[Supravalvular aortic stenosis in two black patients].

Abstract:

:Two male black patients, 18 and 12-year-old, with mental retardation and typical elfin face, presented with severe supravalvular aortic stenosis, thus characterizing Williams's or aortic supravalvular stenosis syndrome. Both were submitted to surgical treatment of the stenosis, and are asymptomatic after a one and four years follow-up. For the first time this syndrome, in its classical form, is described in black patients.

journal_name

Arq Bras Cardiol

authors

Benchimol CB,Araújo JO,Féres JG,Carvalho LA,Przytyk RN,Netto MS,Moll J,Gomes EF,Araújo Filho R,Saad E

subject

Has Abstract

pub_date

1991-10-01 00:00:00

pages

335-8

issue

4

eissn

0066-782X

issn

1678-4170

journal_volume

57

pub_type

杂志文章
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    abstract::There are limited data regarding the use of hypolipidemic agents concomitantly with immunosuppressive drugs. Best evidence is provided for the use of statins and cyclosporine. In terms of pharmacodynamics, these two drugs have different substrates. In respect to pharmacokinetics, statins usually do not modify serum co...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:/S0066-782X2005002400013

    authors: Izar MC

    更新日期:2005-10-01 00:00:00

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    abstract:BACKGROUND:Several studies have been attempting to ascertain the risks of Sleep Apnea Syndrome (SAS) and its morbidity and mortality. OBJECTIVE:The main objective was to verify whether SAS increases the risk of death; the secondary objective was to evaluate its morbidity in relation to cardiovascular disease and the n...

    journal_title:Arquivos brasileiros de cardiologia

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    doi:10.5935/abc.20140172

    authors: Fonseca MI,Pereira T,Caseiro P

    更新日期:2015-01-01 00:00:00

  • [Directional atherectomy and coronary angioplasty: a therapy complementary to myocardial revascularization surgery].

    abstract::A white male patient, 59 years old, with two prior surgical myocardial revascularization and unstable angina, was submitted to coronary arteriography that showed: all the saphenous vein grafts patent and obstruction of 75% in the saphenous vein graft to the second marginal branch of left circumflex artery. Left intern...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:

    authors: Pimentel Filho WA,Büchler JR,Assis SF,Araújo EC,Neves Filho M,Pinheiro LF,de Souza JA,Ascer E,Ribas W,Vieira VD

    更新日期:1992-03-01 00:00:00

  • [Use of implantable pacemaker in the treatment of paroxysmal supraventricular tachycardia refractory to pharmacologic therapy].

    abstract:PURPOSE:To evaluate the results with the use of an automatic antitachycardia pacemaker in patients with refractory paroxysmal supraventricular tachycardia. PATIENTS AND METHODS:Nine patients aged 32 to 63 years with symptoms from 2 to more than 40 years and prophylactic treatment with several antiarrhythmic drugs that...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:

    authors: Sant'Anna JR,Medeiros C,Halperin C,Lucchese F,Kalil R,Prates P,Nonohay N,Nesralla I

    更新日期:1991-04-01 00:00:00

  • [Different therapies in the treatment of obesity in hypertensive patients].

    abstract:PURPOSE:To evaluate the efficacy and tolerability of different therapies associated with diet in the treatment of hypertensive obese patients. METHODS:In a clinical study we randomly evaluated 39 hypertensive obese patients (body mass index (BMI) > or = 30 kg/m2). After 45 days of diet the patients were again randomly...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 临床试验,杂志文章,随机对照试验

    doi:

    authors: Monego ET,Peixoto Mdo R,Jardim PC,Sousa AL,Braga VL,Moura MF

    更新日期:1996-06-01 00:00:00

  • Effects of added salt reduction on central and peripheral blood pressure.

    abstract:BACKGROUND:Although the effects of salt intake reduction on casual blood pressure have been extensively studied in hypertensive individuals, data on reductions of added salt on arterial stiffness in both normotensive and prehypertensive subjects are scarce. OBJECTIVE:To evaluate the effects of progressive reduction in...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 临床试验,杂志文章

    doi:10.36660/abc.20180426

    authors: Arantes AC,Sousa ALL,Vitorino PVO,Jardim PCBV,Jardim TSV,Rezende JM,Lelis ES,Rodrigues RB,Coca A,Barroso WKS

    更新日期:2020-05-01 00:00:00

  • Features of the onset of Takayasu's arteritis according to gender.

