapy plus diet reduced total cholesterol 19 +/- 3% in 11 hypercholesterolemic children after two months and 13 +/- 5% after two years in five children. (2) Diet therapy did not significantly reduce serum concentration of any of the fat-soluble vitamins or folate. (3) During 24 months of c...
journal_title：Pediatrics
pub_type： 杂志文章
doi：
更新日期：1980-02-01 00:00:00
abstract：OBJECTIVE:To quantify pediatric injuries and deaths that result from toppled television sets. DESIGN:Retrospective analysis of incident files compiled by the US Consumer Product Safety Commission (CPSC) data systems and The Children's Hospital of Alabama (TCHA) inpatient medical records. SETTING:United States, Januar...
journal_title：Pediatrics
pub_type： 杂志文章
doi：10.1542/peds.102.3.e32
更新日期：1998-09-01 00:00:00
abstract：OBJECTIVES:To determine the feasibility of implementing the Community Outpatient Practice Experience (COPE), a community-based continuity program, in a large, tertiary-care-oriented pediatric residency; to assess the impact of the continuity program on pediatric residents' experience; and to compare the experience in a...
journal_title：Pediatrics
pub_type： 杂志文章
doi：
更新日期：1995-07-01 00:00:00
abstract：:National morbidity figures show a decline in reported rubella and congenital rubella syndrome since 1969, concurrent with widespread use of rubella vaccine. In addition, no nationwide outbreak, such as the 1963-1964 epidemic, has occurred, though on the basis of long-term secular trends, one would be expected between ...
journal_title：Pediatrics
pub_type： 杂志文章,评审
doi：
更新日期：1975-01-01 00:00:00
abstract：OBJECTIVE:The goal was to determine whether the increasing prevalence of autism, on the basis of educational data, in Wisconsin between 2002 and 2008 was uniform in all school districts or was greatest in districts with lower baseline (2002) prevalence. METHODS:Special education counts were obtained for all Wisconsin ...
journal_title：Pediatrics
pub_type： 杂志文章
doi：10.1542/peds.2010-1023
更新日期：2010-11-01 00:00:00
abstract：OBJECTIVE:To report the first case of human infection (infective endocarditis [IE]) caused by Pasteurella gallinarum and to review the literature regarding IE caused by the genus Pasteurella. SETTING:University hospital based. PATIENT:An adolescent boy who underwent successful correction for truncus arteriosus 10 yea...
journal_title：Pediatrics
pub_type： 杂志文章,评审
doi：
更新日期：1995-06-01 00:00:00
abstract：OBJECTIVE:To investigate the relationship between specific television-viewing habits and both sleep habits and sleep disturbances in school children. METHODS:The parents of 495 children in grades kindergarten through fourth grade in three public elementary schools completed two retrospective survey questionnaires, one...
journal_title：Pediatrics
pub_type： 杂志文章
doi：10.1542/peds.104.3.e27
更新日期：1999-09-01 00:00:00
abstract：:A program that calculates a value of clearance for an individual patient prior to reaching steady state in the early stages of aminophylline therapy is presented. The program is written for the Texas Instruments TI-59 programmable calculator and may be used with or without the PC-100C printer. The program can provide ...
journal_title：Pediatrics
pub_type： 杂志文章
doi：
更新日期：1984-01-01 00:00:00
abstract：:The purpose of this statement is to update recommendations for routine use of seasonal influenza vaccine and antiviral medications for the prevention and treatment of influenza in children. The American Academy of Pediatrics recommends annual seasonal influenza immunization for all people 6 months and older, including...
journal_title：Pediatrics
pub_type： 杂志文章,实务指引
doi：10.1542/peds.2015-2920
更新日期：2015-10-01 00:00:00
abstract：:Adult patients with long-standing hypertension have been reported to experience an impairment in renal function when treatment with potent vasodilating agents is initiated. To document that this sequence may occur in children as well, we report the case of a 4-year-old boy with renal disease in whom reduction of blood...
