Fibroadipose vascular anomaly treated with sirolimus: Successful outcome in two patients.

Abstract:

:Fibroadipose vascular anomaly (FAVA) is a rare, complex mesenchymal malformation combining fibrofatty replacement of the affected muscles and slow-flow vascular malformation. The condition is characterized by localized swelling, severe pain, phlebectasia, and contracture of the affected limb. Treatment paradigms are not well established for this rare, recently recognized condition. We report two cases of FAVA in which treatment with sirolimus produced rapid, dramatic improvement in pain and quality of life.

journal_name

Pediatr Dermatol

journal_title

Pediatric dermatology

authors

Erickson J,McAuliffe W,Blennerhassett L,Halbert A

doi

10.1111/pde.13260

subject

Has Abstract

pub_date

2017-11-01 00:00:00

pages

e317-e320

issue

6

eissn

0736-8046

issn

1525-1470

journal_volume

34

pub_type

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