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    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.5935/abc.20130180

    authors: Mont'Alverne AR,Paula LE,Shinjo SK

    更新日期:2013-10-01 00:00:00

  • Echocardiography in chronic liver disease: systematic review.

    abstract:BACKGROUND:Doppler echocardiography (Echo) is a non-invasive method of excellent accuracy to screen portopulmonary hypertension (PPH) and to assess intrapulmonary shunts (IPS) in chronic liver disease (CLD). In the past decade, Echo proved to play a fundamental role in the diagnosis of cirrhotic cardiomyopathy (CCM). ...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章,评审

    doi:

    authors: Mota VG,Markman Filho B

    更新日期:2013-04-01 00:00:00

  • Triceps skinfold as a prognostic predictor in outpatient heart failure.

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    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.5935/abc.20130185

    authors: Zuchinali P,Souza GC,Alves FD,d'Almeida KS,Goldraich LA,Clausell NO,Rohde LE

    更新日期:2013-11-01 00:00:00

  • [Current insights into the modern treatment of decompensated heart failure].

    abstract::Treatment of DHF is a challenge even for the experienced physician. Advances in research have brought new treatment options that are helping change paradigms. The available evidence suggests that new drugs like levosimendan and nesiritide will assume relevant positions as alternatives or complements to treatment with ...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章,评审

    doi:10.1590/s0066-782x2006001600022

    authors: Vilas-Boas F,Follath F

    更新日期:2006-09-01 00:00:00

  • Do diabetic patients with acute coronary syndromes have a higher threshold for ischemic pain?

    abstract:BACKGROUND:Data from over 4 decades have reported a higher incidence of silent infarction among patients with diabetes mellitus (DM), but recent publications have shown conflicting results regarding the correlation between DM and presence of pain in patients with acute coronary syndromes (ACS). OBJECTIVE:Our primary o...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.5935/abc.20140106

    authors: Nicolau JC,Barbosa CJ,Franci A,Baracioli LM,Franken M,Lima FG,Giraldez RR,Kalil Filho R,Ramires JA,Giugliano RP

    更新日期:2014-09-01 00:00:00

  • Comparison of diagnostic criteria for acute kidney injury in cardiac surgery.

    abstract:BACKGROUND:There is considerable controversy regarding the diagnosis of Acute Kidney Injury (AKI), and there are over 30 different definitions. OBJECTIVE:To evaluate the incidence and risk factors for the development of AKI following cardiac surgery according to the RIFLE, AKIN and KDIGO criteria, and compare the prog...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.5935/abc.20130115

    authors: Sampaio MC,Máximo CA,Montenegro CM,Mota DM,Fernandes TR,Bianco AC,Amodeo C,Cordeiro AC

    更新日期:2013-07-01 00:00:00

  • [Cardiovascular risk factors and mortality. Long-term follow-up (up to 20 years) in a preventive program carried out by occupational medicine].

    abstract:OBJECTIVE:The decrease in mortality due to cardiovascular diseases (CVD) has been achieved in the United States and the same decrease has been happening in developing countries, thanks to favorable changes in lifestyle and risk factors. Despite such consideration, the volume of information available on the distribution...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2005001400005

    authors: Ciorlia LA,Godoy MF

    更新日期:2005-07-01 00:00:00

  • Prevalence and surgical approach of supravalvular pulmonary stenosis after Jatene operation for transposition of great arteries.