journal_title：Pediatrics
pub_type： 杂志文章
doi：
更新日期：1981-06-01 00:00:00
abstract：OBJECTIVE:Croup is the most common form of airway obstruction in children. Known to be primarily viral, the seasonality of croup has been examined largely through its association with the human parainfluenza viruses. This study examined the seasonal pattern of croup hospitalizations in relation to age and gender for th...
journal_title：Pediatrics
pub_type： 杂志文章
doi：10.1542/peds.2004-1892
更新日期：2005-07-01 00:00:00
abstract：:A prospective, randomized, crossover trial was conducted comparing therapy with rifampin to therapy with ampicillin in eradicating Haemophilus influenzae type b carriage. Twenty-eight carriers were identified in a day care center following exposure to a patient with H influenzae type b meningitis; 26 children were ran...
journal_title：Pediatrics
pub_type： 临床试验,杂志文章,随机对照试验
doi：
更新日期：1980-07-01 00:00:00
abstract：OBJECTIVE:We sought to document health-related quality of life (HRQoL) impairment and depressive symptomatology in adolescents with extreme obesity considering surgical weight loss. STUDY DESIGN:A retrospective review of clinical data was conducted for 33 consecutive extremely obese adolescents presenting for evaluati...
journal_title：Pediatrics
pub_type： 杂志文章
doi：10.1542/peds.2005-1141
更新日期：2006-04-01 00:00:00
abstract：BACKGROUND AND OBJECTIVE:Observation status, in contrast to inpatient status, is a billing designation for hospital payment. Observation-status stays are presumed to be shorter and less resource-intensive, but utilization for pediatric observation-status stays has not been studied. The goal of this study was to describ...
journal_title：Pediatrics
pub_type： 杂志文章,多中心研究
doi：10.1542/peds.2012-2494
更新日期：2013-06-01 00:00:00
abstract：:Severe hypercalcemia with decreased renal function, hypertension, and renal calcifications developed in a 14-year-old boy who required prolonged immobilization for multiple fractures. Parathyroid hormone was not detectable in the serum. Urinary calcium excretion was high. Initially, mobilization was impossible and the...
journal_title：Pediatrics
pub_type： 杂志文章
doi：
更新日期：1979-01-01 00:00:00
abstract：BACKGROUND AND OBJECTIVES:The Joint Commission introduced 3 Children's Asthma Care (CAC 1-3) measures to improve the quality of pediatric inpatient asthma care. Validity of the commission's measures has not yet been demonstrated. The objectives of this quality improvement study were to examine changes in provider compl...
journal_title：Pediatrics
pub_type： 杂志文章
doi：10.1542/peds.2011-3318
更新日期：2012-09-01 00:00:00
abstract：OBJECTIVE:We hypothesized that patients with cystic fibrosis (CF) have higher rates of protein breakdown than normal volunteers and that the infusion of insulin would result in less suppression of proteolysis. Methods. Using [1-C]leucine and a three-step hyperinsulinemic euglycemic clamp, we measured rates of leucine a...
journal_title：Pediatrics
pub_type： 杂志文章
doi：10.1542/peds.101.3.433
更新日期：1998-03-01 00:00:00
abstract：OBJECTIVE:To assess 1) knowledge of neural tube defect (NTD) prevention by folic acid, 2) frequency of intake of multivitamins and folate- and folic acid-fortified food, and 3) factors associated with knowledge and prevention practices among sexually active minority adolescent and young adult women. METHODS:Young mino...
journal_title：Pediatrics
pub_type： 杂志文章
doi：10.1542/peds.112.3.536
更新日期：2003-09-01 00:00:00
abstract：OBJECTIVE:To assess determinants of health care visits among children in a 12-county region of western North Carolina representative of rural areas in the United States. METHODS:Households were randomly selected for surveys of household characteristics, health status, and health care use. Surveys were conducted June 1...
