Non-canonical manifestations of familial Mediterranean fever: a changing paradigm.

abstract：:Kikuchi-Fujimoto disease (KFD) or histiocytic necrotizing lymphadenitis is a rare, benign, autoimmune condition characterized by lymphadenopathy, fever, and neutropenia. KFD can frequently mimic various diseases including infection, malignancy, and autoimmune disease. KFD has also been infrequently reported in associa...

journal_title：Clinical rheumatology

authors： Kampitak T

更新日期：2008-08-01 00:00:00

abstract：:Spontaneous fractures of the sternum are rare but worth knowing as they may simulate acute cardiac and pulmonary emergencies. A case of an insufficiency sternal fracture mimicking myocardial infarction and subsequent anginal pain is presented. The risk factors of this condition, its clinical features and the diagnosti...

journal_title：Clinical rheumatology

authors： Schapira D,Nachtigal A,Scharf Y

更新日期：1995-07-01 00:00:00

abstract：:To examine the relationship between physical appearance concern and psychological distress in female adolescent patients with systemic lupus erythematosus (SLE) was the aim of this study. A total of 84 adolescent SLE female patients and 80 age-matching healthy adolescents were evaluated for levels of appearance concer...

journal_title：Clinical rheumatology

authors： Ji L,Lili S,Jing W,Yanyan H,Min W,Juan X,Hongmei S

更新日期：2012-12-01 00:00:00

abstract：:The signalling lymphocyte activation molecule (SLAM) family receptors play important roles in modulating immune responses. Previous studies in murine models and patients have suggested an association of the SLAM family (SLAMF) members with the development of autoimmunity, particularly systemic lupus erythematosus (SLE...

journal_title：Clinical rheumatology

authors： Mak A,Thornhill SI,Lee HY,Lee B,Poidinger M,Connolly JE,Fairhurst AM

更新日期：2018-03-01 00:00:00

abstract：:To estimate the mortality and describe the causes of death in a large multicenter cohort of hospitalized patients with SLE in China. This was a retrospective study of a nationwide SLE cohort (10 centers, 29,510 hospitalized patients) from 2005 to 2014 in China. Standardized mortality ratios (SMRs) were calculated for ...

journal_title：Clinical rheumatology

authors： Wu XY,Yang M,Xie YS,Xiao WG,Lin J,Zhou B,Guan X,Luo CN,Che N,Liu XZ,Wang C,Teng JL,Cheng XB,Ye JN,Su YT,Shi H,Yin YF,Liu MR,Sun Y,Hu QY,Zhou ZC,Chi HH,Liu Y,Zhang X,Chen JW,Zhang MJ,Zhao DB,Yang CD,

更新日期：2019-01-01 00:00:00

abstract：OBJECTIVES:Decreased natural killer (NK) cells have been reported in systemic lupus erythematosus (SLE) patients. However, the role of NK cells in the pathogenesis of SLE is not well understood. In this study, we aimed to characterize NK cell subsets, phenotypes, and cytokine-secreting functions and investigate the cli...

journal_title：Clinical rheumatology

authors： Liu M,Liu J,Zhang X,Xiao Y,Jiang G,Huang X

更新日期：2020-08-14 00:00:00

abstract：:This study aims to compare the mean platelet volume (MPV) levels in children and adults diagnosed with familial Mediterranean fever (FMF) during attack-free periods in order to find out whether it reflects the emergence of microalbuminuria/proteinuria and the development of amyloidosis or not. The study consisted of 6...

journal_title：Clinical rheumatology

authors： Sakallı H,Kal O

更新日期：2013-08-01 00:00:00

abstract：:Since diffuse idiopathic skeletal hyperostosis (DISH) is frequently difficult to differentiate radiologically from the axial involvement of ankylosing spondylitis and osteoarthrosis, some features of these 3 different diseases were compared. The predominantly horizontal nature of the enthesiophyte in DISH and its righ...

journal_title：Clinical rheumatology

authors： Maertens M,Mielants H,Verstraete K,Veys EM

更新日期：1992-12-01 00:00:00

abstract：:Pauci-immune necrotizing glomerulonephritis is a form of a rapidly progressive glomerulonephritis that is associated with the anti-neutrophil cytoplasmic antibodies (ANCA). ANCA-associated pauci-immune glomerulonephritis may be secondary to rheumatic diseases. We report on a patient with limited cutaneous systemic scl...

journal_title：Clinical rheumatology

authors： Chan PT,Mok CC

更新日期：2012-08-01 00:00:00

abstract：:Lysosomal storage diseases are rare metabolic disorders, some of which can now be treated using enzyme replacement therapies. Because the time point of treatment initiation significantly influences the outcome in Gaucher disease, Fabry disease, and mucopolysaccharidosis type I, early diagnosis is of utmost importance....