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    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章,多中心研究

    doi:10.1590/s0066-782x2008001300003

    authors: Jatene MB,Jatene IB,Oliveira PM,Moysés RA,Souza LC,Fontes V,Miura N,Lopes AA,Marcial MB,Jatene AD

    更新日期:2008-07-01 00:00:00

  • Determinants of Aortic Prosthesis Mismatch in a Brazilian Public Health System Hospital: Big Patients or Small Prosthesis?

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    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.5935/abc.20190231

    authors: Otto ME,Atik FA,Moreira MDN,Ribeiro LCM,Mello BCR,Lima JGE,Ribeiro MS,Domingues ACPM,Calzada RP,Jreige A Jr,Schloicka LL,Pibarot P

    更新日期:2020-01-01 00:00:00

  • One-year follow-up after primary coronary intervention for acute myocardial infarction in diabetic patients. A substudy of the STENT PAMI trial.

    abstract:OBJECTIVE:This analysis was undertaken to determine the composite incidence of cumulative adverse events (death, reinfarction, disabling stroke, and target vessel revascularization) at the end of the first year after acute myocardial infarction, in diabetic patients who underwent coronary stenting or primary coronary b...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 临床试验,杂志文章,随机对照试验

    doi:10.1590/s0066-782x2001001200006

    authors: Mattos LA,Grines CL,Sousa JE,Sousa AG,Stone GW,Cox D,Garcia E,Morice MC,O'Neill W,Grines L,Boura J

    更新日期:2001-12-01 00:00:00

  • Successful reversal of pulmonary hypertension in Eisenmenger complex.

    abstract::We present a case of a 19-year old female with systemic pulmonary artery (PA) pressure due to a congenital ventricular septal defect (VSD) and atrial septal defect (ASD). She was pink at rest and cyanotic on exercise. Lung biopsy revealed grade IV pulmonary vascular changes. As a preliminary step PA was banded to incr...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:

    authors: Batista RJ,Santos JL,Takeshita N,Eocchino L,Lima PN,Goehr M,Cunha MA,Kawaguchi AT,Salerno TA

    更新日期:1997-04-01 00:00:00

  • [Reproducibility of head-up tilt test in patients with neurocardiogenic syncope].

    abstract:PURPOSE:In order to identify the reproducibility of head-up tilt test, a second test one week later in 22 patients with a positive first test, was performed. METHODS:The test was performed in a fasting state during the morning. The heart rate and blood pressure were monitored during 20 minutes in the supine position a...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:

    authors: Hachul D,Sosa EA,Consolim F,Magalhães L,Scanavacca M,Martinelli M,Bellotti G,Pileggi F

    更新日期:1994-05-01 00:00:00

  • [Subaortic stenosis associated with perimembranous ventricular septal defect. Clinical follow-up of 36 patients].

    abstract:OBJECTIVE:To study the clinical pattern of subaortic stenosis associated with perimembranous ventricular septal defect. METHODS:From January 1979 to June 2000, 36 children with perimembranous ventricular septal defect and fixed subaortic stenosis were followed-up regarding anatomic characteristics, evolvement, and cli...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2005000200002

    authors: Horta Mda G,Faria CA,Rezende DF,Masci TL,Rabelo CC,Katina T,Oliveira Md,Oliveira LP

    更新日期:2005-02-01 00:00:00

  • [Subaortic stenosis caused by anomalous chordae tendineae of the mitral valve ("mitral web")].

    abstract::Patient with subaortic stenosis due to the insertion of anomalous chordae tendineae of the mitral valve in the interventricular septum (mitral web) associated with mitral stenosis with diagnosis made by bidimensional echocardiographic study with Doppler and confirmed by hemodynamic study. The patient was submitted to ...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:

    authors: Groppo AA,Santos GG,Simões RM,Haddad VL,Stolf NA

    更新日期:1993-09-01 00:00:00

  • [Influence of the clinical presentation on immediate and long-term results after rotational atherectomy].