journal_title：Pediatrics
pub_type： 杂志文章
doi：10.1542/peds.112.2.e143
更新日期：2003-08-01 00:00:00
abstract：OBJECTIVES:To further define the clinical spectrum of the disease for pediatric and metabolic specialists, and to suggest that the general pediatrician and pediatric neurologist consider succinic semialdehyde dehydrogenase (SSADH) deficiency in the differential diagnosis of patients with (idiopathic) mental retardation...
journal_title：Pediatrics
pub_type： 杂志文章
doi：10.1542/peds.99.4.567
更新日期：1997-04-01 00:00:00
abstract：OBJECTIVES:Because children spend a significant proportion of their day in school, pediatric emergencies such as the exacerbation of medical conditions, behavioral crises, and accidental/intentional injuries are likely to occur. Recently, both the American Academy of Pediatrics and the American Heart Association have p...
journal_title：Pediatrics
pub_type： 杂志文章
doi：10.1542/peds.2005-1474
更新日期：2005-12-01 00:00:00
abstract：BACKGROUND:Recommended durations of observation after anaphylaxis have been widely variable, with many ranging from 4 to 24 hours. Prolonged durations often prompt admission for ongoing observation. METHODS:In a multidisciplinary quality improvement initiative, we revised our emergency department (ED) anaphylaxis clin...
journal_title：Pediatrics
pub_type： 杂志文章
doi：10.1542/peds.2017-1616
更新日期：2018-05-01 00:00:00
abstract：OBJECTIVE:In the United States, 15- to 24-year-olds represent approximately 14% of HIV cases diagnosed in 2006 and almost 50% of the 19 million sexually transmitted infections (STIs) reported annually. This survey assessed pediatricians' practices regarding preventive health care screening, provision of reproductive he...
journal_title：Pediatrics
pub_type： 杂志文章,随机对照试验
doi：10.1542/peds.2009-0271
更新日期：2010-04-01 00:00:00
abstract：OBJECTIVE:This study examined the process of health care transition (HCT) posing the following questions: What are the transition experiences of youths and young adults with disabilities and special health care needs, family members, and health care providers? What are promising practices that facilitate successful HCT...
journal_title：Pediatrics
pub_type： 杂志文章
doi：10.1542/peds.2004-1321
更新日期：2005-01-01 00:00:00
abstract：:Because boxing may result in serious brain and eye injuries, the American Academy of Pediatrics opposes this sport. This policy statement summarizes the reasons. ...
journal_title：Pediatrics
pub_type： 杂志文章
doi：
更新日期：1997-01-01 00:00:00
abstract：:In 1992, the Committee on Infectious Diseases and Committee on Fetus and Newborn of the American Academy of Pediatrics provided guidelines for prevention of early-onset group B streptococcal (GBS) disease through intrapartum chemoprophylaxis of selected maternal GBS carriers. The guidelines were based on demonstrated ...
journal_title：Pediatrics
pub_type： 指南,杂志文章,实务指引
doi：10.1542/peds.99.3.489
更新日期：1997-03-01 00:00:00
abstract：OBJECTIVE:The goal was to determine whether home asthma telemonitoring with store-and-forward technology improved outcomes, compared with in-person, office-based visits. METHODS:A total of 120 patients, 6 to 17 years of age, with persistent asthma were assigned randomly to the office-based or virtual group. The 2 grou...
journal_title：Pediatrics
pub_type： 杂志文章,随机对照试验
doi：10.1542/peds.2006-1884
更新日期：2007-03-01 00:00:00
abstract：:The pediatrician plays a key role in the prevention of mother-to-child transmission of HIV-1 infection. For infants born to women with HIV-1 infection identified during pregnancy, the pediatrician ensures that antiretroviral prophylaxis is provided to the infant to decrease the risk of acquiring HIV-1 infection and pr...
journal_title：Pediatrics
pub_type： 杂志文章,评审
doi：10.1542/peds.2008-3076
更新日期：2009-01-01 00:00:00