journal_title：Clinical rheumatology

authors： Manger B,Mengel E,Schaefer RM

更新日期：2007-03-01 00:00:00

abstract：:Behçet's disease is a systemic vasculitic syndrome with unknown etiology. The aim of the present study was to compare the Helicobacter pylori seropositivity and cytotoxin associated gene-A status in patients with Behçet's disease. Ninety-one patients with Behçet's disease and 83 age- and sex-matched persons with or wi...

journal_title：Clinical rheumatology

authors： Apan TZ,Gürsel R,Dolgun A

更新日期：2007-06-01 00:00:00

abstract：:A case of pseudo-pseudohypoparathyroidism (PPH) with shortening of the left femur and tibia and coalition of the base of the fourth metacarpals with capitatum and hamatum in bilateral wrist joints was presented. Involvement of the fourth digits both in hands and feet were more prominent on the left side, with shorteni...

journal_title：Clinical rheumatology

authors： Unlu Z,Orguc S,Yilmaz Ovali G,Bayindir P

更新日期：2007-07-01 00:00:00

abstract：:There are few reports about the coexistence of Sjögren's syndrome (SS) and ankylosing spondylitis (AS). To evaluate the frequency of SS in patients with AS. We studied 70 patients with AS presenting to the university outpatient clinic between January 2002 and November 2003. All the patients were asked about sicca symp...

journal_title：Clinical rheumatology

authors： Kobak S,Kobak AC,Kabasakal Y,Doganavsargil E

更新日期：2007-02-01 00:00:00

abstract：:Adiponectin is a hormone released by adipose tissue with antidiabetic, antiatherogenic, and anti-inflammatory properties. The present observational study focused on the relation between serum adiponectin level and the disease severity of established rheumatoid arthritis (RA). Ninety patients with more than 5-year diag...

journal_title：Clinical rheumatology

authors： Ebina K,Fukuhara A,Ando W,Hirao M,Koga T,Oshima K,Matsuda M,Maeda K,Nakamura T,Ochi T,Shimomura I,Yoshikawa H,Hashimoto J

更新日期：2009-04-01 00:00:00

abstract：:Belimumab is an effective and safe treatment option for systemic lupus erythematosus (SLE). However, data on treatment cessation are lacking. Thus, we investigated belimumab-free remission in SLE patients. SLE patients receiving belimumab in our institute (May 1, 2013-May 31, 2019) were retrospectively identified usin...

journal_title：Clinical rheumatology

authors： Nakai T,Fukui S,Ikeda Y,Shimizu H,Tamaki H,Okada M

更新日期：2020-12-01 00:00:00

abstract：:Sarcoidosis is a multisystemic disease with cutaneous lesions present in about one fourth of patients. Cutaneous lesions may be specific or nonspecific based on the presence or the absence of sarcoidal granulomas. Subcutaneos sarcoidosis is the less frequent of the specific cutaneous lesions of sarcoidosis. We report ...

journal_title：Clinical rheumatology

authors： Dalle Vedove C,Colato C,Girolomoni G

更新日期：2011-08-01 00:00:00

abstract：:The association of different autoimmune diseases in the same subject is not uncommon, also in the pediatric age. The coexistence of morphea and juvenile idiopathic arthritis (JIA) is however exceptional. We report four such cases. Unlike the few other reported cases, in 3/4 of our patients, morphea appeared well after...

journal_title：Clinical rheumatology

authors： Giani T,Madera A,Cimaz R

更新日期：2020-04-01 00:00:00

abstract：:Determine the effect of daily low divided or single daily dose of prednisone on the longitudinal change in the number of tender and swollen joints and HAQ scores in African Americans (AA) with early rheumatoid arthritis (RA) from the Consortium for the Longitudinal Evaluation of African Americans with Early Rheumatoid...

journal_title：Clinical rheumatology

authors： Conn DL,Tiliakos A,Bao G,Liu S,Li S,Easley KA

更新日期：2018-02-01 00:00:00

abstract：:Although peripheral blood eosinophilia is observed in patients with active inflammatory rheumatoid arthritis (RA), RA is not a recognised cause of pulmonary eosinophilia. We describe a 55-year-old woman affected by chronic eosinophilic pneumonia (CEP) concomitantly with an initiation of RA. Both diseases responded rap...

journal_title：Clinical rheumatology

authors： Kwak JJ,Chang JE,Lee J,Cho YJ,Sung SH

更新日期：2003-09-01 00:00:00

abstract：BACKGROUND AND OBJECTIVES:The purpose of this study was to develop an understanding of treatment preferences in patients with inflammatory arthritis (IA) [rheumatoid arthritis (RA), ankylosing spondylitis (AS) and psoriatic arthritis (PsA)] focussing on treatment attributes that patients' value, their relative importan...

journal_title：Clinical rheumatology

authors： Ho KA,Acar M,Puig A,Hutas G,Fifer S

更新日期：2020-04-01 00:00:00

abstract：:Tumor necrosis factor receptor-associated periodic syndrome (TRAPS) is characterized by recurrent episodes of inflammation with fever, abdominal pain, chest pain, rash, myalgia, arthralgia, conjunctivitis, and periorbital edema. This condition is a rare autosomal dominant disease that is strongly associated with heter...

