Fatal nodular xanthomatosis in an infant.

Abstract:

:We describe a unique and puzzling case of a 7-month-old baby with a non-X hypertriglyceridemic histiocytoxanthomatosis. The disease was characterized by a massive nodular eruption that was clinically, histologically, and ultrastructurally consistent with juvenile xanthogranuloma, but it had a rapid, fatal evolution.

journal_name

Pediatr Dermatol

journal_title

Pediatric dermatology

authors

Caputo R,Ermacora E,Gelmetti C,Gianni E

doi

10.1111/j.1525-1470.1987.tb00787.x

subject

Has Abstract

pub_date

1987-11-01 00:00:00

pages

242-6

issue

3

eissn

0736-8046

issn

1525-1470

journal_volume

4

pub_type

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