    abstract:PURPOSE:To analyse the influence of unstable coronary syndromes (UCS) in the early and late prognosis after rotational atherectomy (RA). METHODS:We treated 236 patients with RA between Aug/1992 and May/1996. Patients were divided into two groups: A) stable coronary syndromes 120 (51%) patients; B) UCS: 116 (49%) patie...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:

    authors: Tanajura LF,Sousa AG,Feres F,Mattos LA,Nunes GL,Abizaid A,Pinto IM,Centemero MP,Chaves AJ,Abizaid AC,Sousa JE

    更新日期:1997-02-01 00:00:00

  • Influence of the elevation of the left ventricular diastolic pressure on the values of the first temporal derivative of the ventricular pressure (dP/dt).

    abstract:PURPOSE:To assess the effects of the elevation of the left-ventricular end-diastolic pressure (LVEDP) on the value of the 1st temporal derivative of the ventricular pressure (dP/dt). METHODS:Nineteen anesthetized dogs were studied. The dogs were mechanically ventilated and underwent thoracotomy with parasympathetic ne...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x1999000700004

    authors: Okoshi K,Fioretto JR,Bonatto RC,Tornero MT,Tucci PJ

    更新日期:1999-07-01 00:00:00

  • [Relationship between regular attendance to ambulatory appointments and blood pressure control among hypertensive patients].

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    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2005001600002

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    更新日期:2005-09-01 00:00:00

  • Correlation to NT-ProBNP and remodeling after cardiac surgery.

    abstract:BACKGROUND:Few data are available on diastolic function in patients with aortic stenosis (AOS) with indication of surgical treatment. A potential correlation between biomarkers and diastolic function has not been established. OBJECTIVE:The aim of our study was to evaluate diastolic function in patients with AOS waitin...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.5935/abc.20130076

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    更新日期:2013-05-01 00:00:00

  • [Lipid profile and nutrition counseling effects in adolescents with family history of premature coronary artery disease].

    abstract:OBJECTIVE:To assess lipid profile and nutritional parameters from adolescents with family history of premature coronary artery disease (CAD) and assess the effects of nutritional counseling. METHODS:The study included 48 adolescents of both gender and with ages ranging from 10 and 19 years old (case group, n=18; contr...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2006000500006

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    更新日期:2006-05-01 00:00:00

  • [Reversion of cardiogenic shock by direct angioplasty of the right coronary artery: a case report].

    abstract::A 57 year-old male patient developed cardiogenic shock after inferior wall myocardial infarction. Cinecoronariography demonstrated a critical distal lesion of the right coronary artery. Transluminal percutaneous coronary angioplasty was carried out four hours after onset of pain and thirty minutes after hospital admis...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:

    authors: Medeiros Filho H,de Medeiros Mde F,de Souza JB,Montenegro S,Mesquita E

    更新日期:1990-04-01 00:00:00

  • Coronary artery disease in patients with rheumatic and non-rheumatic valvular heart disease treated at a public hospital in Rio de Janeiro.

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  • Prevalence of dyslipidemia and risk factors in Campos dos Goytacazes, in the Brazilian state of Rio de Janeiro.

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    journal_title:Arquivos brasileiros de cardiologia

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  • [Intermittent ventricular pre-excitation in the presence of total atrioventricular block].

    abstract::An 8 year old child suffering from asthenia and complete atrioventricular block, probably congenital. During the tread-mill test there was a sudden electrocardiogram change to a ventricular preexcitation pattern. Besides this rare association, we emphasize the importance of the autonomic balance over the accessory pat...

    journal_title:Arquivos brasileiros de cardiologia

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    authors: Haertel LA,Moffa PJ,Grupi CJ,Camargo PA,Pereyra PA,Lima EV

    更新日期:1993-11-01 00:00:00