journal_title：Clinical rheumatology

authors： Chen Y,Huang X,Zheng S,Zhu Z,Yang W,Liu J

更新日期：2018-05-01 00:00:00

abstract：:Recently, the Ankylosing Spondylitis Disease Activity Score (ASDAS), a new index, has been shown to be validated and highly discriminatory in assessing ankylosing spondylitis (AS) disease activity. This study is to evaluate the performance of ASDAS in a local Chinese cohort of AS in a cross-sectional setting and to co...

journal_title：Clinical rheumatology

authors： Au YL,Wong WS,Mok MY,Chung HY,Chan E,Lau CS

更新日期：2014-08-01 00:00:00

abstract：:Systemic lupus erythematosus (SLE) is a chronic autoimmune disease with a wide range of manifestations and potential to affect several organ systems. Complications arise from both disease and medications especially glucocorticoids, significantly contributing to overall morbidity and mortality. SLE predominantly affect...

journal_title：Clinical rheumatology

authors： Navarra SV,Zamora LD,Collante MTM

更新日期：2020-03-01 00:00:00

abstract：:The aim of the study was to investigate the pulmonary parenchymal abnormalities by high resolution computed tomography (HRCT) in patients with various forms of scleroderma. Three scans were performed sequentially in all cases: one at the level of aortic arch, one at the tracheal carina and one 1-2 cm above the diaphra...

journal_title：Clinical rheumatology

authors： Dévényi K,Czirják L

更新日期：1995-11-01 00:00:00

abstract：INTRODUCTION:We investigated whether rheumatoid arthritis (RA)-related autoantibodies were associated with abnormalities on pulmonary function tests (PFTs). METHODS:We studied RA serostatus and PFT abnormalities within a RA registry. RA serostatus was assessed by research assays for cyclic citrullinated peptide (CCP) ...

journal_title：Clinical rheumatology

authors： Huang S,He X,Doyle TJ,Zaccardelli A,Marshall AA,Friedlander HM,Blaustein RB,Smith EA,Cui J,Iannaccone CK,Mahmoud TG,Weinblatt ME,Dellaripa PF,Shadick NA,Sparks JA

更新日期：2019-12-01 00:00:00

abstract：:The objectives of this study are to assess the risk of asymptomatic cranial neuropathy among patients with systemic lupus erythematosus (SLE) and find any association with disease activity and antiribosomal P antibodies. This study is a case-control study including 60 female patients and 30 healthy female controls. Di...

journal_title：Clinical rheumatology

authors： Gaber W,Ezzat Y,El Fayoumy NM,Helmy H,Mohey AM

更新日期：2014-01-01 00:00:00

abstract：:Adult-onset Still's disease (AOSD) has often been regarded as the adult spectrum of systemic juvenile idiopathic arthritis (sJIA). The present study aims to compare the clinical and laboratory features, the disease course and the response to treatment in patients having AOSD with those having sJIA. Retrospective revie...

journal_title：Clinical rheumatology

authors： Pay S,Türkçapar N,Kalyoncu M,Simşek I,Beyan E,Ertenli I,Oztürk MA,Düzgün N,Erdem H,Ozbalkan Z,Kiraz S,Kinikli G,Besbas N,Dinç A,Ateş A,Olmez U,Calgüneri M,Aydintuğ OT,Bakkaloğlu A,Turan M,Turgay M,Karaaslan Y,

更新日期：2006-09-01 00:00:00

abstract：:The most widely used noninvasive methods of bone mass measurement include: single photon absorptiometry (SPA), quantitative computed tomography (QCT), dual photon absorptiometry (DPA and DEXA). SPA is used to measure bone mineral content (BMC) of the distal radius. Its advantages are low cost and high precision in viv...

journal_title：Clinical rheumatology

authors： Sabatier JP,Guaydier-Souquieres G

更新日期：1989-06-01 00:00:00

abstract：:Mouth and genital ulcer with inflamed cartilage syndrome (MAGIC syndrome) is a rare autoinflammatory disorder with unknown etiology. Except for the common clinical manifestations mimicking Behçet's disease and relapsing polychondritis, some other clinical entities are occasionally observed. In this report, we present ...

journal_title：Clinical rheumatology

authors： Chen Z,Zhang S,Wang L,Fei Y,Shen M,Wu H,Liu J,Zheng W

更新日期：2020-09-11 00:00:00

abstract：:The vitamin D is involved in a wide variety of biological processes including bone metabolism, modulation of the immune response, and regulation of cell proliferation and differentiation. Vitamin D has several immunomodulatory effects through vitamin D receptor (VDR). A series of common single-nucleotide polymorphisms...

journal_title：Clinical rheumatology

authors： Zilahi E,Chen JQ,Papp G,Szántó A,Zeher M

更新日期：2015-02-01 00:00:00